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이선미,정지한,안명임,조덕곤,이교영,강석진 대한병리학회 2008 Journal of Pathology and Translational Medicine Vol.42 No.6
Malignancies in congenital cystic adenomatoid malformations (CCAMs) of the lung are rare. We report a 41-year-old male patient with a pulmonary cystic lesion suspicious for CCAM, unrecognized until the patient was 40 years of age, and which subsequently became more consolidated during the interval between initial presentation and surgery. Microscopic examination of the resected specimen revealed features of type 1 CCAM with a mucinous adenocarcinoma, metastatic to the mediastinal lymph nodes. This case illustrates the importance of prompt surgical resection for all suspected CCAMs, especially those discovered in adulthood.
장기경 대한흉부심장혈관외과학회 1995 Journal of Chest Surgery (J Chest Surg) Vol.28 No.7
Congenital cystic adenomatoid malformation[CCAM of the lung is extremely rare. We have experienced an unusual case of congenital cystic adenomatoid malformation. The patient was 20-year-old male and had chest pain for 10 days. On simple chest x-ray and Thoracic CT scan, there was a large cystic mass surrounded with multiloculated round cysts with air fluid level on the right lower lobe of a lung. Right lower lobectomy was performed and the pathologic result was congenital cystic adenomatoid malformation.
이정희,임진수,최형호,Lee, Jeong-Hui,Im, Jin-Su,Choe, Hyeong-Ho 대한흉부심장혈관외과학회 1993 Journal of Chest Surgery (J Chest Surg) Vol.26 No.4
Congenital cystic adenomatoid malformation [CCAM] of the lung is extremely rare. The patient was 10 year old female and had no specipic signs and symptoms except right lower chest pain for 5 days ago before admission.On simple chest X-ray and thoracic CT scan, about 9x8x8cm sized, heterogenous marginal enhanced multiseparated hypodence lesion with air fluid level and gas bubbles in posterior pleural space in right lower chest .The culture result of needle aspiration of cavity was apergillus flavus. Right lower lobectomy was carried out and the result of biopsy was congenital cystic adenomatoid malformation.
Congenital, Cystic Adenomatoid Malformation을 보이는 복강내 폐분리증
이석구,이우용,김현학,Lee, Suk-Koo,Lee, Woo-Yong,Kim, Hyun-Hahk 대한소아외과학회 1996 소아외과 Vol.2 No.2
Pulmonary sequestration is a complex anomaly involving the pulmonary parenchymal tissue and its vasculature. It presents as a cystic mass of nonfunctional lung tissue without communication with the tracheobronchial system. Usually, it receives blood supply from anomalous systemic vessels. Therefore, preoperative diagnosis of the pulmonary sequestration is difficult, especially when it is located in the abdomen and combined with congenital cystic adenomatoid malformation(CCAM). We encountered such a mass(CCAM type 2) detected prenatally by ultrasonography. It was a kidney bean shaped, pinkish mass straddling the thorax and abdomen on the right side. Because of the sonographic appearance, neuroblastoma was diagnosed preoperatively. The mass was completely extirpated without difficulty.
류현미 ( Lyu Hyeon Mi ),양재혁 ( Yang Jae Hyeog ),최규홍 ( Choe Gyu Hong ),송미진 ( Song Mi Jin ),이영호 ( Lee Yeong Ho ),김문영 ( Kim Mun Yeong ),김은중 ( Kim Eun Jung ),김진홍 ( Kim Jin Hong ) 대한산부인과학회 2003 Obstetrics & Gynecology Science Vol.46 No.8
Objective : Our purpose was to study the outcome of pregancy with a prenatal diagnosis of fetal congenital cystic adenomatoid lung malformation. Methods : A retrospective study was performed of all cases with a prenatal diagnosis of fetal CCALM from Janua
Joo Hee Lim,Jungho Han,신정은,은호선,이순민,박민수,남궁란,박국인 대한신생아학회 2019 Neonatal medicine Vol.26 No.3
Purpose: Congenital pulmonary airway malformation (CPAM)-a rare developmental anomaly-affects the lower respiratory tract in newborns. By comparing the reliability of diagnostic tools and identifying predictive factors for symptoms, we provide comprehensive clinical data for the proper management of CPAM. Methods: We reviewed the medical records of 66 patients with prenatally diagnosed CPAM delivered at Severance Children’s Hospital between January 2005 and July 2017. Results: We enrolled 33 boys and 33 girls. Their mean gestational age and birth weight were 38.8 weeks and 3,050 g, respectively. Prenatal ultrasonography and postnatal radiography, lung ultrasonography, and chest computed tomography (CT) showed inconsistent findings. Chest CT showed superior sensitivity (100%) and positive predictive value (90%). Among the 66 patients, 59 had postnatally confirmed CPAM, three had pulmonary sequestration, one had cystic teratoma, and one had a normal lung. Of the 59 patients with CPAM, 21 (35%; mean age, 23.4 months) underwent surgery, including 15 who underwent video-assisted thoracoscopy. Twenty-five and 12 patients exhibited respiratory symptoms at birth and during infancy, respectively. Apgar scores and mediastinal shift on radiography were significantly associated with respiratory symptoms at birth. However, none of the factors could predict respiratory symptoms during infancy. Conclusion: Radiography or ultrasonography combined with chest CT can confirm an unclear or inconsistent lesion. Apgar scores and mediastinal shift on radiography can predict respiratory symptoms at birth. However, symptoms during infancy are not associated with prenatal and postnatal factors. Chest CT combined with periodic symptom monitoring is important for diagnosing and managing patients with prenatally diagnosed CPAM and to guide appropriate timing of surgery.
누두흉과 선천성 낭종성 선종양 기형의 최소 침습적인 동시수술 -1예 보고-
조덕곤,조민섭,조규도,김경수,왕영필 대한흉부외과학회 2006 Journal of Chest Surgery (J Chest Surg) Vol.39 No.2
최소 침습성 흉부수술은 최근에 가장 발전되어온 중요한 수술의 한 분야이다. 선천성 낭종성 선종양 기형은 비교적 드물게 발생하는 폐질환으로 누두흉, 선천성 심장 및 폐혈관 질환 같은 여러 가지 선천성 기형 등이 동반될 수 있다. 저자들은 우하엽 폐에 선천성 낭종성 선종양 기형이 있으며 누두흉이 동반된 5세 된 남아 환자를 최소 침습적인 방법으로 치료 경험하였다. 저자들은 흉강경을 이용하여 우하엽 폐절제술을 실시하였고, 동시에 누두흉에 대해서는 흉골 하 금속막대를 이용한 너스 술식으로 교정하였다. 이와 같이 이러한 질환에 대한 최소 침습적인 수술방법은 유용하고 미용적으로 우수하다.
( Ju Hyun Ryu ),( Hyun Hwa Cha ),( Suk Joo Choi ),( Soo Young Oh ),( Cheong Rae Roh ),( Jong Hwa Kim ) 대한산부인과학회 2011 Obstetrics & Gynecology Science Vol.54 No.7
This study is to investigate and compare the pregnancy outcomes and prognostic factors of congenital cystic adenomatoid malformation (CCAM) and bronchopulmonary sequestration (BPS). Methods From May 2005 to September 2010, fifty-five medical records of fetuses with prenatally diagnosed CCAM (42 cases) and BPS (13 cases) were reviewed retrospectively in Samsung Medical Center (SMC). We compared the demographic characteristics, sonographic findings, postnatal diagnoses and pregnancy outcomes between CCAM and BPS. The sonographic findings included the locations of lesion, changes of size, existences of mediastinal shift, associated anomalies and existences of hydrops. Postnatal diagnoses were confirmed by pathologic findings and image examinations. Results A total of fifty-five cases were prenatally diagnosed as CCAM (42 cases) and BPS (13 cases). Thirty cases were followed up in SMC. Three of the thirty cases underwent termination and one case was intrauterine fetal death. Twenty-six cases were delivered alive in SMC. The masses were found out to be disappeared by prenatal sonography in four cases (15.4%) who were antenatally diagnosed as CCAM. The sizes of the mass were decreased more than 50% in CCAM seven cases and BPS three cases. The absence of mediastinal shift ( P=0.019) was significantly correlated with the decrease of mass size. Conclusion The concordance rate between antenatal and postnatal diagnosis was 63.0%. There was a tendency of decreasing in lesion with most of the cases. Without mediastinal shift, the mass size decreased significantly. So, existence of mediastinal shift is the most important prognostic factor of CCAM and BPS.
이동희,김천수,박근수,김명성,권태찬,이희정,서수지,이상숙,박창권,유영선 啓明大學校 醫科大學 1997 계명의대학술지 Vol.16 No.1
Congenital cystic diseases of the lung(CCDL) is a clinical group of disorders characterized by a cystic appearance of pulmonary tissue. It can be classified into four distinct categories:Congenital lobar emphysema(CLE), Congenital cystic adenomatoid malformation(CCAM), Pulmonary sequestration(PS), and Bronchogenic cyst(BC). 17 patients with congenital cystic diseases of the lung admitted to the Department of Pediatirics, Keimyung University, Dongsan Hospital from January, 1986 to December, 1995 were investigated for their pathologic classification, clinical characteristics, diagnostic measures and treatment outcome. The results were as follows: 1) 17 cases of CCDL were classified pathologically into four distinct categories: BC 8 cases, PS 5 cases(intralobar 4 cases, extralobar 1 case), CCAM 4 cases. 2) CCDL were seen more commonly in males. 3) In age distribution, 64.7% of CCDL were diagnosed at over 6 years. 4) In BC and PS, right lower lobe was the most frequent site affected. 5) The most frequent presenting symptoms were respiratory distress and recurrent respiratory infection. 6) Chest radiographic findings were quite effective in differentiating cystic lesions of the lung from other conditions. 7) Associated anomalies were obserbed in 4 cases (23.5%). 8) In the symptomatic patient, prompt surgical treatment was recommended. 9) Surgical treatment was quite effective and safe.
박명규 大韓應急醫學會 1997 대한응급의학회지 Vol.8 No.1
Congenital cystic adenomatoid malformation is rare form of disease causing in the lung. The main symptoms and signs are cyanosis, tachypnea, and other form of respiratory distress at or shortly after birth. In auscultation, decreased breath sound is audible and in chest X-ray, shifting of mediastinum, pulmonary herniation and depression of diaphragm are visualized with cystic shadow. We have experienced a case of cystic adenomatoid malformation of lung. After emergency operation, patients were recovered uneventfully.