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이승우,이상학,여동승,이숙영,김석찬,김관형,문화식,송정섭,박성학,정은선,Lee, Seung-Woo,Lee, Sang-Haak,Yeo, Dong-Seung,Lee, Sook-Young,Lee, Seok-Chan,Kim, Kwan-Hyoung,Moon, Hwa-Sik,Song, Jeong-Sup,Park, Sung-Hak,Jung, Eun-Sun 대한결핵및호흡기학회 2002 Tuberculosis and Respiratory Diseases Vol.53 No.6
Amiodarone 폐독성은 약제 복용력이 있는 환자에서 새로운 증상과 X-선의 변화가 있을 때 의심하여야 하며 울혈성 심부전이나 폐감염증, 폐색전증, 악성종양 등과 감별하는 것이 중요하다. 진단은 임상적, 방사선학적, 조직학적 소견을 종합하여 내릴 수 있으며 대부분의 경우에는 약제 중단을 통해서 폐독성의 호전을 기대할 수 있으나 일부에서는 호흡부전으로 진행하거나 기존의 심부정맥의 재발 등으로 인하여 사망하는 경우도 있다. 저자들은 심부정맥으로 amiodarone을 사용하던 환자에서 치명적인 폐독성이 발생한 4예를 경험하였기에 이를 문헌고찰과 함께 보고하는 바이다. The lungs are frequently the site of adverse drug reactions because of their higher oxygen concentration, the distinctive properties of the pulmonary circulation, and the close proximity of the alveolar epithelium to the blood. Amiodarone, an iodinated benzofuran derivative, is an effective antiarrhythmic drug commonly used for refractory tachyarrhythmia. However, it has a wide range of adverse effects, the most serious of which is lung disease. Most patients present with the insidious onset of dyspnea and a nonproductive cough, and generally recover after withdrawing the drug. We recently experienced four fatal cases of amiodarone pulmonary toxicity. Therefore, we discuss these unusual drug-induced pulmonary toxicity cases with a review of the relevant literature.
간질성 음영의 급격한 악화를 보인 림프관성 폐암종증 1예
정정,장재순,주현중,이상학,여동승,현대성,최영미,김석찬,이숙영,문화식,송정섭,박성학,Jung, Jung,Jang, Jae-Soon,Joo, Hyun-Jung,Lee, Sang-Haak,Yeo, Dong-Seung,Hyun, Dae-Seong,Choi, Young-Mee,Kim, Seok-Chan,Lee, Sook-Young,Moon, Hwa-Sik,Song 대한결핵및호흡기학회 2000 Tuberculosis and Respiratory Diseases Vol.48 No.6
호흡곤란과 마른 기침을 주소로 내원한 52세 여자 환자가 미만성 간질성 폐음영의 급속한 악화소견을 보이며 급성호흡부전으로 진행하여 입원 11일째 사망하였다. 입원 초기에 임상적 진단용 내리는데 어려움이 있었으나 기관지경을 통한 경기관지 폐생검상 선암의 림프관성 폐전이를 확진할 수 있었다. 저자들은 암을 아직 진단받지 않은 상태의 환자에서도 미만성 간질성 폐음영이 진행하는 경우 림프관성 폐암종을 감별진단으로 고려하여야 하며 경기관지 폐생검이 진단에 유용할 수 있을 것으로 생각한다. A 52-year-old woman was presented with 2-week history of increasing dyspnea and dry cough. The chest radiograph revealed bilateral reticular infiltrates. Radiographic infiltrates were rapidly progressed and symptoms from hypoxemia were aggravated. The patient was intubated and bronchoscopy with transbronchial lung biopsies was performed. Biopsies revealed lymphatic vessels plugged by nests of metastatic adenocarcinoma. She died 11 days after admission despite of intensive ventilatory support. We had difficulties in the diagnosis of lymphangitic lung carcinomatosis at initial presentation of her illness because the progression was unusually rapid. Lymphangitic lung carcinomatosis shoud should be included in the differential diagnosis of patients showing rapidly progressive interstitial radiographic findings. Also, transbronchial biopsy may be a useful tool to confirm the diagnosis.
이달의 X-선 : 간질성 음영의 급격한 악화를 보인 림프관성 폐암종증 1예
정정 ( Jeong Jeong ),장재순 ( Jang Jae Sun ),주현중 ( Ju Hyeon Jung ),이상학 ( Lee Sang Hag ),여동승 ( Yeo Dong Seung ),현대성 ( Hyeon Dae Seong ),최영미 ( Choe Yeong Mi ),김석찬 ( Kim Seog Chan ),이숙영 ( Lee Sug Yeong ),문화식 대한결핵 및 호흡기학회 2000 Tuberculosis and Respiratory Diseases Vol.48 No.6
류마치스성 관절염과 동반된 Ochronosis ( 조직갈변증 ) 1 예
이광욱(Kwang Uk Lee),강필중(Pill Joong Kang),이헌직(Hun Jig Lee),김진도(Jin Do Kim),이종수(Jong Soo Lee),여동승(Dong Seung Yeo),윤영권(Young Kwon Yun),황병욱(Byung Uk Hwanhg),최장락(Jang Rack Choi),김상현(Sang Hyun Kim),곽임수(Ihm So 대한내과학회 1991 대한내과학회지 Vol.41 No.1
Ochronosis, which is autosomal recessive, results from a decreased amount of the enzyme homogentisic acid oxidase, due to which tyrosine and phenylalanine cannot be broken down via the normal pathway. The clinical manifestations of ochronosis usually appear after the age of 30 as a result of the deposition of pigment in the extracellular macromolecules of the connective tissue, particular of the skin and joints. The diagnosis is made by determination of urinary homogentisic acid excretion, and the clinical and radiological findings can help to diagnose this disease. We report a case of Ochronosis with Rheumatoid arthritis presented with skin pigmentation and migrating polyarthritis in a 57-year-old female patient who was managed with an antiinflammatory agent, steroids, and symptomatic care.