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급성 발열성 호중구성 피부병이 동반된 골수이형성 중후군 2 예
양형인(Hyung In Yang),김현우(Hyun Woo Kim),김시영(Si Yonng Kim),윤휘중(Hwi Joong Yun),조경삼(Kyung Sam Cho),양문호(Mun Ho Yang) 대한내과학회 1991 대한내과학회지 Vol.41 No.5
Acute febrile neutrophilic dermatosis (Sweets syndrome) was introduced to the dermatologic literature by Sweet in 1964, that is charactertized by pyrexia, neutrophilia, erythromatous painful, cutaneous plaques, primarily located on the upper extremities, head and neck; a dense dermal infiltrate of neutrophils; and a prompt response to corticosteroid therapy. That is frequently associated with cancer, solid tumor and especially hematologic malignancies. Patients with malignancy associated Sweet's syndrome have more severe cutaneous features, plaques, nodules, vesicular, bullous and even ulcerative skin lesion, the lesion frequently occur on, especially lower extremities, trunk and back, oral mucous membrane in hematologic mailignancy, have more common extracutaneous involvement, par-ticularily musculoskeletal, renal, eyes, lung and liver. A comparison of the other clinical features present in idiopathic and malignancy-associated Sweets syndrom-me reveals that female predominance, a prior respiratory tract infection and neutrophilia were less frequent. Importantly, Sweets syndrome preceded the diagnosis or was the presenting sign if either a new or recurrent tumor in almost two third of the patients with an associated malignancies. We experienced two cases of acute febrile neutrophilic dermatosis with underlying myelodysplastic syndrome. The one was 42-year-old, woman, she complained nausea, abdominal pain and diarrhea. she had fever, myalgia, neutrophilia and elevated ESR. There were multiple erythematous painful plaques on her extremities and lidedema on her right eye. On bone marrrow biopsy, myelodysplastic syndrome was confirmed. On skin biopsy, dense dermal neutrophil infiltration was appeared. After corticosteroid therapy, her clinical symptoms improved. The oher was 56-year-old, woman. she had throat infection, fever, neutrophilia, edema and vesicles on her both hands. she had no response to antibiotics, had continuing fever. On bone marrow biopsy, myelodysplas-tic syndrome was suggested. On skin biopsy, dermal neutrophilic infiltration, She was diagnoesd to Sweet's syndrome. After corticosteroid therapy, skin lesion were disappeared and fever was absent.
급성 백혈병에 병발된 침윤성 Aspergillus 감염의 치료 1 예
이윤희,유진상,최성근,박주철,조경삼,윤휘중,지현숙 대한내과학회 1987 대한내과학회지 Vol.33 No.6
Invasive Aspergillosis in the immunosuppressed host is usually lethal. There are difficulties in the diagnosis and treatment. We report a case of invasive pulmonary aspergillosis complicating acute myelogenous leukemia, which was sucessfully treated with administration of Amphotericin B and left upper lobectomy of lung. A 29 year old man was admitted to Kyung Hee University Hospital with acute myelogenous leukemia. On 14th day, pneumonia was found on both upper lung. Antibiotics were administreated without improvement. Bronchoscopic findings were nospecific and sputum culture was negative. On 46th day, chest films showed improvement of right upper lobe pneumonia but a cavity with a filling defect (meniscus sign) was found in the left upper lung fields. A two-month course of amphotericin B (960 mg total dose) and left upper lobectomy (On 74 th day) was completed. He is now in complete remission of leukemia and without evidence of Aspergillus infection, after postoperation 16 months.