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상영호,이국형,정상립,김도원 ( Young Ho Sang,Kuk Hyeong Lee,Sang Lip Chung,Do Won Kim ) 대한피부과학회 1990 대한피부과학회지 Vol.28 No.5
A Case of Bullous Pemphigoid in a Patient with Chronic Renal Faiure Young Ho Sang, M.D., Kuk Hyeong Lee, M.D., Sang Lip Chung, M.D., Do Won Kim, M.D. Department of Dermatology, Kyungpook National University, School of Medicine, Toegu, Korea We report a case of bullous pemphigoid in patient with chronic renal failure. The patient was a 17 years-old female who had noted Henoch Schoenlein purpura with nephrotic syndrom(HSPN) 8 years ago. Three years prior to visit, HSPN had progressed to renal failure. Therefore she discontinued furosemide therapy for hypertension and has been treated with maintenance hemodialysis. She revealed multiple tense bullae on the face, neck, abdomen and axilla for 10 days. Histologic findings of early bullous lesion showed subepidermal bullae and direct immunofluorescent study of perilesional skin revealed linear lgG deposition at the dermoepidermal junction. We suggest that there is close relationship between bullous pemphigoid and chronic renal failure, especially uremia. (Kor J Dermatol 28(5) : 615-619, 1990)
김호준(Ho Joon Kim),성기영(Gi Young Sung),김도원(Do Won Kim),전재복(Jae Bok Jun) 대한피부과학회 1989 대한피부과학회지 Vol.27 No.1
Linear porokeratosis is a rare variant of porokerstosis and usually occurs after childhood. We report herein a case of linesr porokeratosis in an 18-year-old female. The lesions had developed since birth and were found on the nearly whole body, including the face, neck, axilla, chest, abdomen, back, and upper and lower extremities. Palms and soles were also affected. Biopsy specirnens from the left forearm and right sole showed typical cornoid lamellae. We could not see any improvement with a course of oral etretinate for 6 weeks.
상영호(Young Ho Sang),서호철(Ho Chul Suh),전재복(Jae Bok Jun),김도원(Do Won Kim) 대한피부과학회 1991 대한피부과학회지 Vol.29 No.1
We report a case of neurofibromatosis with unusual clinical manifestations in a 10-year-old girl. The patient showed an adult palm sized, brightly brown macular patch over the left temporal and zygomatic area with underlying tender soft swelling. The entire scalp and the patch were covered with short curling hairs Histopathologic P.XBmination of a biopsy specimen from the lesion of the zygomatic area revealed increased melanin pigments in the basal layer. Thin wavy fibers, intermingled with cells with oval to spindle shaped nuclei were lying in loosely textured strands and numerous mast, cells were noted in the deep dermis, Hypoplastic changes of left. temporal muscle, zygomatic arch and facial bone were found uncler the skin lesion by brain computed tomrgraphy. (Kor J Dermatol 29(1): 95 99, 1991)
이영헌(Young Hun Lee),서호철(Ho Chull Suh),김도원(Do Won Kim),정상립(Sang Lip Chung) 대한피부과학회 1993 대한피부과학회지 Vol.31 No.6
Addisons disease is the defieient production of glucocorticoid or mireralocorticoid or both, due to the destruction of the adrenal cor tex. We report a case of Addiaons disesse in a 26-year-old male who complained only of skin and oral mucosal hyperpigmentations without other constitutional symptorns, Physical examinations showed scanty pubic and axillary hsirs. On adrenocorticoid funtion study, the ACTH stimulstion test failed to rise the bassl plasme cortisol level and basal ACTH level was marked elevated st PM 6:00. Routine laboratory and other endocrinologic evaluations exhibited within normal limits. Radiologic findings showed negative on both cheet X-ray and abdominal MRI films. Gradisl disapperance of skin snd mucosal hyperpigmentation were noted following administration of phosiologic dose of corticosteriods. Almost normal appearance was obtaineg after 26 months treatment. (Kor J Dermatol 1993;31(6): 957962)
표면 항원 음성인 건강 검진 수진자와 만성 음주자에서 B형 간염 바이러스 잠재 감염
오성남 ( Sung Nam Oh ),연종은 ( Jong Eun Yeon ),한우식 ( Woo Sik Han ),최도원 ( Do Won Choi ),김지현 ( Ji Hyun Kim ),김연호 ( Yeoun Ho Kim ),박종재 ( Jong Jae Park ),김재선 ( Jae Seon Kim ),변관수 ( Kwan Soo Byun ),박영태 ( Young 대한내과학회 2008 대한내과학회지 Vol.75 No.5
Backgrounds/Aims: Hepatitis B virus (HBV) infection and chronic alcoholism are major risk factors for chronic liver disease in Korea. Methods: We investigated the prevalence of occult HBV infection in 198 non-alcoholic (group I) and 85 chronic alcoholic subjects (group II), none of whom showed the hepatitis B surface antigen (HBsAg). Among chronic alcoholics, 25 patients showed cirrhosis. Using serum samples stored at -70℃, liver enzymes, anti-Hbs, and IgG anti-HBc were measured via EIA and serum HBV DNA was quantified via real time PCR. Results: IgG anti-HBc seropositivity, an indicator of past infection, was higher in group II (64.7%) than in group I (43.4%; p<0.01). Eleven of 283 patients (3.2%) were seropositive for HBV DNA, indicating occult infection, but this value did not differ between groups (group I: 3.5%, 7/198; group II: 4.7%, 4/85; p=0.64). In group II, HBV DNA seropositivity was higher in cirrhotic patients (12%, 3/25) than in non-cirrhotic alcoholic liver disease (1.7%, 1/60; p=0.074). Conclusions: Past HBV infection was more prevalent in alcoholics than non-alcoholics, but the prevalence of occult HBV infection did not differ between groups. However, alcoholics with cirrhosis tended to show a higher prevalence of occult HBV infection. (Korean J Med 75:539-545, 2008)