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호흡부전과 신경학적 이상을 동반한 Acute Intermittent Porphyria
전대원(Dae Won Jun),최춘식(Choon Shik Choi),최호순(Ho Soon Choi),전용철(Yong Chul Jung),손주현(Joo Hyun Sohn),한동수(Dong Soo Han),윤병철(Byung Chul Yoon),함준수(Joon Soo Hahm),이민호(Min Ho Lee),이동후(Dong Hoo Lee),기춘석(Choon Shu 대한소화기학회 2000 대한소화기학회지 Vol.36 No.3
The acute intermittent porphyria (AIP) is characterized biochemically by increased excretion of porphyrins and porphyrin precursors, S-aminolevulinic acid (ALA) and porphobilinogen (PBG). AIP presents with abdominal pain, mental disturbances and neurologic dysfunction. A 24-year-old woman with a medical history of AIP was admitted to our hospital because of abdominal pain and proximal muscle weakness. She was treated by carbohydrate loading with intravenous glucose. Twenty five days later, she developed tachycardia, fluctuation of blood pressure and syndrome of inappropriate secretion of antidiuretic hormore (SIADH). On 90th day, intubation was required to control her breathing. Complete flaccid paralysis developed, and the patient became comatose. The neurologic effects of acute porphyria are generally reversible, but the clinical course of severe case is complicated with respiratory failure, fluid electrolyte imbalance. AIP should be considered in differential diagnosis of patient with unexplained respiratory failure. (Kor J Gastroenterol 2000;36:413 - 418)
백상현 ( Sang Hyun Baik ),함준수 ( Jun Soo Hahm ),전용철 ( Young Chul Jeoun ),이오영 ( O Young Lee ),이민호 ( Min Ho Lee ),기춘석 ( Chun Suk Ki ),박준용 ( Jun Yong Park ),은창수 ( Chang Soo Eun ),한동수 ( Dong Su Han ) 대한소화기학회 2002 대한소화기학회 춘계학술대회 Vol.2002 No.-
〈배경〉 현재까지 담석의 증가와 연관성을 가진 병적인 상태를 찾고자하는 연구가 진행되어 왔다. 대개의 류마치스 관절염환자는 NSAID를 복용하고 있는 자가 많고, 동물 실험을 NSAID가 담석 생성과 관련이 있음이 발표되기도 하였다. 본 연구에서는 류마치수 관절염환자에서의 담석의 빈도를 제시하고 matched control과의 여러 다른 기준척도등의 비교를 통해 이들간의 유의성을 비교하였다. 〈연구대상 및 방법〉 한양대 류마치스 병원에 입원하였던 선별검
간 이식 후 합병된 담관 원주 증후군에 의한 폐쇄성 황달
백상현 ( Sang Hyun Bak ),최호순 ( Ho Soon Choi ),양선영 ( Sun Young Yang ),전대원 ( Dae Won Jun ),한성희 ( Sung Hee Han ),이항락 ( Hang Lak Lee ),이오영 ( Oh Young Lee ),윤병철 ( Byung Chul Yoon ),함준수 ( Jun Soo Hahm ),이민호 ( 대한소화기학회 2006 대한소화기학회지 Vol.48 No.2
Biliary complication occurs in 6-34% of all liver transplant patients. Although bile leaks and strictures are relatively common, other biliary complications such as T-tube leak, choledocholithiasis, and biliary cast syndrome can also be observed. The biliary cast syndrome describes the presence of casts causing obstruction with its resultant sequelae of biliary infection, hepatocyte damage secondary to bile stasis and ductal damage, all contributing to cholangiopathy. Because the exact timing of cast formation after orthotopic liver transplantation is not consistent, it is difficult to define the true incidence of biliary cast syndrome without long-term follow-up data. Proposed etiological mechanisms include acute cellular rejection, prolongation of cold ischemic time, infection, biliary drainage tubes, and biliary obstruction. The diagnosis of biliary cast syndrome is usually confirmed by endoscopic retrograde cholangiopancreatography. There have been few published articles about biliary casts in Korea. Herein, we report a case of biliary cast syndrome followed by orthotopic liver transplantation. (Korean J Gastroenterol 2006;48:119-123)
위절제술이 골대사 및 골밀도에 미치는 영향 - 예검법으로서 의미있는 지표
권성준(Sung Joon Kwon),신동일(Donng Ill Shin),원치규(Chi Kyooh Won),전규영(Kyu Young Jun),곽진영(Jin Young Kwak),이광수(Kwang Soo Lee),정파종(Pa Jong Jung),안유헌(Yoo Hern Ahn),함준수(Joon Soo Hahm),김목현(Mok Hyun Kim) 대한소화기학회 1996 대한소화기학회지 Vol.28 No.2
N/A Background/Aims: Abnormalities of bone metabolism occur to gastrectomised patients in the form of a late complication. Nowadays, many biochemical and radiologic measurements are applied to detect these abnormalities. The aim of this study was to determine the parameter for an appropriate screening test during the long-term follow-up period and define the usefulness of new biochemical markers for bone metabo]ism by comparing them with traditional markers. Methods: Among the patients gastrectomised(Billroth II) in the surgica] department of Hanyang University Hospital since 1982, 10 patients were randomly selected with exclusion criteria by measuring several biochemical and radiologic tests. Ten age-matched volunteers who led a healthy normal life were selected with the consent of subjects. Results: Comparing the data with those of a corresponding control group, the ]umbar bone density tneasured by quantitative cornputed tornography(QCT) was statistically significantly lower in the patient group(p0.01). In addition, urinary deoxypyridinoline (DPD), a biochemical marker for bone resorption, was statistica]ly higher in the patient group(p -0.025). Osteocalcin, P1CP, and 1CTP were slightly but not significant]y bigher in the patient group. The serum PTH and 25-hydroxyvitamin D levels were sitnilar in both groups. Conclusiions: Although the nurnber of cases was smal] for data evaluation, we suggest that urinary deoxypyridinoline and QCT were appropriate parameters for tbe screening test for the detection of bone metabolism abnormalities in gastrectomised patients during the long-term follow-up. Furthermore, urinary deoxypyridinoline is a simple and rapid test which can replace cumbersome 24-hour urinary hydroxypro]ine. (Korean J Gastroenterol 1996; 28:172 178)
간장 및 담도 : E . R . C . P . 시행 전 , 후의 T . L . I . ( Trysin Like Immunoveactivity ) 와 Amylase 의 상관관계
이동후(Dong Hoo Lee),박경남(Kyung Nam Park),이민호(Min Ho Lee),배상철(Sang Cheol Bae),이성구(Seong Koo Lee),함준수(Jun Soo Hahm),이종철(Jong Cheol Lee),기춘석(Chun Suk Kee) 대한소화기학회 1986 대한소화기학회지 Vol.18 No.2
N/A Serum TLI and Amylase were studied in 20 patients before and after endoscopic retrograde cholangiopancreatography. None of the patients develops clinical acute pancreatitis. Significant increase in serum TLI and Amylase was found after ERCP (p<0.05). Serum TLI peak was observed at 1 hour and Amylase peak at 6 hours. A significant linear relation was found between serum TLI and Amylase 1, 6, 24 hours after the examination.
함준수,Shimizu, Shuji,Nakashima, Naoki,변태준,이항락,최호순,고용,이경근,김선일,김태은,윤지원,박용진 대한소화기학회 2004 대한소화기학회지 Vol.43 No.6
목적: 인터넷에 기초한 기술의 발달이 사회 전 분야의 발전을 가능하게 하였으며 특히 의료 분야의 자동화와 정보화가 이루어졌다. 많은 임상 의사가 원격 교류를 통해서 원격진료가 가능하게 되었으나 아직은 많은 제한점이 있다. 이 연구의 목적은 디지털 영상 전송 시스템을 사용함으로써 고화질의 영상을 가능하게 해 결국 원격진료 교육에 도움을 주고자 시작하였다. 대상 및 방법: 본 프로젝트는 정보통신부 산하 한국전산원의 지원으로 구축된 KJCN,KOREN (Korea advanced research network)의 활용을 위해현해/겐카이 프로젝트의 부프로젝트로 시작되었다. 일본과의 네트워크를 위해 KJCN의 케이블을 부산과 후쿠오카 사이 300 km 거리의 해저에 설치하였으며, 부산과 서울 한양대학교 사이의 약 300 km 거리는 KOREN을 이용하여 연결하였다. 기본적인 장비를 수술실과 세미나실에 설치하여 수술 현황을 세미나실에서 토의할 수 있도록 하였으며, 일본 후쿠오카의 큐슈대학병원과 네트워크를 연결하였다.2003년 2월 12일 최초로 한양대학병원과 일본 큐수대학병원간의 화상회의로 시작하였다. 결과: 수술 영상을 전송하여 의료진들은 각 회의에서 한 시간 또는 두 시간 동안 외과적 과정에 대해 서로 토론했고 이미지의 질은 원본 디지털 영상과 비교하여 차이가 없었고 일반 영상보다 뛰어났다. 수술시 해부 구조를 명확하게 인식할 수 있었고 그 과정도 잘 이해할 수 있었으며 실시간 전송에 이용된 수술은복강경 담낭제거술과 전립선제거술이었다. 이와 같이 인터넷 프로토콜 기반의 DVTS을 이용한 동영상의 전송은 성공리에 진행되었고 환자의 병력과 수술전의 상태 또한 정지 화상으로 볼 수 있었다. 결론: 본 연구는 인터넷을 통해 해외의 고화질의 영상 전송 시스템을 개발하였으며 이 시스템은 경제적이며 시행하기 쉬우므로 향후 원격진료에 유용한 방법이 될 것으로 생각한다. Background/Aims: The growth of technology based on internet protocol has affected on the informatics and automatic controls of medical fields. The aim of this study was to establish the telemedical educational system by developing the high quality image transfer using the DVTS (digital video transmission system) on the high-speed internet network. Methods: Using telemedicine, we were able to send surgical images not only to domestic areas but also to international area. Moreover, we could discuss the condition of surgical procedures in the operation room and seminar room. The Korean-Japan cable network (KJCN) was structured in the submarine between Busan and Fukuoka. On the other hand, the Korea advanced research network (KOREN) was used to connect between Busan and Seoul. To link the image between the Hanyang University Hospital in Seoul and Kyushu University Hospital in Japan, we started teleconference system and recorded image-streaming system with DVTS on the circumstance with IPv4 network. Results: Two operative cases were transmitted successfully. We could keep enough bandwidth of 60 Mbps for two-line transmission. The quality of transmitted moving image had no frame loss with the rate 30 per second. The sound was also clear and the time delay was less than 0.3 sec. Conclusions: Our study has demonstrated the feasibility of domestic and international telemedicine. We have established an international medical network with high-quality video transmission over internet protocol. It is easy to perform, reliable, and also economical. Thus, it will be a promising tool in remote medicine for worldwide telemedical communication in the future. (Korean J Gastroenterol 2004;43:370-375)
강준구,안유헌,박준성,이창범,박용수,김동선,최웅환,김태화,함준수,박용욱,홍은경 대한내분비학회 2002 Endocrinology and metabolism Vol.17 No.2
Many endocrinologic diseases can induce muscular diseases. Myopathy caused by exogenous steroid is a common problem in patients prescribed steroids as therapy. We report a case of iatrogenic steroid myopathy in a 55-year-old female who had taken steroids under her own volition at a local pharmacy for more than 3 months due to skin rash and itching. She complained of severe proximal muscle wasting and weakness in the lower extremities and also exhibited other stigmata of Cushing's syndrome such as moon face, buffalo hump or easy bruising. Needle electromyography showed the typical pattern of myopathy. Muscle biopsy revealed intermixed numerous, markedly atrophic and angulated basophilic fibers and a few fat cells without inflammation. In addition there was marked and selective atrophy of type II fiber on ATPase staining in pH 9.4 buffer. After discontinuation of steroid treatment, she has experienced slow improvement through physical therapy, including isotonic exercise