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급성 포르피리아 발작중 발생한 심한 저나트륨혈증 1 예
정철원(Chul Won Jung),전은실(Un Sil Jeon),정우경(Woo Kyung Chung),김원석(Won Seog Kim),조종태(Jong Tai Cho),안규리(Cu Rie Ahn),한진석(Jin Suk Han),김성권(Suhng Gwon Kim),이정상(Jung Sang Lee) 대한내과학회 1995 대한내과학회지 Vol.49 No.2
Hepatic porphyria shows impaired heme biosynthesis predominantly in the liver and usually presents with abdominal pain, vomiting, photosensitivity and neurologic abnormalities and sometimes with hyponatremia accompanied by syndrome of inappropriate antidiuretic hormone secretion(SIADH). We report a case seemed to be a hereditary coproporphyria presenting with acute abdominal pain and vomiting. She had severe hyponatremia with the feature of SIADH and peripheral neuropathy which was provoked by the ingestion of alcohol, poor oral intake and by the administration of imipramine. She was thought to have hereditary coproporphyria by the clinical feature, stool porphyrin and quantitation of the 24 hour urine δ-aminolevulinic acid, porpho-bilinogen and porphyrins. Supportive treatment with NaCI infusion and propranolol resulted in symptomatic recovery and she was discharged after education of precipitating factors.
정철원 ( Jung Chul-won ),윤병조 ( Yun Boung-jo ) 한국구조물진단유지관리공학회 1998 한국구조물진단유지관리공학회 학술발표대회 논문집 Vol.2 No.1
Failure probabilities can be estimated by a variety of methods such as FOSM(first order, second moment), AF0SM(advanced FOSM), etc. These methods require the evaluation of the derivatives of the failure equation, which is difficult and even impossible in many situations. In this paper PEM(point estimation technique) is described by which the failure probability could be obtained using the values of the failure function alone evaluated at a number of preselected points. Depending on the number of variables in the problem, the number of points for the function evaluation could be large. To identify the stability of cantilever retaining wall in safe state by the deterministic method, these potential modes of such geotechnical failures as overturning, horizontal sliding and bearing capacity are analyzed using PEM.
Fuzzy-Basian법에 의한 R.C도로교의 신뢰성 및 안전도평가
정철원 ( Jung Chul-won ),이중빈 ( Lee Cheung-bin ),나기현 ( Na Gi-hyun ),박주원 ( Park Ju-won ) 한국구조물진단유지관리공학회 1997 한국구조물진단유지관리공학회 학술발표대회 논문집 Vol.1 No.1
In this paper, an attempt is made to apply the concept of Fuzzy-Bayesian theory to the Reliability Analysis of R.C(Reinforced Concrete) Bridge, uncertainty states are represented in terms of fuzzy sets which define several linguistic variables such as “good”, “average”, ”poor”, etc. Especially, the concept of fuzzy conditional probability aids to derive a new reliability analysis which includes the subjective assessment of engineers without introducing any additional correction factors. Several numerical examples are presented to illustrate the method proposed herein.
이원섭(Won Sup Lee),정철원(Chul Won Jung),이근석(Keun Seok Lee),안진석(Jin Seok Ahn),김성민(Sung Min Kim),오명돈(Myoung Don Oh),박선양(Seon Yang Park),김병국(Byoung Kook Kim),최강원(Kang Won Choe) 대한내과학회 1996 대한내과학회지 Vol.51 No.6
Cytomegalovirus(CMV) pneumonia is a frequent complication of bone marrow transplantation and among patients with cytomegalovirus seropositivity, approximately 15 to 20% of deaths occurring after marrow transplantation can be attributed to CMV disease of the lung. We report two cases of cytomegalovirus pneumonia following allogenic bone marrow transplantation. One case received preemptive therapy of ganciclovir and the other one was given ganciclovir and immune globulin after documentation of cytomegalovirus pneumonia. The former case recovered while the latter died because of respiratiory failure by progressive pneumonia.
다양한 산화물 기판 위에 RF 마그네트론 스퍼터링 방법으로 성장된 ZnO 박막의 특성 비교
이재욱,정철원,한석규,최준호,홍순구,조형균,송정훈,이정용,Lee, Jae-Wook,Jung, Chul-Won,Han, Seok-Kyu,Choi, Jun-Ho,Hong, Soon-Ku,Cho, Hyung-Koun,Song, Jung-Hoon,Lee, Jeong-Yong 한국전기전자재료학회 2007 전기전자재료학회논문지 Vol.20 No.4
ZnO thn films are grown on five kinds of oxide substrates including $c-Al_2O_3(0001),\;r-Al_2O_3(01-12)$, MgO(100), MgO(111), $NdGaO_3(110)$ by rf magnetron sputtering and effects substrate types on properties of ZnO thin films ate investigated. In order to compare the substrate effects one growth condition is selected and all the films are grown by the same growth condition. Structural and optical properties of the ZnO films ate different depending on the substrates although the films ate not epitaxial but polycrystalline. The ZnO film grown on $NdGaO_3(100)$ substrate shows the best overall properties among the films grown on substrates investigated in this study.
폐 , 흉벽 , 중추신경계를 침범한 전신형 모균증 1 예
박수제(Su Je Park),정철원(Chul Won Jung),박언섭(Eon Sub Park),박애자(Ae Ja Park),이상재(Sang Jae Lee) 대한내과학회 1998 대한내과학회지 Vol.54 No.6
Disseminated mucormycosis is a rare but fatal fungal infection with a high mortality rate. Mucormycosis usually occurs in immunocompromised patients such as in patients with diabetes mellitus, leukemia, lymphoma and in patients undergoing anticancer therapy, prolonged immunosuppression, and antibiotic therapy. Early diagnosis and the resolution of predisposing factors, including the use of amphotericin B and wide surgical resection, are essential to make a successful outcome. We report a well-documented case of disseminated mucormycosis involving lung parenchyme, chest wall and central nervous system with the review, of literatures in patients with uncontrolled diabetes and Evans syndrome. Typical broad, branching in right. angle, non-septated hyphae were observed in the biopsy of the nodular mass on the anterior chest wall. Chest CT and brain MRI found three pulmonary cavitary lesions and multiple small nodules with ring-enhancement in the cerebrum, cerebellum and the brainstem. Although 1,116mg of amphotericin B in sum was given with flucytosine, she expired due to progressive mucormycosis.
손상균 ( Sang Kyun Sohn ),정철원 ( Chul Won Jung ),조덕연 ( Deog Yeon Jo ),정준원 ( June Won Cheong ),대한혈액학회만성골수성백혈병연구회 ( Chronic Myelogenous Leukemia Working Party The Korean Societ ),김대영 ( Dae Young Kim ),이정옥 ( 대한내과학회 2015 대한내과학회지 Vol.88 No.4
Background/Aims: The first edition of the Korean treatment guidelines for chronic myelogenous leukemia (CML) was published in 2006. We intend to update those guidelines to include the use of next-generation tyrosine kinase inhibitors (TKIs). Methods: New guidelines were developed in 2012 based on the results of a survey and a consensus meeting of various Korean experts, the reports of recent clinical studies, and updated guidelines from external study groups. Results: An assessment of risk factors is strongly recommended before treating newly diagnosed chronic phase CML. Imatinib, dasatinib, and nilotinib are reimbursable in Korea as first-line treatments, and the patient`s age, comorbidities, and possible adverse events should be considered in the choice of treatment. Molecular studies are recommended for assessing treatment efficacy instead of invasive cytogenetic response evaluations, and an early response is believed to correlate with a good prognosis. Second-line TKIs can be considered for patients who fail or are intolerant of first-line therapy, pending analysis of ABL tyrosine kinase mutation status. For treating advanced stages, a combination of TKIs with cytotoxic agents and hematopoietic cell transplantation is recommended. The adverse effects of TKI therapy can be managed via dose reduction and supportive care, or switching to an alternate TKI. Conclusions: The use of TKIs has improved the outcome of CML treatment. Treatment-free remission after discontinuing TKIs might be possible in select patients who achieve sufficient response, indicating that curative treatment for CML can be expected in the future.