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동일 열성질환에서 반복성 열성경련의 예방을 위한 Diazepam의 효과
조도준(Do Jun Cho),민기식(Ki Sik Min ),김종완(Jong Wan Kim),김광남(Kwang Nam Kim),유기양(Ki Yang Ryoo) 대한소아신경학회 1993 대한소아신경학회지 Vol.1 No.2
The efficacy of short-term diazepam prophylaxis in repeated febrile seizures was evaluated in a prospective controlled study. A total 172 consecutive children admitted with their febrile seizure were participated in our study from May,1991 to June,1992. The children of control group were admitted with their febrile seizure from January,1987 to December,1990. Intravenous Diazepam(0.1mg/kg) is administered to patients with febrile seizures at admission. And oral Diazepam(0.5mg/kg/day) is administered at first hospitalization day. At second hospitalization day, consecutive oral Diazepam (0.6 mg/kg/day) is administered. The results were as follows: 1) The incidence of repeated febrile seizure was 8.1% in study group and 17.0%in control group. 2) In hospital, repeated febrile convulsion was 0.6% in study group and 4.3% in control group. 3) The repeat rate of febrile seizure with fever less than 39℃ was 6.3% in study group and 20.5% in control group. 4) The repeat rate of febrile seizure with serum sodium concentration under 135mEq/L was 10.9% in study group and 47.4% in control group. 5) There was no serious side effects of diazepam.
조옥연,허권회,조도준,김덕하,민기식,유기양,이열,Cho, Ok Yeon,Huh, Kwon Hoe,Cho, Do Jun,Kim, Dug Ha,Min, Ki Sik,Yoo, Ki Yang,Lee, Yul 대한소아청소년과학회 2003 Clinical and Experimental Pediatrics (CEP) Vol.46 No.4
저자들은 경련, 구토를 주소로 입원한 환아에서 만성 경막하출혈과 망막출혈을 보여 흔들린 아이 증후군으로 진단한 5례를 경험하였다. 현재까지 국내에서는 보고와 연구가 드물지만 의료인이 흔들린 아이 증후군에 대한 가능성을 염두에 두고 좀 더 적극적으로 방사선 검사나 안과 검사를 시행하면 올바른 진단과 함께 치명적인 합병증의 발생을 감소시킬 수 있다고 사료되는 바 문헌 고찰과 함께 보고하는 바이다. Shaken baby syndrome is a serious form of child abuse, mostly involving children younger than 2 years. It results from extreme rotational cranial acceleration induced by violent shaking. The characteristic injuries include subdural hemorrhage, retinal hemorrhage, and fracture of ribs or long bones. If physicians have no recognition of, or suspicion about, shaken baby syndrome, this syndome is difficult to diagnosis because of a lack of obvious external signs and failure of the abuser to admit his or her actions. In addition to the high mortality, 60% of survivors have significant long term neurologic and developmental abnormality. The authors experienced five cases of shaken baby syndrome presented with seizures or vomiting, without external signs of trauma. All of these cases had subdural hemorrhages, and four cases had retinal hemorrahges. In our follow up, two children were found to have sequelae such as quadriplegia, monoplegia, and developmental delay. We emphasize that early recognition and prompt treament are key to overall success of case management. The incidence of shaken baby syndrome can be reduced through public awareness and education of parents not to shake a babies.
이경은,조옥연,심은정,조도준,김덕하,민기식,유기양,이관섭 대한소아청소년과학회 2004 Clinical and Experimental Pediatrics (CEP) Vol.47 No.7
Neonatal hydrometrocolpos is the cystic dilatation of the vagina and uterus, which is caused by the combination of vaginal obstruction such as imperforate hymen, transverse vaginal septum, or vaginal atresia, and glandular secretion by maternal estrogenic stimulation. Although hydrometrocolpos is a rare congenital abnormality unlike pubertal hematocolpos, it is one of the relatively common abdominal masses in neonates. In typical cases the diagnosis may be determined easily by the combination of a pelvic mass, upper urinary tract dilatation and a bulging membrane in the vaginal introitus. The presense of a lower abdominal mass in a female infant should always arouse suspicion of hydrometrocolpos and lead to careful examination of the vagina. We report a case of neonatal hydrometrocolpos due to imperforate hymen which was initially presented as a large abdominal mass and a bulging membrane in the vaginal introitus. For 72 hrs, the abdominal mass increased rapidly, accompanied by urinary tract obstruction. It was relieved by a simple incision of the imperforate hymen and drainage of 300 cc of whitish mucoid vaginal fluid, and by Foley catheter drainage of 750 cc urine. No other anomaly was observed. 저자들은 구토와 복부 팽만을 주소로 내원한 환아에서 처녀막 폐쇄로 인해 급격히 진행된 요로 폐쇄를 동반한 수질자궁증 1례를 경험하였다. 현재까지 국내에서는 보고된 경우가 드물지만 복부 팽만과 복부 종괴 소견이 있는 환아에서 요로 폐쇄 증상을 보일 경우 수질자궁증에 대한 가능성을 염두에 두고 자세한 진찰과 검사 및 조기진단과 치료를 시행하면 불필요한 개복과 합병증의 발생을 감소시킬 수 있다고 사료되는 바 문헌고찰과 함께 보고하는 바이다.