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오윤경(Yoon Kyeong Oh),박희철(Hee Chul Park),기근홍(Keun Hong Kee),전호종(Ho Jong Jeon),박유환(You Hwan Park),정춘해(Choon Hai Chung) 대한방사선종양학회 2000 Radiation Oncology Journal Vol.18 No.4
자궁 평활근육종의 경부림프절로의 전이는 지금까지 보고되지 않았으며 타 부위로의 전이 시에도 방사선치료는 드물게 이용되어왔다. 저자들은 자궁 평활근육종 환자에서 수술과 골반부 방사선치료를 시행 받고 10개월 후에 경부림프절 전이가 발생하여 인접한 후두주위공간, 척추골, 척추관을 함께 침습하였기에 방사선치료와 화학요법의 경험과 함께 보고하는 바이다. 전이된 종양은 수술이 불가능하여 방사선치료가 의뢰되었으며 총 6,000 cGy의 경부 방사선치료와 taxol과 carboplatin으로 화학요법을 시행하였다. 전이 암은 점차로 크기가 감소하여서 거의 만져지지 않을정도로 되었다. 환자는 경부 방사선치료와 화학요법을 시행 받은 후 8개월간 척수압박증상을 발생하지 않았고, 연하곤란은 회복되어서 좋은 상태를 유지하였다. 광범위한 경부전이 암이 고선량 경부방사선치료와 화학요법에 좋은 국소 반응을 보였기에 수술이 불가능한 전이성 평활근육종 환자에서 이 두 가지 치료법이 고려될 수도 있겠다. The metastasis of uterine leiomyosarcoma to the neck node has not been reported previously and the radiotherapy has been rarely used for the metastatic lesion of the other sites. We report a case of neck metastasis from a uterine leiomyosarcoma, which developed 10 months after surgery and postoperative pelvic radiotherapy. It also involved the parapharyngeal space, adjacent spine, and spinal canal. The metastatic neck mass was inoperable, and was treated by neck radiotherapy (6,000 cGy) and chemotherapy including taxol and carboplatin. The mass has regressed progressively to a nearly impalpable state. She has never developed spinal cord compression syndrome, and has maintained good swallowing for eight months since the neck radiotherapy and chemotherapy. Since the extensive metastatic neck mass showed good local response to high dose radiotherapy and chemotherapy, both treatments may be considered for an unresectable metastatic leiomyosarcoma.
척수압박으로 발현된 급성 골수성 백혈병에 동반된 과립구성 육종 1 례
윤상준,김영곤,김희종,박유환,정춘해,김양수,김태균,박영진,전호종 조선대학교 부설 의학연구소 2000 The Medical Journal of Chosun University Vol.25 No.1
저자들은 척수압박으로 하지마비를 보인 환자에서 수술 후에 급성 백혈병에 동반된 과립구성 육종으로 진단된 환자 1례를 경험하였기에 문헌고찰과 함께 보고하는 바이다. Granulocytic sarcoma(GS) is an uncommon tumor composed of immature cells of the granulocytic series. Most case of GS occur in the course of acute leukemia and the blast crisis of chronic leukemia, Rarely, however, it may present before leukemia becomes clinically apparent. It may also occur in patients with myeloproliferative disoders. GS has been reported that it occurs in 3% to 9% of patients with acute myelogenous leukemia(AML) and the incidence of GS is reported to be higher in patients with t(8;21). GS occurs relatively commonly in africa and has been reported to affect 10-25% of black children presenting with AML. This is very rare case of granulocytic sarcoma with AML(FAB M5) presented with spinal cord compression which was supported by decompression laminectomy.
이기주,이봉규,정중화,이만재,전용준,박유환,정춘해 朝鮮大學校 附設 醫學硏究所 1997 The Medical Journal of Chosun University Vol.22 No.2
A 16-years-old-girl was presented with chief complaints of dizziness and exertional dyspnea. She was tall 146 cm (less than the fifth percentile) and sexually developed normally. But she experienced intermittent menorrhagia. She had a shield chest, a low-set nuchal hairline and a short left metatarsal bone. There were no other dysmorphic facial features, no webbed neck, no cubitus valgus, & no mental retardation. The blood hemoglobin was 6.2 g/dl and peripheral blood smear showed hypochromic microcytic red blood cells. Bone marrow showed moderate erythroid hyperplasia and normoblast with scant cytoplasm, and it was not stained by Prussian Blue stain. She had a mosaicism of 45.X/46.XXr in the cells, cultured from the peripheral blood. Fifty five cells were examined. Forty-two cells had 45 chromosome, with one X. The remaining thirteen cells had 46 chromosomes per cell, with a normal X and a ring X chromosome. The mother was 155 cm tall and had normal karyotype. We herein report a Turner syndrome patient with a ring X chromosome with a brief review of literature.
Systemic Lupus Erythematosus를 동반한 Multiple sclerosis
이지현,이기주,윤성호,부귀범,손현화,박유환,정춘해,김진호,정원영 조선대학교 부설 의학연구소 1998 The Medical Journal of Chosun University Vol.23 No.2
Multiple sclerosis and lupus erythematosus are chronic, potentially disabling diseases of unknown cause. It is a rare occasion that the finding of both diseases occurs in one patient. Because both diseases may affect the central nervous system, it may be difficult at times to differentiate symptoms of lupus erythematosus from those of multiple sclerosis. As far as we know, there was no case report of SLE in multilple sclerosis in Korea. We report a case of multiple sclerosis accompanied by SLE.
진영기,이기주,문규,김현리,김태원,이만재,박유환,정춘해 朝鮮大學校 附設 醫學硏究所 1997 The Medical Journal of Chosun University Vol.22 No.1
Objective: Multiple myeloma is characterized by the neoplastic proliferation of a single clone of plasma cells engaged in the production of a monoclonal immunoglobulin. This clone of plasma cells proliferates in the bone marrow and frequently invades the adjacent bone. producing extensive skeletal destruction that results in bone pain and fractures. Anemia. hypercalcemia, and renal insufficiency are important features. We analyses clinical manifestation of multiple myeloma. Method: A clinical observation on 20 cases of myeloma which were diagnosed by criteria of the SW0G(Southwest Oncology Group) between March 1993 and December 1996 at Chosun University Hospital was done. Result: 1. The peak incidence was in 6th decade and male to female ratio was 0.8:1 2. The presenting symptoms at first diagnosis were bone pain(45%). and anemia(20%), but non specific symptoms were also noted. 3. Initial clinical stages were classified as stage in 20%, stage Ⅰ in 25%. and stage 11 in 55%. 40% of stage Ⅱ and 64% of stage Ⅲ patients showed renal impairment. 4. The distribution of immunoglobulin classes were IgG 61%, IgA 22% and light chain 5% 5. Complications of multiple myeloma, such as renal impairment, infections, compression fractures of spine and spinal cord compression were observed, Pneumonia was predominant in infections.
김현리,문규,김동민,정중화,이지현,김태원,이만재,정회상,정종훈,정춘해 朝鮮大學校 附設 醫學硏究所 1997 The Medical Journal of Chosun University Vol.22 No.1
A 34-year-old man was admitted with 3 month history of nausea, vomiting and general weakness. On admission, laboratory studies revealed Hb 8.8g/dL, Hct26.2%, WBC 9040/mm3, Platelet 243,000/mm3, serum calcium 18mg/dL, serum phosphate4. Img/dL and serum PTH 7.0pg/dL. Bone marrow study showed abnormal lymphoid cell as much as 23%. Simple X-ray showed osteolytic bone lesions on left mandibular area. The patients was treated with cyclophosphamide, adriamycin, vincnstin, prednisone as remission chemotherapy and achieved normal range of serum calcium and renal function with complete remission hematologically and received 2 times of chemotherapy thereafter. The patient was re-admitted with nausea, vomiting and general weakness, during follow-up. He was improved symptomatically and hypercalcemia was disappeared, but lymphoma was metastasis to lung. The patient with his family refused further therapy, and discharged. He died after discharge.
문규,김동민,김현리,이기주,이봉규,이만재,김태원,이영미,정춘해 朝鮮大學校 附設 醫學硏究所 1997 The Medical Journal of Chosun University Vol.22 No.1
Primary conjunctival Non-Hodgkin's lymphoma is a very rare lymphoma. A 36-yera-old woman presented with an indolent salmon-colored tumor of the left lower eyelid conjunctiva. Histologically, we found a small lymphocytic infiltrate in the subepithelium consist of uniform component. An immunohistological study demonstrated B cell lineage. A comprehensive investigation, in particulary an orbital CT scan did not demonstrate any other localization of this lymphoma. She was treated with chemotherapy (CHOP) and Radiotherapy. Here in we report a case of primary Non-Hodgkin's lymphoma on the conjuctinva with literature review.
김현리,배학연,장성종,김희중,정재용,김양수,김태균,박유환,정춘해 조선대학교 부설 의학연구소 1999 The Medical Journal of Chosun University Vol.24 No.2
Objective: Leptin, the product of obesity (ob) gene, is a 16-kDa peptide hormone secreted by adipocytes and is thought to be a homeostatic signal that contributes to body weight regulation through modulating feeding behavior and/or energy expenditure. Mutations of the ob gene that led to leptin deficiency or production of a truncated inactive protein are associated with hyperphagia, hypometabolism, obesity, and noninsulindependent diabetes mellitus(NIDDM) in obese ob/ob mice. Leptin' s role in humans with obesity and NDDM is not known. Plasma leptin concentrations are shown to be elevated in obese humans. We questioned whether subjects with NIDDM have an altered regulation of serum leptin levels. Therefore, the object of this study is to evaluate the relationships between the serum leptin level and BMI, NIDDM. Method: This study were made of 70 subjects(control: 35, NIDDM:35) at Chosun University Hospital in Kwangju from March, 1998 to September, 1998. We measured the height and weight for BMI. Also, we measured leptin and C-peptide through radioimmunoassay. Result: The serum leptin concentration were not different in patients with type II diabetic and nondiabetic subjects (6.3 0.86/7.22 0.96, p=0.476) and the BMI was similar in diabetic and nondiabetic subjects(24 0.57/24 0.45, p=0.93). The leptin concentration were higher in women than in men regardless of diabetic status (diabetes: male 3.07 0.40 / female 8.20 1.18, p<0.05 control: male 4.88 1.28 / female 8.60 1.25, p<0.05). Conclusion: We concluded that the leptin concentrations were not different in diabetic and nondiabetic subjects and that the association of leptin with sexual dimorphism was similar in diabetic and nondiabetic subjects.