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당뇨병과 흑색극세포증을 동반한 Laurence-Moon-Biedl 증후군 1 예
김순호,김훤,윤철승,위대철,임동명,임중규,허진득 대한내과학회 1994 대한내과학회지 Vol.47 No.2
Laurence-Moon-Biedl syndrome is characterized by obesity, mental retardation, polydactyly, hypogonadism, spastic paraparesis, and pigmented retinal dystrophy. We report a 19-year-old girl with Laurence-Moon- Biedl syndrome who showed obesity, polydactyly, mental retardation, and retinitis pigmentosa. In addition, she was found to have acanthosis nigricans and diabetes mellitus with insulin resistance. This suggests the Laurence-Moon-Biedl syndrome has a variable expression.
임동명(Dong Myung Lim),김훤(Hueon Kim),위대철(Dae Chel Wee),윤철승(Cheol Seung Yun),임연근(Yun Geun Lim),여향순(Hyang Sun Yeo),박홍배(Hong Bae Park) 대한소화기학회 1994 대한소화기학회지 Vol.26 No.3
Pyogenic liver abscess has been a serious illness with a uniformly fetal outcorne if left un- treated. Recently, there has been a steady rise in cornplications of pyogenic abscess with the irnprovement of diagnosis and management. Rupture into the peritoneum is second most fre- quent complication next to extention into the thorax. Rupture into the stomach and bowel is extremely rare. We report a case of hepatocolic fistula associated with ruptured multiple pyo- genic abscess in 59 years old female with the review of literatures.(Korean J Gastroenterol 1994; 26: S96%00)
임동명,김순호,임중규,허진득,장진형,김훤,위대철,윤철승 대한내분비학회 1992 Endocrinology and metabolism Vol.7 No.4
The syndrome of polyostotic fibrous dysplasia (PFD), cutaneous pigmentation and endocrinopathy (Albright's syndrome) continuous today to remain enigmatic. Not all patient with PFD have complete syndrome. In addition to the described in Albright's original patients, other endocrinopathies have been reported, including hyperthyroidism, acromegaly, hyperparathyroidism, Cushing's syndrome, adenoma of pituitary, thyroid, parathyroid and adrenal gland, vitamine Dresistant rickets and hypothalamic hypogonadotrophic hypogonadism. A 27-year-old man was found to have polyostotic fibrous dysplasia of bone, cutaneous pigmentation and acromegaly with diabetes mellitus. He started to have pain in left hip joint and it caused an alternation on his gait in 1983. X-ray study revealed that he had fibrous dysplasia. He gradually developed clinical feature of acromegaly. Subsequent biochemical study of growth hormone and radiologic study of the sellar confirmed the diagnosis of acromegaly. Bone biopsy and microscopic examination of the pituitary tumor tissue obtained through transsphenoidal procedure were reported to be fibrous dysplasia and acidophilic adenoma, respectively. The purpose of this report is to describe a patient with incomplete Albright's syndrome with acromegaly, which is very rare and we believe this is the first case to be reported in Korean literature.(J Kor Soc Endocrinol 7:402~408, 1992)