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Hirschsprung's Disease의 진단과 치료 : 1992년도 현황 -대한소아외과학회 회원대상 선호도 설문조사-
유수영,김상윤,김우기,김인구,김재억,박귀원,박우현,박주섭,송영택,오수명,이두선,이명덕,이성철,장수일,정상영,정을삼,정풍만,주종수,최금자,최순옥,최승훈,허영수,황의호,Yeo, S.Y.,Kim, S.Y.,Kim, W.K.,Kim, I.K.,Kim, J.E.,Park, K.W.,Park, W.H.,Park, J.S.,Song, Y.T.,Oh, S.M.,Lee, 대한소아외과학회 1996 소아외과 Vol.2 No.1
This report present the result of the national survey of pediatric surgeons' preferences on diagnosis and treatment of Hirschsprung's disease(HD) carried out in 1993. The questionnaires were sent to twenty-seven members of the Korean Association of Pediatric Surgeons (KAPS) working in twenty-four institutions. The questionnaires were designed to determine the individual surgeon's preference for the methods of diagnosis and treatment of the disease. Twenty-three pediatric surgeons from twenty institutions returned completed forms. The total number of patients diagnosed with HD in 1992 was 190 in this group. The estimated incidence of HD was 1/3,900. The most important symptom was delayed meconium passing and the most preferred diagnostic procedure was barium study. Anorectal manometric examination was carried out by 13 pediatric surgeons and 19 confirmed the diagnosis before operation by rectal biopsy, 12 with full-thickness biopsy and 7 with suction. Frozen section biopsy during operation was done by 22 surgeons. Eight surgeons did one stage operation if the age of the patient is suitable. Definitive operation was usually done at the age of 6 to 11 months. The most preferred operation was Duhamel procedure done by 19. Enterocolitis was the most serious complication of HD. Most of patients had normal continence within 6 to 12 months after operation. The follow-up period was less than 6 years in 16 surgeons. The results were presented at the 9th annual meeting of KAPS in June of 1993. This is the first national survey of HD and it can provide guidelines of diagnosis and treatment of Hirschprung's disease even though it is not a detailed study of patient data.
1999년도 한국 신생아외과 현황 -대한소아외과학회 회원대상 전국조사(제 2 차)-
김우기,김상윤,김신곤,김인구,김재천,김현학,박귀원,박우현,송영택,오수명,유수영,이두선,이명덕,이성철,이석구,서정민,정상영,정성은,정을삼,정풍만,Kim, W.K.,Kim, S.Y.,Kim, S.K.,Kim, I.K.,Kim, J.C.,Kim, H.H.,Park, K.W.,Park, W.H.,Song, Y.T.,Oh, S.M.,Yoo, Y.S.,Lee, D.S 대한소아외과학회 2001 소아외과 Vol.7 No.1
To understand the current status of neonatal surgery in Korea, a survey was made among the 36 members of the Korean Association of Pediatric Surgeons. The response rate was 75 % (26 surgeons in 20 hospitals). Five hundred fifty three neonatal surgical patients treated in 1999 were analyzed. Regional numbers of patients were closely related to the regional population in most areas. Ano-rectal malformations (17 %), pyloric stenosis (16 %), Hirschsprung's disease (13 %), atresia/stenosis of the gut (11 %), esophageal atresia (8 %) were the most common anomalies treated. The majority of operations were done within the first week of life. Seventy one per cent of cases were major life threatening or so-called neonatal index cases. Over-all mortality was 8 per cent. Higher mortality was observed in patients with diaphragmatic hernia (26 %), gastro-intestinal perforation (18 %), NEC (18 %), and esophageal atresia(14 %). Higher mortality was observed in patients with extremely low birth weight (33%) and low birth weight (18 %). Associated anomalies were observed in 20 %. Prenatal ultrasound was performed in 36 per cent with sensitivity of 20 %. Result of this study was compared to the previous report (1994) and that of Japan (1998).
1994년도 한국신생아외과의 현황 - 대한소아외과학회 회원대상 전국조사 -
김우기,김상윤,김신곤,김인구,김재천,박귀원,박영식,박우현,박주섭,송영택,오수명,이두선,이명덕,이성철,장수일,정을삼,정풍만,주종수,최순옥,허영수,황의호,Kim, W.K.,Kim, S.Y.,Kim, S.K.,Kim, I.K.,Kim, J.C.,Park, K.W.,Park, Y.S.,Park, W.H.,Park, J.S.,Song, Y.T.,Oh, S.M.,Le 대한소아외과학회 1996 소아외과 Vol.2 No.1
To understand the current status of neonatal surgery in Korea, a survey was made among the 27 members of Korean Association of Pediatric Surgeons. Response rate among surgeons was 78 percent, eighteen hospitals participated in this study. Five hundred and three cases of neonatal surgical patients were analyzed. In Korea, about 50% of cases were treated at the hospital in the capital city area. Regional number of patients were closely related to the regional population. Imperforate anus(19%), atresia/stenosis of gut(12%), and Hirschsprung's diseases(12%) were sitting at the top in the list. Majority of operation was done within the first week of life, especially during the first 24 hour period. Eighty per cent was major or so called index cases. Mortality in so-called index cases was 17%. High mortality was observed in patients with diaphragmatic hernia(47%), gastrointestinal perforation(65%) and esophageal atresia(28%). Low birth weight babies showed higher mortality in gastrointestinal perforation, esophageal atresia and abdominal wall defect. These were compared to 1993 survey of Japanese Society of Pediatric Surgeons.
한국의 항문-직장 기형 -1999년도 대한소아외과학회 회원 대상 전국 조사-
이명덕,김상윤,김우기,김인구,김재억,김재천,김현학,박귀원,박우현,송영택,오수명,유수영,이두선,이석구,이성철,장수일,정상영,정성은,정을삼,정풍만,Lee, M.D.,Kim, S.Y.,Kim, W.K.,Kim, I.K.,Kim, J.U.,Kim, J.C.,Kim, H.H.,Park, K.W.,Park, W.H.,Song, Y.T.,Oh, S.M.,Yoo, S.Y 대한소아외과학회 2000 소아외과 Vol.6 No.2
The purpose of the survey was to clarify the clinical features and management of the anorectal malformations (ARM) in Korea. Twenty-seven members of the Korean Association of Pediatric Surgeons were surveyed. The members completed a case registration form for each patient during the two years period of 1996-1997, and a questionnaire that contained their management preferences for primary and complicated patients. Twenty-four members of the 22 institutions registered 295 cases of the ARM, and 27 out of 34 members (77.1 %) responded to the questionnaire. The patients were classified by the Wingspread classification of ARM(1984). The case registration form was a modification of Wingspread workshop for the postoperative assessment and case registration. The male to female ratio was 1.7 : 1. The average number of patients per surgeon was 6.1 cases per year. Prematurity(< 36 weeks) was present in 1.9 % of cases and low birth weight (< 2.6 Kg) in 12.1 %. Among 187 male patients, 62 were high(H) type, 29 intermediate(l) type, 88 low(L), and 8 unclassified. In female, there were 2 cases of cloacal anomalies(C), 4 H type, 30 I type, 66 L type and 6 unclass ified. For male, 87.9 % of H and I type were operated by the Pena procedure, but only 7.9 % in L types. In female, all of C, H and I types, and 40.9 % of L type were done by the Pena procedure. One case expired (MR; 0.003%) as a result of surgical complication. Over-all complication rate was 12.5 %. Among 6 cases of reoperation, 4 were failed Pena procedures. Among 140 colostomies sigmoid colon was utilized in 75.7%, and loop colostomy was commonly used. Ten surgeons prefered primary maturation of the stoma. In conclusion, posterior sagittal anorectoplasty is popular for high types of ARM in this country, but considerable number of patients are still suffering from failed operations. For better understanding and analysis, necessity of prospective study by new classification was discussed.