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국한성 결절성 근염(Localized nodular myositis) 2례
서기현 ( Gi Hyeon Seo ),김지은 ( Jee Eun Kim ),김진석 ( Jin Seok Kim ),고은미 ( Eun Mi Koh ),이종헌 ( Chong H. Rhee ),안중모 ( Joong Mo Ahn ),서연림 ( Yeon Lim Suh ) 대한류마티스학회 1998 대한류마티스학회지 Vol.5 No.1
Localized nodular myositis is an uncommon benign inflammatory myopathy of unkonwn cause affecting skeletal muscle and, presenting as a localized painful swelling within the soft tissue of an extremity. Histological examination reveals lymphocytic infiltration, scattered muscle fiber necrosis and regeneration, and interstitial fibrosis. MRI finding is an enhancement with increased signal intensity around the lesion. We report two cases of localized nodular myositis presenting as pseudothrobothrombophlebitis. We believe this is the first case report of localized nodular myositis in Korea.
문성오 ( Mun Seong O ),서용수 ( Seo Yong Su ),김철중 ( Kim Cheol Jung ),이지수 ( Lee Ji Su ),최수란 ( Choe Su Lan ),서연림 ( Seo Yeon Lim ),권지은 ( Kwon Ji Eun ),김종화 ( Kim Jong Hwa ) 대한산부인과학회 2004 Obstetrics & Gynecology Science Vol.47 No.4
Cloacal anomaly is an extremely rare congenital malformation results from a failure in the development of the urorectal fold that separates the rectum from uterovaginal tract. It is characterized by the presence of a single duct where the gastrointestinal
허림 ( Rimm Huh ),안소윤 ( So Yoon Ahn ),성세인 ( Se In Sung ),유혜수 ( Hye Su Yoo ),서연림 ( Yeon Lim Seo ),이지훈 ( Jee Hun Lee ),장윤실 ( Yun Sil Chang ),박원순 ( Won Soon Park ) 대한주산의학회 2013 Perinatology Vol.24 No.3
Glycogen storage disease (GSD) is a group of heterogeneous disorders of glycogen metabolism that results in abnormal storage of glycogen in multiple organs. Clinical manifestations of GSD vary according to the basic enzyme defect. Only types II, IV, V or VII of GSD have been known to manifest in the infantile period. Of the 11 types of GSD, the congenital subtype of GSD type IV is characterized by severe neonatal hypotonia, multiple contractures, polyhydramnios, and fetal hydrops. We report a case of a patient born at a gestational age of 34 weeks and 3 days with fetal hydrops, joint contractures, and akinesia. Muscle biopsy results were highly indicative of GSD. This is the first case of suspected GSD in Korea presenting as fetal hydrops. The possibility of other disorders associated with glycogen metabolism should be considered in fatal fetal hydrops patients with severe hypotonia and arthrogryposis, and aggressive investigations such as muscle biopsy should be performed for early diagnosis.
류마토이드 관절염 환자에서 저용량 methotrexate 투여후 유발된 폐독성 1 예
류재춘(Jae Choon Ryu),김대현(Dae Hyun Kim),오세익(Se Ick Oh),박상현(Sang Hyun Park),이윤우(Yun Woo Lee),김동순(Dong Soon Kim),전우기(Woo Gi Jeon),서연림(Yeon Lim Seo) 대한내과학회 1994 대한내과학회지 Vol.46 No.6
Low dose Methtrexate has been known as an effective therapy Rheumatoid Arthritis without sereous side effect. But recently there are reports of interstitial pneumonitis due to low dose Methotrexate therapy and we experienced a case of fatal pneumonitis induceded by low dose Methotrexate for Rheumatoid Arthritis. Patient was a 70 year-old man, who developed rapidly progressing dyspnea after the administration of 107 5 mg of Methotrexate in 17 weeks. In spite of discontinuation of Methotrexate and high dose steroid therapy, patient expired and necropsy of the lung revealed severe interstitial fibrosis and diffuse alveolar damage.
고재현 ( Jae Hyun Koh ),홍석주 ( Suk Joo Hong ),안홍준 ( Hong Joon Ahn ),안중경 ( Joong Kyung Ahn ),전찬홍 ( Chan Hong Jeon ),차훈석 ( Hoon Suk Cha ),안중모 ( Joong Mo Ahn ),김현숙 ( Hyun Sook Kim ),서연림 ( Yeon Lim Seo ),고은미 대한류마티스학회 2002 대한류마티스학회지 Vol.9 No.3
Objective: The purpose of the study is to describe the magnetic resonance imaging (MRI) findings and to investigate useful sequences of MRI in inflammatory myopathies. A third goal is to correlate MRI findings with the grade of histopathologic severity. Methods: Sixteen patients (13 women, 3 men), aged 21~74 years (median age of 49) with inflammatory myositis (examined with both MRI and muscle biopsy) were studied. Ten patients were diagnosed with polymyositis and 6 with dermatomyositis. Conventional T1-weighted (SE 366/12) and T2-weighted (SE 4766/90) fast spin-echo and fat-suppressed T1-weighted MR images with contrast enhancement (FSAT T1 CE) were obtained. Ratios between the signal intensities of a muscle and the signal intensities of subcutaneous fat in the same tomographic sections were calculated to objectively represent the degree of signal intensities. Semi-quantitative grading of severities in muscle biopsy specimen was examined based on invasion of inflammatory cells and necrosis, degeneration and regeneration of muscle fiber by a neuromuscular pathologist. Results: FSAT T1 CE could objectively describe the severity of involvement in inflammatory myopathies. The quadriceps muscle group, especially the vastus muscle tended to be most severely and frequently involved in inflammatory myositis with FSAT T1 CE (statistically insignificant). The vastus intermedius muscle was more severely involved in dermatomyositis than polymyositis. The signal intensity of abnormal muscle sampled by biopsy correlated positively with the grade of muscle biopsy. Conclusion: MRI shows promise in identifying pathologic muscle in patients suspected of having one of the inflammatory myopathies. The degree of signal intensity on MRI may reflect the severity of grade in muscle biopsy.