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재발형 다발성경화증처럼 발현한 원발성 Sjogren 증후군 2예
조정희,김승민,김지현,주종규,이미희,신혜원,도원영,선우일남 대한신경과학회 2004 대한신경과학회지 Vol.22 No.4
Sjögren's syndrome is a slowly progressive autoimmune disorder that predominantly affects major exocrine glands, and may also involve the central nervous system (CNS). It is sometimes very difficult to differentiate the CNS Sjögren's syndrome from multiple sclerosis. Here, we report two cases of Sjögren's syndrome who developed variable neurological symptoms mimicking the relapsing-remitting form of multiple sclerosis. There had been several relapses during the course of interferon-beta treatment but no relapses have occurred after steroid maintenance therapy
가역적 치매 증상을 보인 상시상 정맥동 경막 동정맥루 1예
김홍식,조필자,김정찬,주종규,김승민,선우일남 대한신경과학회 2005 대한신경과학회지 Vol.23 No.5
A 58-years-old man came to the hospital because of progressive intellectual deterioration, gait disturbance and postural instability for 6 months. Neuropsychological tests showed severe impairment of memory and executive functions, and dural arteriovenous fistula of the superior sagittal sinus (dAVF of SSS) was found on brain MRI and angiography. The symptoms were markedly improved after selective transvascular embolization treatments. Even though the dAVF of SSS is a rare cause of dementia, we suggest that it can be one of the treatable causes of dementia.