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신장 조직 검사에서 사구체 면역침착을 보인 베게너 육아종증 1예
서영진 ( Young Jin Seo ),김윤정 ( Yoon Jung Kim ),문지미 ( Ji Mi Moon ),최혜윤 ( Hae Yoon Choi ),우진현 ( Jin Hyun Woo ),최성재 ( Seong Jae Choi ),이영호 ( Young Ho Lee ),지종대 ( Jong Dae Ji ),정운용 ( Woon Yong Jung ),송관규 ( G 대한신장학회 2009 Kidney Research and Clinical Practice Vol.28 No.6
Rapidly progressive glomerulonephritis (RPGN) in Wegener`s granulomatosis patients typically has been characterized by pauci-immune glomerulonephritis (PIGN). In some patients, however, significant amount of glomerular immune deposits was detected and reported that they may have poor prognosis. A 30 year-old-female visited due to the skin rash of both lower extremities, arthralgia and nasal stiffness. She had sinusitis, lung opacity, and proteinuria. Serologic PR-3 ANCA was positive and histologic findings of nasal cavity and lung also showed necrotizing vasculitis and granuloma. Thus we could diagnose Wegener`s granulomatosis. However, gross hematuria developed and renal function worsened in spite of treatment with high dose prednisolone and oral cyclophosphamide. Therefore we performed a kidney biopsy. The kidney biopsy showed crescentic glomerulonephritis with Ig A deposition in the mesangium. We experienced a case of Wegener`s granulomatosis patient with significant IgA deposition in glomeruli. We report this case with brief review of the literature.
대장암 환자에서 발생한 Clostridium septicum에 의한 감염성 대동맥류 파열 1예
최혜윤,박정원,노지윤,허중연,김미정,최원석,조유미,송준영,김우주,정희진 대한감염학회 2009 감염과 화학요법 Vol.41 No.3
Infected aortic aneurysm a life-threatening disease entity. Clostridium septicum is a very rare pathogen of infected aneurysms that carries a high mortality rate and demonstrates a strong association with derlying colonic or hematologic neoplasm. Herein, we report a case of ruptured aortic aneurysm infected by C. septicum in a patient with colon cancer. This is the first reported case of infected aneurysm caused by C. septicum in Korea. Early diagnosis, appropriate antibiotic therapy, and prompt surgical interventions are required considering the rapid downhill progression of C. septicum-induced infected aneurysm.