요로감염증과 연관된 방광요관역류 이외의 선천성 요로계 이상에 관한 고찰

정소희,김정심,김현정,이미나,엄미령,진동규,신화숙,Chung So-Hee,Kim Jung-Sim,Kim Hyun-Jung,Lee Mi-Na,Uhm Mee-Ryung,Jin Dong-Kyu,Shin Hwa-Sook 대한소아신장학회 1999 Childhood kidney diseases Vol.3 No.2

Purpose : It has been well known that urinary tract infection(UTI) in infants and children is frequently associated with vesicoureteral reflux(VUR). However, the publishied papers dealing with congenital anomalies associated with UTI emphasized the importance of VUR only. The aim of our study was to evaluate the type, incidence and spectrum of urologic anomalies associated with UTI. Methods : Medical records of clinical, bacteriologic and radiologic study were assessed retrospectively in 65 infants or children with documented UTI who were admitted to the Department of Pediatrics, Samsung Seoul Hospital from March 1996 to February 1998. Results : Spectrum of anomalies were associated with UTI as follows: VUR(n=23), both ectopic kidney(n=1), ureterovesical junction(UVJ) obstruction(n=1), multicystic dysplastic kidney(n=1), ureteropelvic junction(UPJ) obstruction with hydronephrosis(n=1), hutch diverticulum(n=1), UPJ stenosis(n=1), posterior urethral valve(n=1), urachal remnant(n=1) and bladder diverticula(n=1). Congenital urinary anomalies other than VUR were detected in 9 children among 65 patients with UTI(13.8%). 4 children among 9 congenital urinary anomalies other than VUR were combined with VUR. Sex distribution with congenital urinary anomalies other than VUR was more prevalent in male than female (7 males : 2 females). Age distribution at the time of UTI was less than 5 years in most patient (under 1 year in 1 patient, 1-2 year in 5 patients, 3-5 year in 1 patient, and above 5 year in 2 patients). And age distribution at the time of UTl associated with VUR was less than 5 years in most patient (under 1 year in 6 patients, 1-2 year in 8 patients, 3-5 year in 5 patients, and above 5 year in 4 patients), too Conclusion : Because congenital urinary anomalies other than VUR are seen in as high as 13.8% of patients, more careful evaluation of all possible congenital urinary anomalies as well as VUR is mandatory in pediatric patient with UTI.

Menkes 병의 뇌 자기공명 영상 및 자기공명 혈관 조영술의 소견

정소희(So Hee Chung),이문향(Mun Hyang Le),윤혜경(hye Kyung Yoon),김보경(BoKyung Kim),정희정(Hee Jung Chung) 대한소아신경학회 1998 대한소아신경학회지 Vol.6 No.1

저자들은 심한 발달 저하 및 발작을 주소로 방문한 8개월 남아에서 특징적인 머리카락, 혈액, 소견 등을 통해 드문 질환으로 알려진 Menkes 병을 진단하였고 또한 Menkes 병의 특징적인 뇌 자기공명 및 자기공명 뇌혈관 조영술의 소견을 보고하는 바이다. 자기공명 뇌혈관 조영술은 이 병이 의심되는 환아에서 조기 진단을 내릴 수 있는데 도움이 될뿐만아니라 추적 검사시에도 유용할 것으로 사료된다. Menkes disease is an X-linked recessively inherited neurodiegenerative disorder of copper metabolism leading to death in early childhood. This disease is characterized by low serum, liver and brain Cu levels, whereas the Cu content in nearly all other organs is increased. the main clinical features are irregular kinky hair, characteristic face, progressive degeneration of the central nervous system, bone changes, arterial rupture and thrombosis, and instability of temperature. We have experienced a case of Menkes disease in a eight months old male patient, who manifested by seizure, developmental delay, hypotonia, characteristic hair and face along with low lwvels of serum copper and ceruloplasmin. We report the characteristic findings of cranial MRI and MR angiography in this Menke's patient. I n cranial MRI, he showed progressive brain atrophy with subdural hemorrhage and effusion. MR angio-graphy revealed tortuosity of vessels clearly obviating necessity of more invasive conventional arteriography in diagnosis of this disease. This study suggested that cranial MRI and especially MR angiography might be helpful in making early diagnosis of this disease.

서양음악형식: 역사적 발전과정을 통한 이론적 조망

정소희 ( So Hee Chung ) 이화여자대학교 음악연구소 2007 이화음악논집 Vol.11 No.1

Throughout the history of the Western music, the creation of new music always derived from an effort to find a fundamental of the composition, the analysis. The theory of analysis began to be recognized as an independent academic curricula from the 19th century. From the Medieval period, the musical analysis was already considered as an assisting tool for academic studies but not until 1750s, the analytical approach was widely accepted. Among many analytical theories, the formal analysis is counted as the most important one, which deals with over all aspects of music rather than a fragment of the entire work. This thesis is focusing to the development of formal analysis and its new possibility through following processes: 1) all existing musical forms are categorized based on the currently available published materials, 2) the list of different forms is completed by studying every form ever created, 3) researched on the necessity of a theory for origins, evolutions and disappearance of musical forms. During this research, it has been proved that the theory is a leading factor for musical form`s creation, evolution and disappearance. The theory also is the core of deciding the type of a musical form. Among many theories, the most important musical factor to decide a form is scale system. This system evolved from modal to tonal and to atonal (12-tone music included), dominated and manipulated the development of a musical structure from polyphony to homophony and back to polyphony. One can conclude that the musical form was born out of structural boundaries of a scale system. For example, a representative form of a tonal theory is the sonata form. The reason that other similar forms such as rondo and fugue also has three parts like sonata lies on the fact that the progression of tonic-dominant-tonic is the main organization of a scale. After 1900`s, the new scale system failed to create a major form like Sonata. However, it is feasible that a new form would be created out of a new theory because the logical principles of polyphony will coexist with the Western music.

뇌세포 이주장애에 의한 소아 간질환자의 임상적 특성과 치료 전략

은소희(So Hee Eun),정소희(So Hee Chung),이문향(Munhyang Lee),주찬웅(Chan-Uhng Joo),조수철(Soo-Chul Cho),김선준(Sunjun Kim) 대한소아신경학회 2000 대한소아신경학회지 Vol.8 No.2

배경 : 뇌 영상기법의 발달과 간질의 수술적 처치가 이루어지면서 신경세포의 형태적 이상이나 중추신경계의 기저질환이 알려지고 있다. NMD는 신경세포 이주 과정 중 뇌의 허혈, 저체온, 특정약물 등으로 인해 초래되는 질환군이다. NMD의 경우에는 대부분 뇌성마비, 정신지체, 발달지연, 간질 등을 동반하는 것으로 알려져 있고, 간질은 77-90%의 동반률을 보이며, 대부분은 난치성 간질을 나타내는 것으로 알려져 있다. 하지만 지금까지 발표된 연구는 대부분 간질 수술을 받은 성인 연령환자를 대상으로 분석하였기 때문에 소아 연령에서 진단된 환자의 정확한 간질의 경과 및 예후를 알 수 없었다. 이에 소아 연령의 NMD 환자를 대상으로 하여 병변 분류, 임상특징, 뇌파소견 치료 및 경과 등을 알아보기 위해 본 연구를 시작하였다. 방법 : 1993년 3월부터 2000년 6월까지 전북대학교병원과 삼성의료원 소아과에 내원하여 MRI 또는 간질 수술 후 조직학적으로 NMD로 확진 된 57명의 환자를 대상으로 병록지를 통한 후향적인 방법으로 연구를 시행하였다. 결과: 전체 57명 중 피질이형성증이 26례로 가장 많았고, 활택뇌증 9례, 다소뇌회증 7례, 분열뇌증 6례, 일측성 거대 뇌증 4례, 이중 피질 2례 등이었다. 가장 흔한 임상증상은 간질발작으로 54례(94.7%)에서 있었고, 전반적인 발달지연 19례(33.3 %)였다. 간질발작 시기가 가장 빨랐던 경우는 활택뇌증 환아로 생후 4일째에 발작이 시작되었으며, 활택뇌증, 분열뇌증, 일측성 거대뇌증엔서 비교적 조기에 간질이 시작되었다. 뇌파소견상 발작파가 57례 중 51례(89.5%)에서 나타났고, 비정상 비발작파는 35례(61.4%)에서 나타났으나 정상적인 소견을 보인 경우도 있었다. 항경련제에 대한 간질발작 조절 효과는 약물요법으로만 경련을 조절한 경우는 41례(75.9%)이며, 반응이 좋은 경우가 31례(57.4%)이었다. 수술적 치료를 실시한 경우는 전체 중 14례였고, 피질이형성증에서 10례로 가장 많이 실시하였다. 병변의 완전절제를 실시한 경우에는 발작 없이 관찰 중이나, 부분절제를 실시한 경우에 지속적인 발작의 양상을 보였다. 결론 : NMD의 임상소견 중 간질발작이 가장 흔하였고 기타 다른 신경증상은 활택뇌증에서 좀 더 흔하게 보였지만 특징적인 소견은 아니었다. NMD 환자의 발작이 난치성 간질을 보이는 확률이 높지만 본 연구에서는 57.4%에서 약물치료에 간질이 조절되었다. NMD 진단 후 조기 수술을 시행하기 보다는 합리적이고 적극적인 약물요법을 충분히 실시하는 것이 타당하리라 생각된다. Purpose: The objective of this study is to investige the clinical features, natural histories, and results of medical and surgical treatment of NMD in patients who were diagnosed during childhood. Methods: We performed a retrospective analysis of medical records of 57 patients with NMD who were newly diagnosed by MRI or pathologically in epilepsy children since March 1993 to June 2000. Results: These 57 patients with NMD consisted of 26 with cortical dysplasia, 9 with lissencephaly, 7 with polymicrogyria, 6 with schizencephaly, 4 with hemimegalencephaly, 3 with heterotopias, and 2 with double cortex. Clinically, 94.7% of these patients showed seizures, 33..3% with developmental delay, 21.1% mental retardation, 15.8% cerebral palsy, and 7.0% attention deficit hyperactivity disorder. Their response to antiepileptic drugs was good to 31 patients(75.6%), moderate to 3(7.3%), and poor to 7(17.1%). Twelve patients were completely seizure-free after receiving medication for at least 15 months. Seventeen patients tolerated with monotherapy with antiepileptic drugs. Fourteen patients underwent surgical resection. The results of operation were highly correlated with the complete removal of epileptic focus. Six patients who underwent complete resection were seizure-free after operation. On the other hand, Eight patients who had incomplete resection of the epileptic focus showed poor outcome. Conclusion: Most of previous reports suggested that NMD is associated with refractory to medical treatments, and early surgical operation has been recommended. Our study demonstrates remarkably good responses of NMD patients with medical treatment only.

레이다-카메라 융합 차량 과속 검지용 시스템 개발

정소희(Jeong So-Hee),이송(Li Song),정윤수(YunSu Chung) 한국통신학회 2020 한국통신학회 학술대회논문집 Vol.2020 No.8

지반공동 긴급보강을 위한 저강도 보강재 개발을 위한 기초연구

정다솜(Chung, Da Som),유남재(Yu, Nam Jae),정동호(Jung, Dong Ho),김영호(Kim, Young Ho),정소희(Jeong, So Hee),한중근(Han, Jung Geun) 대한토목학회 2016 대한토목학회 학술대회 Vol.2016 No.10

혈변을 동반한 용혈성 요독 증후군 5례

김정심,박은정,정소희,고시환,엄미령,박문수,이흥재,진동규,Kim Jung-Sim,Park Eun-Jung,Chung So-Hee,Ko See-Hwan,Uhm Mee-Ryung,Park Moon-Su,Lee Heung-Jea,Jin Dong-Kyu 대한소아신장학회 1997 Childhood kidney diseases Vol.1 No.2

Purpose : Hemolytic uremic syndrome(HUS), known as a most common cause of childhood renal failure in western countries, has been a relatively rare disease in Korea. Although the reported cases were not related to any specific cause in Korea, there was an outbreak of HUS with bloody diarrhea in Japan last year. We report here that we experienced the several typical HUS last year. Patients : From Jan.1996 to Dec. 1996, five patients were diagnosed as HUS at Samsung Seoul Medical Center, Dept. Pediatrics. Results : 1) The age of onset was below 3 years in 3 cases and above 9 years in 2 cases. 2) All the cases happened between summer and autumn. Three patients had domestic travel and 4 patients drank well or spring water before the symptoms. 3) The clinical manifestation was generalized edema, oliguria, anuria and hematuria. The bloody diarrhea were present in 5 cases and 1 patient had operation with the impression of appendicitis. 4) There was no bacteria which was isolated from the blood or stool samples. 5) Renal biopsies were performed in 2 cases, because of protracted clinical course. One showed microthrombotic angiopathy and the other cortical necrosis with necrotizing glomeruli. 6) Complete recovery was the outcome in 4 cases and one case progressed to chronic renal failure. Conclusion : In conclusion, typical HUS associated with bloody diarrhea, epidemic and good prognosis can be found in Korea and careful surveillance of the pre-clinical cases will be necessary.

선천성 후두열 1 례

손진아(Jin Ah Son),정소희(So Hee Jeong),김정희(Jeong Hee Kim),강이석(I Seok Kang),이상일(Sang Il Lee),백정환(Chung Hwan Baek) 대한소아알레르기호흡기학회 1997 Allergy Asthma & Respiratory Disease Vol.7 No.1

Congenital laryngeal cleft is a rare anomaly, which can cause serious problems of airway and repeated aspiration pneumonia. It is due to failure of fusion of the posterior cricoid cartilage lamina. Dysphagia with aspiration of food is commonly seen with resultant bouts of pneumonia. Detection of an unsuspected minor cleft may be difficult, but the pediatrician should suspect the possibility of cleft from the clinical features. This paper includes. A detailed case report of one patient with congenital laryngeal cleft and the review of literatures,

탄력섬유종 1예

김대호 ( Dai Ho Kim ),정소희 ( So Hee Jeong ),최성우 ( Sung Woo Choi ),김정원 ( Chung Won Kim ),강석진 ( Seok Jin Kang ) 대한피부과학회 1999 대한피부과학회지 Vol.37 No.3

Elastofibroma is a rare disease which presents as a slowly-growing, solid, ill-defined fibroelastic mass occuring almost exclusively in elderly women and arising mainly from the connective tissue between the lower part of the scapula and chest wall. Of the 270 cases of elastofibroma which have been reported, 170 cases had developed in Japanese patients. Despite the fact that there have been only two case reports in Korea, there might be a higher prevalence of elastofibroma in Korea than expected because of geographical similarity. We experienced a case of elastofibroma occurring in a 56-year-old man. To our knowledge, this is the first case report of elastofibroma in Korean dermatologic of literature. (Korean J Dermatol 1999;37(3) : 417-419)

세립분 함량에 따른 지반 내 공동 형상에 관한 실험적 연구

김영호(Kim, Young-Ho),정다솜(Chung, Da-Som),정소희(Jeong, So-Hee),유승경(You, Seung-Kyong),한중근(Han, Jung-Geun) 한국지반신소재학회 2016 한국토목섬유학회 학술발표회 Vol.2016 No.10