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재발된 그레이브스병 환자에서 항갑상샘약제 재투여 후 발생한 무과립구증 1예
정귀홍 ( Gwi Hong Jeong ),김성균 ( Seong Kyun Kim ),명대성 ( Dae Seong Myung ),정진욱 ( Jin Ook Chung ),조동혁 ( Dong Hyeok Cho ),정동진 ( Dong Jin Chung ),정민영 ( Min Young Chung ) 대한내과학회 2008 대한내과학회지 Vol.75 No.3
Antithyroid drugs are the most common treatment modality for Graves` disease and are used for the treatment of relapsed Graves` disease in Korea. Agranulocytosis is a rare and severe complication of antithyroid drug therapy, and most cases occur within 3 month after drug treatment. Agranulocytosis can develop in patients who have relapsed Graves` disease and undergo a second course of antithyroid drugs with a prior uneventful course of drug therapy. We report a case of antithyroid drug-induced agranulocytosis in a relapsed Graves` disease patient who had undergone prior uneventful antithyroid drug therapy. We also present a review of the relevant literature. (Korean J Med 75:362-366, 2008)
제2형 당뇨병 환자에서 초음파 측정 내장지방 지표와 심혈관계 위험인자와의 관계
정귀홍 ( Gwi Hong Jeong ),김성균 ( Sung Kyun Kim ),정진욱 ( Jin Ook Chung ),조동혁 ( Dong Hyeok Cho ),정동진 ( Dong Jin Chung ),정민영 ( Min Young Chung ) 대한내과학회 2007 대한내과학회지 Vol.73 No.6
Background: Visceral obesity is known as an independent risk factor of cardiovascular disease and metabolic syndrome. The objective of this study was to evaluate the association of ultrasonographic-determined visceral fat thickness and other parameters of obesity, metabolic syndrome, and risk factors of cardiovascular disease in type 2 diabetes. Methods: A total of 191 type 2 diabetic patients (101 men and 90 women) participated in this study. Anthropometric, clinical, and laboratory data including the body mass index, waist circumference, blood pressure and lipid profiles were measured. Insulin resistance was calculated by using the homeostasis model assessment-insulin resistance (HOMA-IR). The visceral fat thickness was measured by abdominal ultrasonography at 1 cm above the umbilicus. Results: The visceral fat thickness was positively correlated with the body mass index (p<0.001), waist circumference (p<0.001), fat mass (p<0.001), fat distribution (p<0.001), and HOMA-IR (p<0.05), whereas it was negatively correlated with the HDL-cholesterol level (p<0.05). The visceral fat thickness was better correlated with the presence of metabolic syndrome than with the subcutaneous fat thickness. The highest tertile of visceral fat thickness had a higher odds ratio for hypertension (OR=4.02, 95% CI 1.08~14.98), dyslipidemia (OR=9.64, 95% CI 1.08~85.37), and metabolic syndrome (OR=11.35, 95% CI 1.34~96.00) than did those in the lowest tertile, after adjustment for age, sex, and body mass index. Conclusions: The results of our study show that the measurement of abdominal visceral fat thickness using abdominal ultrasonography can be used as a reliable method to identify the risk for metabolic syndrome and cardiovascular disease in type 2 diabetic patients. (Korean J Med 73:618-630, 2007)
두개내출혈과 동반되어 고칼슘혈증 위기로 발현된 낭종성 부갑상선 선종에 의한 원발성 부갑상선기능항진증 1예
정진욱,정귀홍,홍세인,조동혁,정동진,정민영 대한내분비학회 2007 Endocrinology and metabolism Vol.22 No.4
낭종성 부갑상선 선종은 매우 드문 질환으로 원발성 부갑상선기능항진증을 초래할 수 있으며 드물지만 고칼슘혈증 위기를 유발할 수 있다. 문헌고찰에서 외국에서도 보고한 예가 많지 않으며 국내에서도 몇 예를 보고한 바 있으나 고칼슘혈증의 위기로 발현한 경우는 없었다. 이에 저자들은 두개내출혈로 보존적 치료 중 고칼슘혈증, 의식변화와 신기능 감소로 내원한 환자에서 수액요법, 푸로세미드, pamidronate 정맥 주사 후에 호전되어 수술적 절제를 시행했던 낭종성 부갑상선 선종에 의한 원발성 부갑상선기능항진증 1예를 경험하였기에 문헌 고찰과 함께 보고하는 바이다. Most patients with hypercalcemia are asymptomatic or they have non-specific symptoms at diagnosis. Yet hypercalcemic crisis is a potentially fatal complication of hyperparathyroidism. Cystic parathyroid adenoma is a rare cause of primary hyperparathyroidism and hypercalcemic crisis. A 52-year-old woman was transferred to our hospital due to her relapsed drowsy mental state and renal insufficiency that occurred in course of her management for intracranial hemorrhage with manitol. The total serum calcium was 16.2 mg/dL and the intact parathyroid hormone was 546 pg/mL. Neck computed tomography showed a 3.1 × 1.8 cm sized cystic mass on the right thyroid lower pole. 99mTc-labelled sestamibi scintigraphy showed no significant uptake. In addition to prompt saline infusion and loop diuretics, the patient was given pamidronate to lower the serum calcium, and she was improved to an alert mental state with normal renal function. Surgical excision of the parathyroid cyst was performed. A histological examination confirmed a cystic parathyroid adenoma. The levels of plasma PTH and serum calcium were normalized after resection.
김성균,이우석,정귀홍,김희경,명대성,정진욱,정동진,정민영,강호철 대한내분비학회 2007 Endocrinology and metabolism Vol.22 No.5
An angiomyolipoma is a benign mesenchymal neoplasm that typically occurs in the kidney of patients with tuberous sclerosis. Extrarenal angiomyolipomas are uncommon, and the adrenal gland is an extremely rare site for the tumor. An incidental adrenal mass is the usual presentation of an adrenal angiomyolipoma, as most of the tumors are hormonally inactive. Recently we experienced one case of a right adrenal angiomyolipoma that presented with an adrenal incidentaloma. To the best of our knowledge, this is the first case of an adrenal angiomyolipoma described in the Korean medical literature. We report the case with a special emphasis on the differential imaging findings of fat-containing adrenal tumors. (J Kor Endocrine Soc 22:371~375, 2007) 부신의 혈관근육지방종은 매우 드물며 국내에 보고된 바 없다. 지방 조직, 평활근 및 혈관으로 구성된 중간엽 기원의 양성 종양이며 호르몬 검사상 이상 소견을 보이지 않으므로 대부분 영상진단 검사과정에서 우연히 발견된다. 영상진단 소견상 지방육종과 같은 악성종양과 감별이 어려워 대부분 수술적 절제가 필요하며, 완전히 절제한 경우 양성종양으로 재발의 가능성은 매우 낮다. 저자들은 우측 부신에 발생한 혈관근육지방종을 경험하였기에 그 특징적인 영상진단소견 및 임상상을 보고하는 바이다.