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심광연,노미오,김현정,배상병,김찬규,이규택,이유경,박성규,원종호,박희숙,홍대식 대한혈액학회 2006 Blood Research Vol.41 No.4
골수형성이상증후군 환자의 10%에서 용혈빈혈과 같은, 면역연관 혈액학적 이상과 관련된 다양한 자가면역질환들을 보인다. 그러나 골수형성이상증후군에서는 그물적혈구감소증이 보이므로 쿰스음성자가면역용혈빈혈을 간과할 수 있다. 그래서 말초혈액바른표본검사와 합토글로빈의 측정이 중요하다. 자가면역증상들은 스테로이드와 같은 면역억제제에 반응한다. 본 저자들은 쿰스음성자가면역용혈빈혈에 동반된 골수형성이상증후군과 스테로이드를 이용한 치료를 경험하였기에 임상적인 특징과 경과를 문헌고찰과 함께 보고하는 바이다.
심광연,차상우,엄욱현,전창균,정승원,장재영,조영덕 대한소화기학회 2013 대한소화기학회지 Vol.61 No.2
Gallbladder (GB) cancer occurs predominately as a biliary tract malignant tumor. It generally has a very poor prognosis, and early detection is often difficult. A variety of carcinogens have been implicated as an important cause for GB cancer. Benzene is a well-known carcinogen for hematologic malignancy, and its casual relationship with GB cancer has been suggested. We report a case of two patients who had operated a laundry cleaning facility together and later simultaneously got GB cancer after prolonged benzene exposure.
세탁소를 운영하는 부부에서 동시에 발생한 담낭암 담낭암과 벤젠과의 연관성
심광연 ( Kwang Yeun Shim ),차상우 ( Sang Woo Cha ),엄욱현 ( Wook Hyun Um ),전창균 ( Chang Gyun Chun ),정승원 ( Soung Won Jeong ),장재영 ( Jae Young Jang ),조영덕 ( Young Deok Cho ) 대한소화기학회 2013 대한소화기학회지 Vol.61 No.2
Gallbladder (GB) cancer occurs predominately as a biliary tract malignant tumor. It generally has a very poor prognosis, and early detection is often difficult. A variety of carcinogens have been implicated as an important cause for GB cancer. Benzene is a well-known carcinogen for hematologic malignancy, and its casual relationship with GB cancer has been suggested. We report a case of two patients who had operated a laundry cleaning facility together and later simultaneously got GB cancer after prolonged benzene exposure.
최수정,심광연,박무용,김나리,김태형,김진국,황승덕 순천향대학교 순천향의학연구소 2008 Journal of Soonchunhyang Medical Science Vol.14 No.1
Purpose: The Number of patients expecting for kidney transplantation and transplantation in foreign countries is rapidly increasing. The infectious complication such as pneumonia has happened commonly during maintenance immunosupression after transplantation. However, there was a lack of information about clinical progresses and outcomes of kidney recipients, underwent cadaveric kidney transplantation in China. Methods: We included 27 patients underwent cadaveric kidney transplantation in China and have been managed at Soonchunhyang University Bucheon Hospital from January 2002 to december 2007. We performed retrospectively study based medical records and clinical analysis for patients with pneumonia. Results: Mean age of 27 patients underwent kidney transplantation was 42.4 10.9 years. One of them didn't experience dialysis before transplantation. Twenty-one and five patients has been treated with hemodialysis and peritoneal dialysis, respectively. The mean dialysis duration was 32.6 ± 23.7 months. Among the causes of end stage renal disease of them, Chronic glomerulonephritis was most common. Post-transplantation follow-up duration was 26.6 ± 10.5 months. During the period above, the number of post-transplantation complication was 19. Pneumonia was most common and next was acute rejection. Ten patients experienced pneumonia at mean 123.7 48.4 day after transplantation. Mean age of them was 44.5 ± 7.8 years, and male to female ratio was 9:1. They had fever and admitted for mean 5.8 ± 4.2, and 19.6 ± 10.9 days, respectively. Seven and 3 patients were diagnosed as Pneumocystis carinii, and cytomegaloviral pneumonia, respectively. Two patients needed mechanical ventilator. One patient with cytomegaloviral pneumonia was expired. Conclusion: We offer informations and problems about kidney transplantation in china, and should be aware of possible complications including pneumonia of recipients undergoing cadaveric kidney transplantation in china.
Peroral Endoscopic Myotomy for Treatment of Achalasia: Initial Results of a Korean Study
이병후,심광연,홍수진,복진현,조준형,이태희,조주영 대한소화기내시경학회 2013 Clinical Endoscopy Vol.46 No.2
Background/Aims: Achalasia is a rare esophageal motility disorder. Recently, a novel endoscopic technique, peroral endoscopic myotomy (POEM), was introduced as an alternative treatment for achalasia. We report the results and short term outcomes of POEM for patients with achalasia. Methods: POEM was performed in 13 patients with achalasia. The procedure consisted of creating a submucosal tunnel followed by endoscopic myotomy of circular muscle bundles. The mucosal entry was closed by conventional hemostatic clips. A validated clinical symptom score (Eckardt score) and high resolution manometry were used to evaluate the outcomes. Results: Both the clinical score of achalasia, as well as the resting lower esophageal sphincter (LES) pressure, were significantly reduced after POEM. Mean post-treatment Eckardt score was 0.4±0.7, compared to 6.4±1.9 prior to the treatment (p=0.001). The mean pre and post-treatment LES pressure was 30.3 and 15.3 mm Hg, respectively (p=0.007). Following POEM, symptomatic relief from dysphagia without reflux symptoms was observed in all patients (13/13). No serious complications related to POEM were encountered. Conclusions: Based upon our initial experience, the authors believe that POEM is a feasible, safe, and effective treatment and may possibly substitute established treatments of refractory achalasia.
Gastric Schwannoma Diagnosed by Endoscopic Ultrasonography-Guided Trucut Biopsy
홍성욱,조원영,김진오,천창균,심광연,복진현,엄욱현,이지은 대한소화기내시경학회 2013 Clinical Endoscopy Vol.46 No.3
Schwannomas of the gastrointestinal (GI) tract are rare subepithelial tumors comprising approximately 3.3% to 12.8% of all mesenchymal tumors of the GI tract. On endoscopic ultrasound (EUS) they are seen as hypoechoic tumors arising most commonly from the 4th proper muscle layer. Although EUS helps to distinguish tumor characteristics, tissue sampling is required for differentiation with other more common tumors such as GI stromal tumors. Both EUS-guided fine needle aspiration and EUS-guided trucut biopsy (EUS-TCB) can be used for tissue sampling. However, only EUS-TCB allows core biopsy and a high yield of immunohistochemical staining. We report a case of a gastric schwannoma diagnosed by EUS-TCB.
신현주 ( Hyun Joo Shin ),심광연 ( Kwang Yeon Shim ),박무용 ( Moo Yong Park ),최수정 ( Soo Jeong Choi ),김진국 ( Jin Kuk Kim ),황승덕 ( Seung Duk Hwang ),권계원 ( Kye Won Kwon ) 대한내과학회 2007 대한내과학회지 Vol.73 No.4
Background: Proteinuria is rarely observed in patients who suffer from thin basement membrane nephropathy (TBMN). Our study was performed to evaluate the clinical characteristics and prognosis of TBMN patients with proteinuria. Methods: We conducted a retrospective study on 231 kidney biopsies. A urine protein level more than 500 mg for the 24-hour urine excretion was considered as significant proteinuria. We studied the clinical characteristics, the pathological findings and the response to treatment of these patients. Results: Ten (4 males and 6 females) of 17 cases of TBMN had significant proteinuria (59%). The mean patient age was 35 years. Six patients had hypertension and 1 patient had nephrotic syndrome. Two patients had proteinuria only, and 8 patients had both hematuria and proteinuria. At the time of biopsy, the amount of urine protein was 1,881 mg per day, and all the patients except one showed normal renal function. The GBM thickness ranged from 201 to 252 nm. Nine patients were treated with angiotensin receptor blocker, and 1 patient suffering from nephrotic syndrome was treated with prednisolone and cyclophosphamide. Marked improvement of the proteinuria (659 mg per day) was observed in 8 patients during the follow-up period. Conclusions: Thin basement membrane nephropathy is one of the causes of proteinuria. Therefore, reduction of the proteinuria should be considered for treating these patients.(Korean J Med 73:407-414, 2007)