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신우요관이행부폐색과 동반된 일과성 가성저알도스테론혈증 1례
최준기,한혜원,유한욱,박영서,Choi Jun-Gi,Hahn Hye-Won,You Han-Wook,Park Young-Seo 대한소아신장학회 2004 Childhood kidney diseases Vol.8 No.1
저자들은 신우요관이행부폐색에 의한 심한 수신증이 있는 한 환아에서 2M NaCl 경구투여만으로 증상이 호전되고 폐색성 요로 병증의 교정 이후 재발되지 않는 일과성 가성저알도스테론혈증 1례를 경험하였기에 보고하는 바이다. We report a 2-month-old boy who presented with severe hyponatremia and hyperkalemia secondary to ureteropelvic junction(VPJ) obstruction. By prenatal ultrasonography at 19 weeks of gestation, severe hydronephrosis was found which was confirmed postnatally Pyeloplasty was done on the 45th day of life, and fifteen days after pyeloplasty, non-bilious vomiting, decreased activity and dehydration developed. Severe hyponatremia and hyperkalemia were observed, as a result of elevated serum aldosterone and plasma renin activity. The anterior posterior pelvic diameter(APPD) and Society for Fetal Urology(SFU) grade measured showed no interval change before and after pyeloplasty. Pseudohypoaldosteronism was diagnosed, and 2M NaCl was administrated orally for 7 days. The electrolyte imbalance was corrected, and 8 weeks later, the elevated levels of aldosterone and plasma renin activity were normalized. The left hydronephrosis was improved at 5 months of age. We hereby report a transient pseudohypoaldosteronism secondary to UPJ obstruction with a review of the literature.
마이코플라스마 폐렴의 호산구성 기도 염증과 천식의 병인과의 연관성
최준기 ( Jun Gi Choi ),고지연 ( Ji Yeon Koh ),김효빈 ( Hyo Bin Kim ),김창근 ( Chang Geun Kim ) 대한소아알레르기호흡기학회(구 대한소아알레르기 및 호흡기학회) 2009 소아알레르기 및 호흡기학회지 Vol.19 No.1
목적: 기도 내 호산구의 활성화와 탈과립 현상이 마이코플라스마 폐렴과 어떻게 관련이 있는지를 알아보고자 하였다. 이를 위해 호산구의 활성도를 나타내는 염증성 매개체인 EDN과 ECP를 마이코플라스마 폐렴 환자의 객담 및 혈청에서 측정하여 그 면역학적 기전을 알아보고자 하였다. 방법: 마이코플라스마 폐렴 환자 40명의 급성기와 회복기, 안정기 천식군 20명, 정상 대조군 20명을 대상으로 하여, 유도 객담 검사 및 혈액을 체취한 후 EDN, ECP를 측정하여 세 군간의 차이를 분석하였다. 결과: 마이코플라스마 폐렴군 급성기의 혈청 EDN, ECP 농도는 안정기 천식군과 유의한 차이를 보이지 않을 만큼 증가되어 있었고, 회복기의 혈청 EDN 농도는 천식군에 비하여 의미 있게 낮아진 소견을 보였다. 마이코플라스마 폐렴군 급성기의 객담 EDN 농도는 안정기 천식군과 유의한 차이를 보이지 않을 만큼 증가되어 있었고, 회복기의 객담 EDN 농도는 안정기 천식군에 비하여 의미 있게 낮아진 소견을 보였다. 마이코플라스마 폐렴군 급성기의 객담 ECP 농도는 안정기 천식군과 유의한 차이를 보이지 않을 만큼 증가되어 있었고, 회복기의 객담 ECP 농도는 안정기 천식군의 값에 비하여 낮아진 경향을 보였지만 통계적으로 의미 있는 차이는 보이지 않았다. 결론: 호산구의 탈과립과 활성화를 나타내는 호산구염증 매개체가 마이코플라스마 폐렴의 급성기에는 증가하고 회복기에는 감소하는 결과를 보임으로써, 호산구의 탈과립이 마이코플라스마 폐렴의 병태생리학적 기전에서 중요한 역할을 함을 보여주었다. Purpose: To investigate whether airway eosinophilic degranulation develops in Mycoplasma pneumonia (M. pneumonia), and to elucidate the association between M. pneumonia and asthma. Methods: Forty patients with M. pneumonia, 20 stable asthma patients (stable asthma) and 20 normal controls were recruited from October 2005 to February 2007. In the M. pneumonia, blood and induced sputum sampling were collected at admission (acute stage) and 6 to 8 weeks later (convalescent stage). Eosinophil-derived neurotoxin (EDN) and eosinophil cationic protein (ECP) levels in sputum and serum were measured in all 3 groups. Results: Serum levels of EDN and ECP in the acute stage of M. pneumonia were comparable to those in the stable asthma group. However, in the convalescent stage of M. pneumonia, EDN and ECP levels were significantly lower than in the stable asthma (P<0.01 and P<0.05, respectively). Sputum levels of EDN and ECP levels in the acute stage of M. pneumonia were comparable to those in the stable asthma. Sputum EDN levels in the convalescent stage of M. pneumonia were significantly lower than those in the stable asthma (P<0.05), and sputum ECP levels were lower than those in the stable asthma, which was not statistically significant. Conclusion: Eosinophilic degranulation may play an important role in the pathogenesis of M. pneumonia, which suggests the association between M. pneumonia and asthma. [Pediatr Allergy Respir Dis(Korea) 2009;19:63-70]
영유아천식 악화시 Eosinophil-derived Neurotoxin 및 Eosinophil Cationic Protein 농도와 기도벽 비후 사이의 연관성
김효빈 ( Hyo Bin Kim ),최준기 ( Jun Gi Choi ),윤운기 ( Un Ki Youn ),마영수 ( Young Soo Ma ),신보문 ( Bo Moon Shin ),김정숙 ( Joung Sook Kim ),김창근 ( Chang Keun Kim ),Rachel Fletcher 대한소아알레르기 및 호흡기학회 2007 소아알레르기 및 호흡기학회지 Vol.17 No.2
Swyer-James 증후군에서 주기적 고용량 스테로이드 투여 후 완전 관해를 보인
김문섭 ( Mun Sub Kim ),최준기 ( Jun Gi Choi ),김효빈 ( Hyo Bin Kim ),김정숙 ( Joung Sook Kim ),김창근 ( Chang Keun Kim ) 대한소아알레르기호흡기학회 2008 소아알레르기 및 호흡기학회지 Vol.18 No.3
Swyer-James syndrome (SJS) is characterized by a small-or normal-sized unilateral hyperlucent lung with decreased vascularity and air trapping on plain radiographs. SJS is considered to be a postinfectious form of bronchiolitis obliterans and has occurred following childhood pulmonary infection by adenovirus, measles, influenza virus, Bordetella pertussis, Mycobacterium tuberculosis or Mycoplasma pneumoniae. The standard treatment modality for SJS is supportive care. Despite the prominent role of inflammation in the pathogenesis of SJS, the use of corticosteroids has remained controversial. We report herein a case of SJS which was successfully treated with monthly methylprednisolone pulse therapy, resulting in complete remission as verified by high resolution computed tomography. [Pediatr Allergy Respir Dis(Korea) 2008;18:260-265]
Human Rhinovirus Group A의 치명적인 하기도 감염 증례
윤정림 ( Jung Rim Yoon ),최준기 ( Jun Gi Choi ),김효빈 ( Hyo Bin Kim ),김창근 ( Chang Keun Kim ),( Zak Callaway ) 대한소아알레르기호흡기학회(구 대한소아알레르기 및 호흡기학회) 2010 소아알레르기 및 호흡기학회지 Vol.20 No.1
Human rhinoviruses (HRV) 는 성인과 소아에서 상기도 감염의 가장 흔한 바이러스로 알려져 왔다. 최근 HRV의 하기도 감염이나 천식과의 연관성에 대한 연구들이 보고되고 있으며, HRV가 3개월 미만 영아에서 SIDS (sudden infant death syndrome)의 병인 중에 하나로 알려져 있다. 이에 저자들이 경험한 HRV의 치명적인 하기도 감염의 증례 2례를 보고하는 바이다. Human rhinoviruses (HRV) mostly cause mild and self-limiting upper respiratory tract infections. We report 2 infants with acute respiratory failure requiring mechanical ventilation, 1 of whom deteriorated to death. The causal pathogen was HRV group A confirmed by multiplex-PCR. In Korea, this is the first report of severe respiratory failure caused by HRV group A during the same season. [Pediatr Allergy Respir Dis (Korea) 2010;20:76-80]
아토피피부염에서 포도상구균 집락과 장독소 유무에 따른 임상양상
반혜련 ( Hye Ryun Ban ),이소연 ( So Yeon Lee ),최준기 ( Jun Gi Choi ),김효빈 ( Hyo Bin Kim ),송영화 ( Young Wha Song ),김병주 ( Byoung Joo Kim ),유진호 ( Jin Ho Yu ),김미나 ( Mi Na Kim ),홍수종 ( Soo-Jong Hong ) 대한천식알레르기학회 2008 천식 및 알레르기 Vol.28 No.2
Background: Atopic dermatitis (AD) is a chronically relapsing allergic skin inflammatory disease with a high incidence in the early childhood. Staphylococcus aureus colonization (S. aureus) is frequent in the skin of patients with AD and is one of the important environmental factors that develop or exacerbate this disorder. Objective: The aim of this study was to investigate the different clinical features of AD with S. aureus colonization and to seek its relation with the clinical features of AD. Method: We recruited 342 children with AD who visited the pediatric allergy clinic in Asan Medical Center from July 2003 to January 2007. They were divided into 2 groups based on the results of skin cultures: group 1 with no bacteria cultured and group 2 with S. aureus cultured. The clinical and laboratory data, such as SCORAD (SCORing Atopic Dermatitis), total eosinophil count (TEC), eosinophil fraction (%), serum total IgE, serum eosinophil cationic protein (ECP) and staphylococcal enterotoxin A and B -specific IgE levels, were evaluated and were compared between individual groups. Result: There was a statistical difference between groups 1 and 2 in TEC, eosinophil fraction (%), total IgE, serum ECP and SCORAD index. There was a significant difference in total IgE between the enterotoxin-negative and enterotoxin-positive groups. S. aureus colony counts were significantly correlated with total eosinophil count (r=0.259, P= 0.003), eosinophil (%) (r=0.196, P=0.009), and serum ECP (r=0.212, P=0.035). Total IgE levels were significantly correlated with specific IgE levels to enterotoxins A and B (r=0.335, P=0.012; r=0.393, P=0.002). S. aureus colonization and specific IgE levels to staphyloccal enterotoxins A were correlated with SCORAD index and total IgE levels. Conclusion: Skin infections with S. aureus may be associated with pathogenesis of AD. (Korean J Asthma Allergy Clin Immunol 2008;28:105-112)