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李昊宗,潘奉贊 순천대학교 공업기술연구소 1990 工業技術硏究所論文集 Vol.4 No.-
The process of graphite formation in solid state was observed after the graphitization heat treatment of the white cast irons artificially made to contain pores or CaO inclusion by means of the additions of Se, gas bubble formation agents or CaO, a compound of oxygen in the hypoeutectic cast iron melts. The process of graphite formation in liquid state was examined after the additions of MmH_2 or Kl in the hypereutectic cast iron melts and cooling either slowly or rapidly. The influences of the amount of MmH_2 addition, different holding times after the additions and different S amount in the melts were also investigated. According to the results obtained, the mechanism of spheroidal graphite formation was studied in the view of the gas bubble theory. The results obtained in this work were as follows: 1. in the case of the graphitization heat treatment of the white cast irons under Se, CaCO_3 additions, temper carbon was preferentially precipitated on the remaining gas pores, but with only CaO addition, little graphite was formed on the CaO inclusion in the samples. From the results the behavior of graphite in solid state was preferred at the defects such as the remained pores in cast iron. 2. In the case of the addition of 0.5wt% MmH_2, a gas bubble formation agent, to the hypereutectic melts with 0.015 and 0.030wt% S, there appeared an increase in the count of spheroidal graphite, the rate of graphite formation and the time for spheroidal graphite to remain in the melts with 0.015wt% S rather than 0.030wt% S. 3. In Kl addition to the hypereutectic melts with 0.030wt% S spheroidal graphite was made when cooling the sample rapidly, but flake graphite was made when cooling slowly. These results were in accordance with the view of the gas bubble theory.
潘奉贊,李昊宗 順天大學校 1988 論文集 Vol.7 No.1
D.C.-arc furnaces as a new smelting aggregate are used for the production of Fe and ferro-alloys. To obtain a fuller understanding of electrophoretic phenomena occuring in slag phase during the smelting process, electrophoresis data in slag phase are reviewed and dicussed, and the results obtained in the titanium slag are presented. The discussion is extened to the determination of metal drop velocity in the arc smelting process. Also, the theoretical comparision for the determination of iron drop velocity in the above mentioned titanium slag is described.
신경섬유종증 1형: 두개의 새로운 돌연변이에 대한 보고
이호종,김웅전,김우신,고영진,박건,장숙진,강성호 대한진단검사의학회 2021 Laboratory Medicine Online Vol.11 No.2
Neurofibromatosis type 1 (NF1) is characterized by multiple café-au-lait spots, axillary and inguinal freckling, Lisch nodules in the iris, and fibromatous tumors of the skin. We performed direct sequencing of 58 exons comprising the NF1 gene along with the associated intronic regions in suspected cases of NF1. We have detected two different novel frameshift mutations in two cases, respectively. The first case involved a 59-year-old male presenting with neurofibromas and a positive family history of NF1. The patient presented with leiomyomas of the iliac bone and right adrenal gland, and an astrocytoma of the left cerebellum. The mutation in this patient was caused by heterozygous deletion of base A at nucleotide position 3108 (c.3108delA; p.Lys1036Asnfs*14). The second case involved a 25-month-old girl presenting with multiple café-au-lait spots and a positive family history of NF1. The mutation in this patient was caused by heterozygous deletion of base G at nucleotide position 7623 (c.7623delG;p.Ile2541Serfs*7). These novel mutations may be useful for advanced genetic counseling and clinical management of patients with NF1 and their families. 신경섬유종증 1형(NF1)은 피부에 나타나는 밀크커피색 반점, 겨드랑이와 서혜부의 주근깨, 홍채의 Lisch 결절, 신경섬유종 등을 특징으로 한다. 신경섬유종증 1형이 의심되는 환자에서 NF1 유전자의 58개의 엑손과 주변 인트론에 대하여 염기서열분석을 실시하였다. 이를 통해 2명의 환자에서 병원성으로 판단되는 이전에 보고되지 않은 틀이동돌연변이를 검출하였다. 환자1은 59세 남자 환자로 신경섬유종과 가족력이 있었고, 오른쪽 엉덩뼈에 양성 종양, 오른쪽 부신에 양성종양, 좌측 소뇌에 별아교세포종이 발견되었고, 3108번 핵산에 A염기의 이형 결실 돌연변이(c.3108delA; p.Lys1036Asnfs*14)가 발견되었다. 환자2는 25개월 여아로 가족력과 밀크커피색 반점이 있었고, 7623번 핵산에 G염기의 이형 결실돌연변이(c. 7623delG; p.Ile2541Serfs*7)의 틀이동돌연변이가 발견되었다. 새로운 변이의 보고를 통해 신경섬유종증 1형 환자와 가족의 유전상담과 임상관리에 유용하게 사용될 수 있겠다.
중추성 요붕증의 감별진단에 있어서의 혈중 ADH의 중요성
이호종,양인명,민선기,노정현,박철영,오승준,김덕윤,우정택,김성운,김진우,김영설,최영길 대한내분비학회 2001 Endocrinology and metabolism Vol.16 No.4
Background: Although the water restriction test (WRT) has been used as a standard test for the differential diagnosis of diabetes insipidus (DI), the measurement of plasma ADH concentration is also known to be useful method for differential diagnosis. Recent studies have shown that some patients with idiopathic central DI (CDI) were found to have a lesion on follow-up imaging studies. There have been no report in Korea on plasma ADH measurement for the differential diagnosis of DI, nor on follow-up imaging study of the idiopathic CDI. Methods: We retrospectively reviewed the clinical and laboratory findings of 26 patients (12 men, 14 women, age 9-65 years) with CDI, including pituitary MRI or CT scan, who had been diagnosed with WRT and had undergone plasma ADH concentration measurement. Results: 1) Clinical features of the patients with complete CDI did not differ from those of patients with partial CDI. 2) Maximal urine osmolality of complete CDI and partial CDI were 168±69 mOsm/㎏ and 431±141 mOsm/㎏, respectively, and the percentage increase in the urinary osmolality after ADH injection was 209±149% and 29±17%, respectively. 3) Among the 26 patients, 10 patients had their plasma ADH measured. Nine patients in this group were diagnosed as CDI by WRT and plasma ADH concentration of the 9 was compatible for CDI. The plasma ADH level was also inappropriately low in one patient who had been diagnosed with primary polydipsia by WRT, the patient was diagnosed as partial CDI. 4) The findings of follow-up MRI revealed isolated thickening of the pituitary stalk in two cases of idiopathic CDI diagnosed initially with MRI. Conclusion: This study suggests that the measurement of plasma ADH can ensure a better differential diagnosis between partial CDI and primary polydipsia, and that the patients with idiopathic CDI should be examined regularly with MRI brain scan, including the pituitary gland