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Marfan 증후군에 동반되어 좌우관상동맥확장을 보인 1 예
심대중(Dae Jung Shim),김범수(Bum Soo Kim),강진호(Jin Ho Kang),이만호(Man Ho Lee),박정로(Jeong Ro Park),이상종(Sang Jong Lee),오태윤(Tae Un Oh),장운하(Oun Ha Jang),김명숙(Myung Sook Kim) 대한내과학회 1998 대한내과학회지 Vol.54 No.6
Marfan`s syndrome is a an autosomal dominant disorder of connective tissue that is characterized by ocular, skeletal, and cardiovascular manifestation. It is estimated to have a prevalence of 4-6 per 10,000 people, and at least 25 percent of the cases occur in the absence of a family history. Coronary artery ectasia is a diffuse abnormality of the vessel wall, which has been reported in associated with coronary atherosclerosis, infectious process, congenital heart lesion, syphilis, Ehlers-Danlos syndrome. We reported a case of 25-year-old male who presented with Marfan`s syndrome associated with dissecting ascending arotic aneurysm and diffuse dilatated coronary artery ectasia. Coronary angiographic study demonstrated the diffusely dilatated coronary artery ectasia.
한국인의 인슐린비의존형 당뇨병과 정상 대조군간의 Leptin 농도 차이
김상훈,이화영,김준영,심대중,김신연,정을순,최홍업,최윤상,이상종 대한비만학회 1999 The Korean journal of obesity Vol.8 No.2
Background: Obesity is risk factor for a number of chronic disease, including NIDDM, hypertension, cardiovascular disease. The etiology of obesity is unclear, although it appears that both genetic and enviromental factors contribute to develope. Identification of the ob gene and its product, Leptin, has increased our understanding of the pathophysiology of obesity. Change in glycemia precedes change in body weigth, suggesting that insulin may have a direct effect on Leptin. another, insulin may have a direct effect on Leptin. authors questioned whether NIDDM patients altered regulation of serum Leptin levels. We compared diabetic patients and norrnal persons with serum Leptin level and other metabolic profiles. Methods: Using radioimmunoassay, we measured serum Leptin concentrations in 80 NIDDM patients (male 40, female 40) and 80 controls (male 40, female 40) matched by age, sex and BMI. The data were using t-test of difference in serum Leptin concentration and other factors means between two groups. The association between serum Leptin concentration and other factors were measured by correlation analysis. Results: 1) NIDDM patients had a slightly high body mass index and Leptin concentration than controls, although these were not stastically significant (p$gt;0.05). 2) Women had significant higher Leptin concentration than men (p$lt;0.05). 3) Old age groups had higher Leptin concentrations than young groups (p$lt;0.05), 4) A significant correlation between serum Leptin concentration with age (r=0.173, p$lt;0.05), female sex (r=0.599 p$lt;0,01), BMI (r=0.355, p$lt;0.01) was observed in NIDDM patients. 5) Serum Leptin concentration did not differ by diabetic status. Conclusion: Leptin concentration did not differ by diabetic status. serum Leptin concentrations were significantly correlated with age, sex, BMI. we concluded serum Leptin concentrations were not different in diabetic and non diabetic subjects.
박창영,손정일,김명숙,심대중,전우규,이상종,김병익,편유장,정을순 대한소화기내시경학회 1998 Clinical Endoscopy Vol.18 No.6
Collagenous colitis was first described by Lindstrom in 1976. Now this disorder is recognized as one of the more common causes of chronic diarrhea of obscure origin. This disorder is described as a disease of colon associated with chronic watery diarrhea and the typical histologic findings of a thickened subepithelial collagenous band. But in korea a few cases have been reported. We had observed a 52-year-old businessman with chronic watery diarrhea without abdominal pain in the past. And then we had reported previously that case. We also recently observed a 42-year-old housewife with chronic watery diarrhea with lower abdominal discomfort for 10 years. Colonoscopy disclosed no gross abnormalities through the entire colon ineluding the terminal ileum but we could find the pronounced thickening of subepithelial collageous band and chronic inflammation in the lamina propria in the histologic examination. We summarized the above two cases of collagenous colitis with a review of literatures.
박창영,이승원,김명숙,이만호,심대중,전우규,정을순,이상종,김병익,강진호,김경수 대한소화기학회 1998 대한소화기학회지 Vol.30 No.6
Background/Aims: In Korea, intra-abdominal tuberculosis is decreasing, but still a common curable disease by antituberculous medication and has potency of rebounding prevalence rate due to steadily increasing acquired immunodeficiency syndrome(AIDS). Due to the above reasons and easy accessibility of colonoscopy and laparoscopy, importance of histologic and microbiologic dia- gnosis should be more emphasized. We have conducted this study to observe the clinical characteristics and cere reviewing the literature for better and improved management in this clinical field. Methods: We retrospectively observed 65 patients who had been dignosed with intra- abdominal tuberculosis histologically or microbiologically at Kangbuk Samsung Hospital frorn 1980 to 1996. Results: The most cornmon site of the disease involvement was the terminal ileum(40.0%). 60.0% of the patients were between the ages from 20 and 40. The ratio of male to female was 1:1.2. Clinical symptoms were abdominal pain, diarrhea, general weakness, etc. and the physical signs were abdominal tenderness, abdominal distention, abdominal mass, etc. There was an evidence of pulmonary tuberculosis including pleural effusion and iliary tuberculosis in 70.8% of the patients and cervical tuberculous lymphadenitis in 3.1%. Modalities for definite diagnosis were colonoscopy in 56.9% of the patients, laparoscopy in 26.2% and explo-laparotomy in 16.9%. Results of AFB smear and biopsy showed caseous necrosis in 52 3% of the patients, positive AFB in 31.3% and both in 15.4%. Methods for treatent were antituterculous medication in 84.5% of the patients, surgical resection with antituberculous medication in 9.2% and conservative treatment in 6.2%. Clinical improvement was observed in 96.9% of the patients while 2 of the patients(3.1%) died. Conclusions: As intra-abdominal tuberculosis rnay show indefinite and nonspecific clinical and physical findings, it might be difficult to confirm diagnosis by blood, ascites and imaging studies. Therefore, if suspected, we suggest that histologic and microbiologic approach employing colonoscopy or laparoscopy is in essential step in diagnosing intra-abdominal tuberculosis.
김상훈(Sang Hoon Kim),심대중(Dae Jung Shim),서원태(Won Tae Seo),임시영(Si Young Lim),이승세(Seung Sei Lee),국신호(Shin Ho Kook),금주섭(Joo Seob Keum),오태윤(Tae Yoon Oh),장운하(Woon Ha Chang) 대한내과학회 1999 대한내과학회지 Vol.57 No.1
Epithelioid hemangioendothelioma(EH) is a rare vascular tumor of low-grade malignancy. It was previously described as intravascular bronchioloalveolar tumor (IVBAT). But electron microscopic study and immunohistochemical staining results have proved endothelial origin. Patients are usually asymptomatic and the tumors are found incidentally on routine chest X-rays. Most patients show a slowly progressive clinical course, even though some patients occasionally die as results of respiratory failure or extrathoracic complications. Confirmative diagnosis is made through thoracoscopic or open-lung biopsy. There is still no effective therapeutic modality for pulmonary EH. We have experienced a 55-year-old woman whose simple chest x-ray film revealed bilateral multiple small nodules. The nodules were histopathologically and immunohistochemically diagnosed as primary epithelioid hemangioendothelioma of the lung. The possibility of metastatic disease was excluded thorough clinical, laboratory and radiological studies. Comparison of radiographic chest film taken 3 years ago showed no significant progression of the pulmonary nodular lesions. Conservative management was instituted and careful 4 months follow-up showed no significant changes.