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토혈을 주소로 내원한 선천성 간섬유종 환자에서 내시경적 정맥류결찰술 치료 경험 1예
이승환,김현영,김승용,신영록,김연석,나비석,이석수,강길현,유철희 대한소화기학회 2000 대한소화기학회지 Vol.35 No.5
Congenital hepatic fibrosis (CHF) is characterized by periportal fibrosis with irregulary shaped proliferating bile ducts and is recognized as a member of the fibrocystic disease family. It is such a rare disorder that only about 200 patients with CHF has been reported. Affected children or adults often show portal hypertension and related complications, which may lead to bleeding from gastroesophageal varices. The diagnosis of CHF is usually confirmed by its typical histological features. The patients with portal hypertension due to CHF are ideal candidates for portosystemic shunt because most of them have good liver function. Recently, we experienced a case of CHF without hepatic and renal lesions presenting with hematemesis. Endoscopic variceal ligation was performed. We report this case with a review of relevant literatures.
Somatostatin Analogue(Octreotide)치료가 유효했던 췌장성 복수 1예
신정현,김명환,정성희,이성구,서동완,민영일,김선영,유교상,박은택,임병철,나비석,표승일 대한소화기학회 2000 대한소화기학회지 Vol.35 No.4
Pancreatic ascites has the characteristics of highly proteinaceous, amylase-rich intraperitoneal fluid. It usually occurs as a result of rupture of a pseudocyst or disruption of main pancreatic duct during the course of acute or chronic pancreatitis. It can be managed by traditional conservative methods including fasting, total parenteral nutrition and ascites tapping or surgical interventions. Recently, several cases of treating pancreatic ascites with somatostatin analogue (octreotide) successfully have been reported. We experienced a patient with chronic pancreatitis and pancreatic ascites, who was successfully treated by somatostatin analogue (octreotide).
이승환,김현영,김명환,이성구,서동완,민영일,유교상,손정민,나비석,이석수,심선진,전병민 대한소화기내시경학회 2000 Clinical Endoscopy Vol.20 No.3
A Pancreaticobiliary fistula is a rare complication of acute necrotizing pancreatitis or pancreatic abscess. One case is herein reported of pancreaticobiliary fistula that was found following removal of pancreatic duct stones by extracorporeal shock-wave lithotripsy and endoscopic sphincterotomy. The patient was a 53-year old woman who was admitted with epigastric pain and fever. Endoscopic retrograde pancreatography revealed multiple stones in the main pancreatic duct. Pus from the pancreatic duct was drained through the major papilla during cannulation. On balloon cholangiogram obtained after removal of the stones, a direct fistulous connection between the main pancreatic duct and distal common bile duct was noted. It is speculated that pancreatic abscess or mechanical compression of pancreatic duct stones may contribute to the destruction of the intrapancreatic bile duct, which leads to the formation of a pancreaticobiliary fistula.
췌장의 Intraductal Papillary Mucinous Tumor (IPMT) 와 동반된 간내 점액 과분비 담관종양
이승환,장우영,김종철,김명환,민영일,유은실,송희곤,김영민,한상택,고관호,나비석,손정민,서일우 대한소화기내시경학회 2000 Clinical Endoscopy Vol.21 No.5
Intraductal papillary mucinous tumor (IPMT) of the pancreas is a recently understood unique clinicopathologic disease entity comprising approximately 1% of all exocrine pancreatic tumors and 11% of cysticneoplasms of pancreas. It has been reported worldwide, mostly in Japan. It is generally characterized by recurrent pancreatitis, mucin oozing from the papilla of Vater, and dilated pancreatic duct with intraductal filling defects. Microscopically, the mucin-producing columnar epithelium forms papillary proliferation into the dilated pancreatic duct and this feature differentiates IPMT of the pancreas from the more common mucinous cystic neoplasms of the pancreas which usually do not communicate with the pancreatic duct. On the other hand, mucin-hypersecreting bile duct tumors have been rarely reported in the English literature. We herein present the first case of mucin-hypersecreting bile duct tumor combied with IPMT of the pancreas with a review of the related literature.
부췌관에서 발생한 Intraductal Papillary Mucinous Tumor (IPMT) 1예
이영미,김명환,유은실,김태경,이성구,박성제,서동완,민영일,송희곤,강재명,주연호,박경하,강호형,이장교,김순종,나비석,서일우 대한소화기내시경학회 2001 Clinical Endoscopy Vol.22 No.2
Mucin-producing tumors of the pancreas were first reported by Ohhashi and Takagi in 1980. Since then, many cases of intraductal papillary mucinous tumor (IPMT) of the pancreas, which is almost homonymous to mucin-producing tumors of the pancreas, have been reported. IPMTs are generally regarded as tumors with a favorable prognosis. Some IPMTs have invasiveness and this is always associated with a poor prognosis. Most IPMTs arise from the main pancreatic duct and IPMTs arising from the accessory pancreatic duct are relatively rare, Only 6 cases have been reported in the literature so far. Our patient was a 43-year old man who was admitted to the hospital due to recurrent pancreatitis. An endoscopic retrograde pancreatography revealed a patulous minor papilla orifice extruding mucin and a cystic lesion in a branch of the accessory duct. A pancreaticoduodenectomy was performed and a pathologic examination of the resected specimen showed intraductal papaillary mucinous neoplasm, low grade malignancy, in the accessory pancreatic duct and its branch. We herein report this interesting case with a review of the literature.