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정상윤 ( Sang Youn Jung ),문진욱 ( Jin Wook Moon ),박민찬 ( Min Chan Park ),박용범 ( Yong Beom Park ),윤미진 ( Mi Jin Yun ),이수곤 ( Soo Kon Lee ) 대한류마티스학회 2003 대한류마티스학회지 Vol.10 No.3
Neuropsychiatric lupus is a complication of systemic lupus erythematosus (SLE) characterized by profound metabolic alteration including impaired blood flow, ischemia, decreased aerobic metabolism and progressive neuronal loss of central nervous system. Because of the lack of useful diagnostic methods, it`s diagnosis and management is difficult. Recently, F-18-fluoro-2-deoxy-D-glucose positron emission tomography (18FDG-PET) is considered to be a sensitive and reliable method for evaluating SLE patients with neuropsychiatric involvement as compared with brain computed tomography (CT) or magnetic resornance imaging (MRI). In SLE patient having mild or severe neuropsychiatric manifestations, 18FDG-PET shows hypo- or hypermetabolism by different glucose utilization in brain tissue. We experienced a 23-year-old woman with SLE who presented with seizure and loss of consciousness. Initially, brain MRI finding was negative, but brain 18FDG-PET revealed significant hypometabolism in the cerebral hemisphere at active stage of disease and complete resolution of metabolic abnormalities after treatment. Herein, we report a case of neuropsychiatric lupus diagnosed by brain 18FDG-PET.
하유정 ( You Jung Ha ),정상윤 ( Sang Youn Jung ),이광훈 ( Kwang Hoon Lee ),최준정 ( Jun Jung Choi ),이광길 ( Kwang Kil Lee ),이수곤 ( Soo Kon Lee ),박용범 ( Yong Beom Park ) 대한류마티스학회 2009 대한류마티스학회지 Vol.16 No.4
Dermatomyositis is a rare inflammatory myopathy with characteristic skin manifestations and accompanied by muscular weakness. Vesicle formation in dermatomyositis is rare. We report a case of dermatomyositis associated with ovarian cancer in a 62-year-old woman who had vesicles and bullae on her arms. She had erythema and edema on the face, chest, abdomen, and shoulder for 2 months. Diagnosis of dermatomyositis was established by clinical manifestations, muscle enzyme elevation, and a characteristic electromyogram. She was successfully treated with cyclosporin and high doses of steroids.
강은진 ( Eun Jin Kang ),최상태 ( Sang Tae Choi ),이상원 ( Sang Won Lee ),정상윤 ( Sang Youn Jung ),손명균 ( Myoung Kyun Son ),이광훈 ( Kwang Hoon Lee ),양우익 ( Woo Ick Yang ),박용범 ( Yong Beom Park ),이수곤 ( Soo Kon Lee ) 대한류마티스학회 2008 대한류마티스학회지 Vol.15 No.1
Kikuchi-Fujimoto`s disease (KFD), or histiocytic necrotizing lymphadenitis, is a rare benign and self-limiting disease. KFD are confused with systemic autoimmune disease as they present with localized lymphadenopathy, fever, fatigue, arthritis, leukopenia. Furthermore as KFD can occur associated with other autoimmune disease, we need to diagnose carefully. Here, we describe a case of 27-year-old female patient, diagnosed as KFD, who subsequently developed adult onset Still`s disesase (AOSD). As far as we know, this is the first case of KFD with AOSD in Korea.
한국인 성인 Henoch-Schonlein Purpura 환자의 임상적 특징
강윤 ( Yoon Kang ),하유정 ( You Jung Ha ),이광훈 ( Kwang Hoon Lee ),정상윤 ( Sang Youn Jung ),이상원 ( Sang Won Lee ),이수곤 ( Soo Kon Lee ),박용범 ( Young Beom Park ) 대한류마티스학회 2010 대한류마티스학회지 Vol.17 No.2
Objective: We investigated the clinical data and analyzed the significant prognostic factors for outcomes in Korean adult patients with Henoch-Schonlein Purpura (HSP). Methods: We retrospectively reviewed the medical records of 52 patients over 20 years-old, who visited the Yonsei University Severance Hospital from December 1999 to November 2009, and fulfilled the classification criteria for HSP. We investigated the epidemiologic data, clinical features, renal biopsy findings, laboratory results and disease outcomes. Results: The median age was 43.5 (20∼83) years old and 29 out of 52 patients (55.8%) were male. HSP exhibited seasonal variation and most frequently developed in winter (42.3%), followed by spring (25.0%). Upper respiratory infection was the most common known preceding event for HSP development. Skin manifestations were observed in all subjects, followed by kidney (80.8%), gastro-intestine (57.7%) and joints (26.9%). After a median follow-up period 14.5 (1∼227) months, 12 patients experienced HSP relapse (23.1%), and 7 patients had chronic renal failure (13.4%). Univariate analysis showed that renal insufficiency (p=0.002) and nephritic syndrome (p=0.026) at diagnosis were significantly related to the development of chronic renal failure. Of the two parameters, only initial renal insufficiency was found to be a significant predictive value for chronic renal failure (OR=28.7, p=0.001, 95% confidential interval 3.6∼225.3). Conclusion: Renal insufficiency at diagnosis may be a useful predictive factor for progression to chronic renal failure in Korean adult patients with HSP.
유희태 ( Hee Tae Yu ),하유정 ( You Jung Ha ),정상윤 ( Sang Youn Jung ),이광훈 ( Kwang Hoon Lee ),김현민 ( Hyun Min Kim ),이수곤 ( Soo Kon Lee ),박용범 ( Yong Beom Park ) 대한류마티스학회 2010 대한류마티스학회지 Vol.17 No.2
Septic arthritis of the sternoclavicular joint is a rare condition. The predisposing risk factors include intravenous drug abuse, subclavian vein catheter placement, diabetes mellitus and trauma. Delayed or inadequate management can lead to irreversible joint damage with subsequent disability, even death. We report a 48-year-old female patient who presented with right sternoclavicular joint swelling and right shoulder pain. Magnetic resonance imaging of the sternum showed swelling of the right sternoclavicular joint with gadolinium enhancement. Synovial fluid and bone tissue culture revealed Escherichia coli (E.coli), and confirmed the diagnosis of sternoclavicular septic arthritis. She was successfully treated with surgical debridement and ciprofloxacin without recurrence. This is the first case report of E.coli sternoclavicular septic arthritis in Korea.
정지영,최석훈,박윤선,진범식,한상훈,허규연,심완섭,이재혁,정상윤,최한석,최준용,박윤수,조정호,장경희,송영구,이광훈,김준명 대한감염학회 2003 감염과 화학요법 Vol.35 No.5
저자들은 면역 억제 치료를 받은 베체트 증후군 환자에서 발생된 주폐포자층 폐렴을 기관지 폐포 세축술 및 경기관지 폐생검을 통해 진단하고 치료한 1예를 경험하였기에 문헌 고찰과 함께 보고하는 바이다. Pneumocystis carinii pneumonia (PCP) is one of the most common causes of infection in patients with HIV infection. With the development of effective prophylactic agent, the incidence of PCP in patients with HIV infection has been declining. On the other hand, however, the incidence of PCP has been increasing in immunocompromised hosts without HIV infection, such as rheumatoid arthritis, bone marrow transplantaion and Behcet syndrome. The increased occurrence of PCP in non-HIV-infected subjects has been attributed to several factors, such as use of stronger immunosuppressive regimens, higher awareness of PCP, advanced diagnostic technology and nosocomial spread of P. carinii. The occurrence of PCP in patients who receive immunosuppressive drugs for autoimmune disease has not been well known in Korea. We report a patient with Behcet syndrome who suffered from PCP after immunosuppressive drugs.
박윤선,한상훈,진범식,최석훈,정상윤,최준용,박윤수,조정호,장경희,송영구,김준명 대한감염학회 2003 감염과 화학요법 Vol.35 No.5
정맥 내 약물 남용에 의한 HIV 감염은 지금까지 국내 사례가 보고된 문헌이 없었으나, 저자들은 미국에서 다년간 거주하며 정맥내 약물 남용을 하였던 43세 남자가 국내에서 HIV 감염을 진단받아 문헌고찰과 함께 보고하는 바이다. Intravenous (Ⅳ) drug abuse is one of important transmission modes of human immunodeficiency virus (HIV) infection. Ⅳ drug abuse in HIV epidemics is frequent in western countries. In Korea, however, no case has been definitely identified although possibility of such infection route does exist considering rising number of Ⅳ drug use (IDU). Recently, we have experienced a case of HIV infection by IDU. We herein offer the case with review of literature.