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Hb Dieppe에 의한 우성유전 베타 지중해빈혈 1례
최유경,이홍진,박원일,이경자,강성하,김지연,박성섭,Choi, You Kyoung,Lee, Hong Jin,Park, Won Il,Lee, Kyung Ja,Kang, Sung Ha,Kim, Ji Yeon,Park, Sung Sup 대한소아청소년과학회 2002 Clinical and Experimental Pediatrics (CEP) Vol.45 No.5
저자들은 상염색체 우성으로 유전되는 경한 저색소성 소구성 빈혈을 보이고 ${\beta}$ 유전자의 127번째 코돈 이 CAG에서 CGG로 치환되는 과오돌연변이로 인하여 매우 불안정한 베타 사슬 변이체를 만드는 우성유전 베타 지중해빈혈을 경험하였기에 문헌고찰과 함께 보고하는 바이다. ${\beta}$ thalassemias are usually transmitted as autosomal recessive traits. However, some dominant forms of ${\beta}$ thalassemia have been identified in individuals who have inherited a single copy of an abnormal ${\beta}$ globin gene. Thalassemia intermedia with mild anemia, jaundice, and splenomegaly has been observed in these patients. Electrophoresis has shown elevated Hemoglobin(Hb) $A_2$ and Hb F levels. In particular, there are inclusion bodies in the erythroid precursors and peripheral red blood cells after splenectomy. The molecular basis of these dominant ${\beta}$ thalassemias is heterogeneous. The authors studied the first Korean case of dominantly inherited ${\beta}$ thalassemia due to Hb Dieppe. Hb Dieppe is a missense mutation of ${\beta}$ codon $127(CAG{\rightarrow}CGG)Gln{\rightarrow}Arg$. The patient in this case was characterized by moderate anemia, hypochromia, microcytosis, elevated Hb $A_2$ levels, elevated Hb F levels and splenomegaly. The father of the patient also has the same disease. We report this case and review related literature.
초등 교사들의 온라인상에서의 수업자료 공유에 대한 사례연구
서경혜 ( Kyoung Hye Seo ),최유경 ( You Kyung Choi ),김수진 ( Su Jin Kim ) 한국초등교육학회 2011 초등교육연구 Vol.24 No.2
In recent years, increasing number of teachers have participated in online teacher communities and shared their instructional materials in order to improve their teaching. However, little has been known what kinds of instructional materials teachers share online. The present study explored teachers` sharing of instructional materials in online teacher communities. For this purpose, Indischool, an online teacher community, was selected and what kinds of instructional materials were shared in indischool online teacher community was examined. The findings showed that, first, teachers shared a variety of instructional materials including PowerPoint presentation files, multimedia materials, student learning activity sheets, exercise sheets, and so on. Second, teachers` instructional materials focused on how to deliver the textbook contents to students. In particular, the instructional materials effective to draw students` attention were popular among teachers. Third, teachers` instructional materials were mostly finished products so that teachers could use them immediately without further revision or modification. Further, most of them were one-shot use. These features of instructional materials seemed to reflect the circumstances of elementary school teachers who taught more than 10 subject matters and different grades almost every year. Based on these findings, how to respond to the teachers` needs for instructional materials and support teachers` efforts to improve their teaching was discussed.
비당뇨병성 말기신부전증 환자에서 양측성 기저핵 병변과 소뇌 병변을 동반한 요독성 뇌병증
심성록 ( Soung Rok Sim ),이상훈 ( Sang Hun Lee ),장재훈 ( Jae Hoon Jahng ),임재윤 ( Jae Yun Lim ),최유경 ( You Kyoung Choi ),배기선 ( Ki Sun Bae ),박우일 ( Woo Il Park ),김기중 ( Ki Joong Kim ),이경열 ( Kyung Yul Lee ),박형천 ( Hy 대한신장학회 2006 Kidney Research and Clinical Practice Vol.25 No.6
Involvement of central nervous system is a well-known compication in uremic patients. However, development of acute extrapyramidal symptoms with bilateral basal ganglia involvement (acute basal ganglia syndrome), especially in non-diabetic hemodialysis patient is very rare. We report a case of acute basal ganglia syndrome in a non-diabetic hemodialysis patient. A 45-year-old man with autosomal dominant polycystic kidney disease (ADPKD) on chronic hemodialysis treatment for the last 4 years was admitted due to generalized myalgia. On admission, the patient was found to have rhabdomyolysis and intractable metabolic acidosis. Nine days after admission, he suddenly developed dysarthria, lateralizing ataxia, and bradykinesia. Brain MRI demonstrated low and high signals in bilateral basal ganglia and cerebellar vermis in T1-weighted and T2-weighted images, respectively. Intensified hemodialysis treatment combined with general supportive therapy resolved the severe metabolic acidosis and the neurologic manifestations gradually improved. Follow up brain CT scan taken 3 months later showed decreased size of initial low attenuation lesions in bilateral basal ganglia and cerebellar vermis. Although no definite pathophysiology is yet established, severe metabolic disorder is believed to play an important role in development of acute basal ganglia syndrome. Correction of metabolic acidosis and hypoglycemia in our patient lead to improvement in neurologic manifestations and organic brain lesions. Our case suggests that severe metabolic acidosis and hypoglycemia in uremic patient may act as risk factors for acute basal ganglia syndrome even in non-diabetic patient. (Korean J Nephrol 2006;25(6):1061-1066)
최유경,임재윤,이상훈,심성록,제현철,김명수,김준명,송영구 대한감염학회 2006 감염과 화학요법 Vol.38 No.5
저자들은 척추뼈에 발생한 침습적 Aspergillus 감염증을 수술과 항생제 치료로 치료한 1예를 경험하였기에 문헌 고찰과 함께 보고하는 바이다. Invasive aspergillosis has been reported in patients with profound neutropenia or patients with any form of immunodeficiency. Bone aspergillosis remains a rare. Herein, as we had experienced one case of bone aspergillosis patient treated with voriconazole, we report it with the review of literature.
최유경,김혜진,임재윤,심성록,이상훈,윤희정,김명수,송영구,김준명 대한감염학회 2006 감염과 화학요법 Vol.38 No.5
2명의 간경변 환자에서 비브리오균혈증을 경험하였다. 1명은 구토와 설사 등의 장염 증세로 내원하여 혈액배양검사에서 비브리오균이 검출되었다. 다른 환자는 설사를 주소로 내원하였고 다리에 수포성 병변도 같이 발생하였고 혈액배양 검사에서 비브리오균이 검출되었다. 두 환자 모두 수액과 항생제 치료로 증세 호전되고 혈액배양검사 음전되어 퇴원하였다. We have experienced two cases of bacteremia in liver cirrhosis patients caused by Vibrio parahemolyticus. One presented with acute gastroenteritidis symptoms such as vomiting, diarrhea. Vibrio parahemolyticus was cultured in the blood. In the other patients showed vesicular rash in lower extremities with a positive blood culture. Both patients had been treated with intravenous fluid and antibiotics.
Salmonella choleraesuis 감염에 의한 흉부 농양 1예
황도유,최유경,임재윤,제현철,김명수,김준명,송영구 대한감염학회 2007 감염과 화학요법 Vol.39 No.1
저자들은 17세의 양성 흉선종을 동반한 남자 환자에서 Salmonella choleraesuis에 의한 흉부 농양을 경험하였기에 문헌고찰과 함께 보고하는 바이다. Salmonella are motile, gram-negative, non-spore-forming members of the family Enterobacteriaceae. Among nontyphoid Salmonella serotypes, Salmonella choleraesuis shows a high predilection to cause systemic infections in humans. Thoracic infection is a rare complication of Salmonella infection. So far, most of reported cases of empyema caused by Salmonella spp. have involved immunocompromised patients. Herein, as we had experienced one case of thoracic empyema due to Salmonella choleraesuis related thymoma, we report it with review of literature.