http://chineseinput.net/에서 pinyin(병음)방식으로 중국어를 변환할 수 있습니다.
변환된 중국어를 복사하여 사용하시면 됩니다.
Idiopathic Hypereosinophilic Syndrome Involving Thoracic Spine
Park, Chi-Young,Kim, Seok-Won The Korean Neurosurgical Society 2010 Journal of Korean neurosurgical society Vol.47 No.5
Hypereosinophilic syndrome is a rare hematologic disorder with sustained eosinophilia. Peripheral blood eosinophilia without an underlying etiology and with organs dysfunction has been designated hypereosinophilic syndrome. We report a rare case of symptomatic spinal infiltration of eosinophils at osteolytic T5 in patient with idiopathic hypereosinophilic syndrome.
김영미,이윤진,박재홍,이준우,이창훈 대한간학회 2002 Clinical and Molecular Hepatology(대한간학회지) Vol.8 No.3
저자들은 발열과 우상복부 동통을 주소로 내원 한 5세 남아에서 임상증상과 복부 초음파 검사 및 컴퓨터 단층 촬영에서 간농양으로 생각하고 치료 하던 중에 지속적인 호산구증을 보이고 방사선학적 검사에서 이차적인 간내 병변을 보이고, 기생충 등 다른 질환의 증거를 보이지 않는 환아에서 간 생검으로 호산구의 침착을 확인하고 간을 침범한 특발성 과호산구 증후군을 진단하였기에 문헌 고찰과 함께 보고하는 바이다. Idiopathic hypereosinophilic syndrome is defined as the presence of prolonged eosinophilia without an identifiable underlying cause and with evidence of end-organ dysfunction. The organs involved are the heart, bone marrow, nervous system, lungs, liver, skin, and gastrointestinal tract. Hepatic involvement is found in about 30% of patients of idiopathic hypereosinophilic syndrome. It occurs rarely in infants and children. In this report, we experienced one case of idiopathic hypereosinophilic syndrome with hepatic involvement in a 5-year-old boy who complained of intermittent fever and right upper quadrant abdominal pain. An abdominal ultrasound examination revealed an ill-defined low-echoic lesion in the liver. Pathologic findings of a biopsy specimen clearly showed the infiltration of eosinophils in the liver. Laboratory data disclosed absolute eosinophilia. There was no evidence of allergic disease or parasitic infestation. (Korean J Hepatol 2002;8:321-326)
김성수(Sung Soo Kim),김범수(Pum Soo Kim),이홍복(Hong Bock Lee),류정선(Jeong Seon Ryu),서정기(Jeong Kee Seo),최승원(Seung Won Choi) 대한천식알레르기학회 1998 천식 및 알레르기 Vol.18 No.4
Eosinophilia accompanied by eosinophilic invasion and organ dysfunction may develope idio- pathic hypereosinophilic syndrome. Any organ can be involved including bone marrow, lung, skin, heart, gastrointestinal tract and nervous system. Cough, dyspnea, pleural effusion or chest pain are common pulmonary manifestation, and they may be attributed to parenchymal infiltration, pulmonary embolism or heart failure. We report a 43-year-old woman with idiopathic hypereosinophilic syndrome involving bone marrow, skin, and lung. The patient developed acute dyspnea and chest pain. High resolution CT demonstrated multiple wedge-shaped segmental involvement with pleural effusion thought to be a pulmonary infarction or heart failure. Echocardiography could not find any abnormality. Lung biopsy showed interstitial eosinophilic infiltration with increased eosinophils in BAL fluid. She was treated with high dose corticosteroid and hydroxyurea. Within few days, most of her symptoms disappeared and chest radiography nearly cleared up.
인공 대동맥판막 기능부전을 일으킨 특발성 과호산구 증후군 -1예 보고-
박종빈,유동곤,성규완,정상식,강길현,김종욱 대한흉부외과학회 2007 Journal of Chest Surgery (J Chest Surg) Vol.40 No.4
특발성 과호산구 증후군은 호산구 매개에 의한 조직 손상으로 인해 다발성 장기부전, 특히 심장을 침범하는 드문 전신성, 백혈구증식성 질환이다. 심장침범은 특발성 과호산구 증후군 환자의 75% 이상에서 일어난다. 심장증상은 심내막 하 섬유증, 제한성 심근병증, 판막부전, 그리고 말초동맥 혈전증을 유발하는 혈전이다. 이 질환은 남자에서 여자보다 9:1로 호발하고, 20∼50대에서 주로 발현하는 경향이 있으며 소아에서는 매우 드물다. 인공 대동맥판막부전을 나타낸 특발성 과호산구 증후군 환자(58세, 남자)를 인공판막 재치환 수술 후 부신피질호르몬제와 hydroxyurea 투여로 성공적으로 치료하였기에 보고하는 바이다.
권건영,조승제,박관규,장은숙,Kwon, Kun-Young,Cho, Seung-Che,Park, Kwan-Kyu,Chang, Eun-Sook 대한세포병리학회 1990 대한세포병리학회지 Vol.1 No.2
Bronchoalveolar lavage (BAL) has emerged as a useful technique for the study of pulmonary interstitial disorders. Several types of Information are provided by the evaluation of lavage fluid identification of cellular constituents helps to separate inflammatory process. Recently we have studied cellular constituents of BAL from three cases with histologically confirmed pulmonary sarcoidosis, idiopathic pulmonary fibrosis and hypereosinophilic syndrome. Pulmonary sarcoidosis showed a marked increase in lymphocytes, idiopathic pulmonary fibrosis revealed a predominance of neutrophils, and hypereosinophilic syndrome presented a marked increase in eosinophils in the lavage fluids.
증례보고 : 특발성 과호산구 증후군 환자의 마취경험 -증례보고-
조혜란 ( Hye Ran Cho ),한상지 ( Sang Ji Han ),권영은 ( Young Eun Kwon ),이준학 ( Jun Hak Lee ) 대한마취과학회 2007 Korean Journal of Anesthesiology Vol.52 No.6
Idiopathic hypereosinophilic syndrome is characterized by prolonged markedly elevated peripheral blood eosinophil count and eosinophil-related tissue damage to variable organs without an identifiable underlying cause. Eosinophilopoiesis is related with T-lymphocyte activation and cytokine cascade controlling eosinophilic production. It shows tissue infiltration in many organs including endomyocardium, lung, liver, gastrointestinal tract. Here we report a case of idiopathic hypereosinophilic syndrome presenting ruptured rectus sheath hematoma due to coagulopathy involving the liver. Severe postoperative complications were developed after general anesthesia. The patient suffered from life-threatening acute respiratory distress syndrome (ARDS). This case suggest that, in patients with marked eosinophilia requiring general anesthesia, perioperative steroid cover is advisable. This may reduce or prevent serious lung damage and other complications. (Korean J Anesthesiol 2007; 52: 728~32)
A Case of Idiopathic Hypereosinophilic Syndrome Presenting With Acute Respiratory Distress Syndrome
임경숙,고재훈,이성수,신범수,최동철,이병재 대한천식알레르기학회 2014 Allergy, Asthma & Immunology Research Vol.6 No.1
Although idiopathic hypereosinophilic syndrome(IHES) commonly involves the lung, it is rarely associated with acute respiratory distress syndrome (ARDS). Here we describe a case of IHES presented in conjunction with ARDS. A 37-year-old male visited the emergency department at Samsung Medical Center, Seoul, Korea, with a chief complaint of dyspnea. Blood tests showed profound peripheral eosinophilia and thrombocytopenia. Patchy areas of consolidation with ground-glass opacity were noticed in both lower lung zones on chest radiography. Rapid progression of dyspnea and hypoxia despite supplement of oxygen necessitated the use of mechanical ventilation. Eosinophilic airway inflammation was subsequently confirmed by bronchoalveolar lavage, leading to a diagnosis of IHES. High-dose corticosteroids were administered, resulting in a dramatic clinical response.