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A Soft Tissue Perineurioma and a Hybrid Tumor of Perineurioma and Schwannoma
박지영,이상숙,박남조,김상표,권건영 대한병리학회 2012 Journal of Pathology and Translational Medicine Vol.46 No.1
Perineuriomas are composed of differentiated perineurial cells. Perineuriomas have been recently recognized by the immunoreactivity for epithelial membrane antigen (EMA). Microscopically, perineuriomas show proliferation of spindle cells with wavy nuclei and delicate elongated bipolar cytoplasmic processes. The tumor cells are usually negative for the S-100 protein. Ultrastructurally, perineurial cells reveal slender, nontapered processes containing pinocytic vesicles and discontinuous basal lamina. Interestingly, hybrid tumors of benign peripheral nerve sheath tumor (PNST) have been recently reported by using immunohistochemical and ultrastructural investigations. Herein, we report a case of soft tissue perineurioma arising in the skin of a 56-year-old female; another case of a hybrid tumor of perineurioma and schwannoma in the posterior mediastinum occurred in a 53-year-old male, which is the first case of the hybrid PNST tumor reported in Korea.
손가락에 다수 발생한 진피에 국한된 연부 조직 신경주막종
김지훈 ( Ji Hoon Kim ),최준석 ( Joon Seok Choi ),윤정환 ( Jeong Hwan Yun ),강홍규 ( Hong Kyu Kang ),이종록 ( Jong Rok Lee ),노주영 ( Joo Young Roh ),김태은 ( Tae Eun Kim ),안정석 ( Jeong Seok Ahn ),백진옥 ( Jin Ok Baek ) 대한피부과학회 2013 대한피부과학회지 Vol.51 No.6
Perineurioma is a rare benign peripheral nerve sheath tumor, composed uniformly of perineurial cells. Soft tissue perineurioma primarily arises within the subcutaneous tissue of extremities and trunk as a painless solitary nodule, and should be distinguished from dermatofibroma, neurofibroma, dermatofibrosarcoma protuberans, meningioma and so on. A 25 year-old female is presented with three small asymptomatic papules on the third left finger which were found 3 years ago. Punch biopsy was performed on all of the papules. Microscopic examination demonstrated well-demarcated tumor within dermis, and proliferation of spindle cells with wavy nuclei and elongated bipolar cytoplasmic process, arranged in a whorled pattern. According to immunohistochemical analysis, the tumor cell showed positivity for epithelial membrane antigen, but negativity for S-100 protein, factor XIIIa, CD34, and smooth muscle actin. The diagnosis of soft tissue perineurioma was being made. We report this rare case of perineurioma presented as multiple papules localized within dermis of the digit.
Soft Tissue Perineurioma - A Case Report -
김준모,최준혁 대한병리학회 2009 Journal of Pathology and Translational Medicine Vol.43 No.3
Soft tissue perineurioma is a very rare tumor composed of entirely of neoplastic perineurial cells. A 54-year-old woman presented with a palpable mass in the right lower leg. The mass was excised. Grossly, the tumor measured 2.0×2.0×1.5 ㎝. The cut surface was well circumscribed, pale pinkish gray, and rubbery soft. Histological examination showed that the tumor was composed of spindle cells within collagenous and myxoid stroma. The tumor cells had elongated, tapering nuclei with long and thin cytoplasmic processes, and were arranged in fascicular, whorled, and storiform pattern. The tumor cells were positive for epithelial membrane antigen and collagen type IV and negative for S-100 protein. Ultrastructurally, tumor cells showed long and thin cytoplasmic processes, pinocytic vesicles, and incomplete external lamina. The diagnosis of soft tissue perineurioma was confirmed by immunohistochemical stain and ultrastructural study.
문우성 ( Woo Sung Moon ),김숙 ( Sook Kim ),최호열 ( Ho Yeul Choi ) 전북대학교 의과학연구소 2001 全北醫大論文集 Vol.25 No.2
악성 말초신경초종양(Malignant peripheral nerve sheath tumors, MPNST)은 조직학적 소견이 매우 다양하다. 종양을 구성하는 세포의 기원은 아직까지 정립되어 있지 않다. 최근에 악성 말초신경초종양 중 주로 신경주위 세포(perineurial cell)로 구성되어 있는 종양을 신경주위 악성 말초신경초종양(perineurial MPNST)으로 분리하였다. 저자들은 45세 남자에서 발생한 신경주위 악성 말초신경초종양 1예를 경험하였기에 보고하고자 한다. 이 종양은 상완의 피하조직에서 발견되며 방추형 혹은 난원형 세포들이 다발을 이루거나 작은 혈관주위로 소용돌이치는 배열을 특징으로 하였다. 그리고 이들 세포들은 전자현미경적으로 신경주위 세포임이 확인이 되었다. 임상 및 병리소견이 다른 종류의 악성 말초신경초 종양과 다르므로 신경주위 악성 말초신경종양은 면역학적 검사와 전자현미경적 검사를 통해 확진을 해주어야 된다.