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신중호,김종봉,차미경,양동호,조무식,송옥평,백승호,오도연,이지윤,추원석,홍세용,김도진 대한내과학회 1994 대한내과학회지 Vol.46 No.1
Hereditary factor V1I deficiency is a rare bleeding disorder, with an estimated incidence of 1 in 500,000 and approximately 150 cases reported. It is inherited in an autosomal recessive pattern, with variable expression Homozygotes may have bleeding problems, the severity of which does not always correlate with factor VII levels. Recently, we have experienced a case who was admitted for donor study. Potential recipient was his younger brother who has been dialysed for 5months due to ESRD (end-stage renal disease). During donor study, he exhibited prolonged prothrombin time and normal activated partial thromboplastin time. Delayed prothrombin time was not corrected by vitamine K injection but did by cryoprecipitate transfusion. Assay of coagulation factors revealed deficiency of factor VII. Other coagulation profiles and quantatitation of coagulation factors were normal range. Family members coagulation test were normal range. Successful renal transplantation was performed after cryoprecipitate transfusion. Thus, we report a case of factor VII deficiency with literatures.