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백세현(Sei Hyun Baik),구양서(Yang Suh Koo),김상진(Sang Jin Kim),심완주(Wan Joo Shim),최동섭(Dong Seop Choi),김인선(In Sun Kim),정희진(Hee Jin Jeong) 대한내과학회 1992 대한내과학회지 Vol.43 No.2
A POEMS syndrome is a rare diaease of which main clinical characteristics are polyneuropathy, organomegaly, endocrinopathy, M proteins and skin changes. Although the proliferation of plasma cell is considered to do a pathogenetic role, the definite etiology and pathogenesis is still unclear. A 47years old woman who has been treated for valvular heart disease admitted to the hospital because of low extremity pain, walking disturbance, aggravation of exertional dyspnea and abdominal distention. She also complained of the anterior neck swelling and dark discoloration of skin. She had been suffered from diabetes mellitus for 5months. Inspite of repeated centesis of ascitic and pleural fluid with medical freatment for heart tailure, and administration of insulin and thyroid hormone for DM and hypothyroidism, dyspnia and abdominal distention did not improved. On the tenth day of admission, 2×2 cm sized palpable axillary lymph node biopsy was done and prednisolone was prescribed under the impression of POEMS syndrome. The findings of lymph node biopsy and bone marrow biopsy which was done 6weeks later was compatible with POKMS syndrome. In bone mar- row biopsy, most plasma cells which slightly increased in proportion were positive for IgA λ on immunohistochemical stain. There was a dramatic improvement of low extremity pain, edema, skin lesions and other symptoms after 10days use of prednisolone. But blood sugar level fluctuated although splitted doses of insulin were applied. General condition of the patient was improved continuosly, so she discharged with well being sense. We exprienced a case of POEMS syndrome in a 47years woman who has all major characteristics of the syndrome. We report this case with a review of literatures.
( Hyun Jung Lee ),( Ja Young Ryu ),( Ho Cheol Hong ),( Kyung Mook Choi ),( Sei Hyun Baik ),( Hye Jin Yoo ) 대한내과학회 2014 대한내과학회 추계학술발표논문집 Vol.2014 No.1
Background: Fat distribution may become more central, or android, after menopause. Although many studies have been performed to identify superiority among anthropometric indices to predict cardiovascular disease (CVD) risk in individuals with all age ranges or with different ethnic groups or with type-2 diabetes, studies to evaluate the association between menopausal status and indicators of atherosclerosis are limited. Thus, the objective of the present study is to assess the efficacy of body mass index (BMI), waist circumference (WC) and waist-to-hip ratio (WHR) for predicting atherosclerosis in pre and post-menopausal women. Methods: A total of 442 participants (209 pre-menopausal and 233 post-menopausal women), who underwent a health examination between April 2012 and May 2013 were prospectively enrolled. We investigated the efficacy of each anthropometric marker including BMI, WC and WHR for predicting atherosclerosis in pre and post-menopausal women by carotid intima-media thickness (CIMT) and brachial ankle pulse wave velocity (baPWV) in healthy Korean women. Results: Compared with post-menopausal women, pre-menopausal women had a thinner WC (76cm and 71cm respectively), and had a lower BMI (23.2 kg/m2 and 21.8 kg/m2 respectively) and WHR (0.9 and 0.8 respectively). In pre-menopausal women all anthropometric parameters (BMI, WC, WHR) are positively correlated to baPWV (0.20, 0.19 and 0.21, P < 0.01, respectively), and CIMT values (0.36, 0.34 and 0.27, P < 0.01, respectively) whereas in post-menopausal women only WHR was positively correlated to baPWV values (0.27, P < 0.01) and WC, WHR were positively correlated to CIMT (0.15, P < 0.05 and 0.21, P < 0.01, respectively) The correlation coefficient in all parameters of CIMT was significantly higher in WHR than WC in post-menopausal women. Conclusions: This study shows that WHR has the best predict value for predicting atherosclerosis than BMI or WC in post-menopausal women.
Fra-1 Expression in Malignant and Benign Thyroid Tumor
(Yong Hyun Kim),(Jeong Heon Oh),(Nan Hee Kim),(Kyung Muk Choi),(Sang Jin Kim),(Sei Hyun Baik),(Dong Seop Choi),(Eung Seok Lee) 대한내과학회 2001 The Korean Journal of Internal Medicine Vol.16 No.2
N/A Background : The differential diagnosis of thyroid nodules is very important in deciding the treatment modality and the fine needle aspiration is the best diagnostic method. But, there are some limitations in use because of inadequate test materials and difficulty in interpreting. According to the study of oncogene and tumor suppressor gene about the origin of thyroid tumor, expression of Fra-1, one of AP-1 complex, is increased in thyroid neoplasm, though not present in the normal tissue. So, there is a possibility that it will be used as a method for the differential diagnosis of thyroid nodules. We tried to know whether presence or absence of Fra-1 expression can be used as a diagnostic method in differential diagnosis of thyroid nodules using the immunohistochemical (IHC) staining method. Method : In 4 types of thyroid tumor that were confirmed by histologic diagnosis after operation (18 cases of adenomatous goiter, 16 cases of follicular adenoma, 30 cases of papillary cancer, 10 cases of follicular cancer), IHC staining method was performed to evaluate the expression of Fra-1. Result : In papillary and follicular thyroid cancers, the expression of Fra-1 was stronger than in benign thyroid tumor, but there was no difference in Fra-1 expression between the two types of carcinoma. Weak expression of Fra-1 was observed in all cases of follicular adenoma, though it was weaker than in carcinoma, and it was also weakly expressed only in some cases (33%) of adenomatous goiter. Conclusion : The expression of Fra-1 was stronger in thyroid cancer than in benign thyroid tumor, but it was impossible to differentiate thyroid cancer from benign thyroid tumor by presence or absence of Fra-1 expression using IHC staining method.
류옥현,류혜진,박수연,권순범,박상수,김희영,이계원,서지아,오정헌,김신곤,김난희,최경묵,백세현,최동섭 대한내분비학회 2004 Endocrinology and metabolism Vol.19 No.1
저자들은 국내에서 처음으로 음핵 비대와 지속적인 질출혈을 주소로 내원한 19세 여성에서 고혈압이 동반되지 않으면서 11 -수산화효소 결핍으로 인한 선천성부신증식증을 경험하였기에 문헌 고찰과 함께 이를 보고하는 바이다. Congenital adrenal hyperplasia refers to a group of autosomal recessive disorders that is defective in the synthesis of cortisol. The enzymes most often affected are 21-hydroxylase and 11 - hydroxylase. The low levels of cortisol stimulate the pituitary gland to release ACTH. Chronic elevation of the ACTH level causes bilateral adrenal hyperplasia and a secondary increase in androgen formation. We examined a 19 year-old woman presented with clitoral hypertrophy and vaginal spotting. The subjects basal level of serum cortisol was low, but the serum levels of ACTH, 17a-hydroxyprogesterone, deoxy-corticosterone were elevated. The urinary excretions of 17-ketosteroids and 17-hydroxycorticosteroids were also increased. The karyotyping study and transrectal ultrasonography showed normal findings. The patient underwent clitoris reduction surgery and received hydrocortisone. To the best of our knowledge, this is the first case of 11 -hydroxylase deficiency in Korea (J Kor Soc Endocrinol 19:58∼63, 2004).