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증례 / 본드 및 휘발성 용제의 습관적 흡입 후에 발생한 재생불량성 빈혈 1예
권덕호(Deog Ho Kwon),정상용(Sang Yong Jung),김진휘(Jin Hee Kim),정종익(Jong Ik Jung),신동우(Dong Woo Shin),천정현(Jung Hyun Chun),신재욱(Jae Wook Shin),권정아(Jung Ah Kwon),송태의(Tae Eui Song) 대한내과학회 1999 대한내과학회지 Vol.57 No.1
The inhalation of volatile substances has becoming a popular fad among adolescents in the world. Glue sniffing is associated with injury of nervous system, liver and kidney. And rarely abnormality of blood and bone marrow suppression can develop. The main components of volatile substances that cause hematologic abnormality is thought to be benzene, toluene, and xylene. A 24 year-old male was admitted to our hospital due to gum bleeding. He was a chronic glue and organic solvents sniffer for 6 years, and quit sniffing 1 year before admission. He had no specific drug history. On admission, CBC was as follows: WBC 2,500/mm3; hemoglobin 8.9g/dl; hematocrit 25.1%; platelet 2,000/mm3. Bone marrow biopsy showed severe hypocellular marrow compatible with aplastic anemia. We report a case of aplastic anemia after habitual sniffing of glue and volatile substances with brief review of the literature.
투석이 필요했던 중증 급성 신손상 환자에서 신장기능의 예후
최경아 ( Kyung A Choi ),권정아 ( Jeong Ah Kwon ),김영훈 ( Young Hoon Kim ),이유지 ( Yu Ji Lee ),오하영 ( Ha Young Oh ),김대중 ( Dae Joong Kim ),김윤구 ( Yoon Goo Kim ),허우성 ( Woo Seong Huh ),이정은 ( Jung Eun Lee ) 대한신장학회 2009 Kidney Research and Clinical Practice Vol.28 No.4
Purpose: Acute tubular necrosis (ATN) is a serious complication in critically ill patients. This study investigated the renal outcome of severe ATN requiring RRT and prognostic factors for renal recovery. Methods: Between January 2000 and May 2008, surviving patients with presumed ATN requiring dialysis were analyzed retrospectively. Patients with pre-existing chronic kidney disease and other causes of ARF rather than ATN were excluded. Primary outcomes were complete renal recovery (CR) and dialysis withdrawal. CR was defined as a return to basal serum creatinine level or creatinine <1.5 mg/dL (male) or <1.3 mg/dL (female) without dialysis. Results: Of one hundred twenty two patients, 79 (65%) patients were male. The mean age was 54±16 years and 87 patients (71%) received continuous renal replacement therapy. 55% had ischemic ATN, 29% had septic ATN, and 16% had nephrotoxic ATN. Mean duration of dialysis was 12 (6-29) days. Dialysis withdrawal rate at 30 days and at 60 days after initiation of dialysis were 51% and 77%, respectively. CR at 60 days after initiation was 50%. Multivariate analysis revealed that older age (per year, Hazard ratio (HR)=0.981, 95% Confidence interval (CI) 0.963 to 0.999), ischemic ATN (vs. toxic ATN, HR=0.481, 95% CI 0.238 to 0.974),and longer duration of oliguria (per day, HR=0.979, 95 % CI 0.962 to 0.996) were independent prognostic factors of renal recovery. Conclusion: Young age and short duration of oliguria were favorable factors for renal recovery from ATN requiring dialysis. The cause of ATN might be also an independent prognostic factor.
혈중 Lipoprotein ( a ) 의 농도가 인체내 혈전 생성 및 용해 인자에 미치는 영향에 관한 연구
서홍석(Hong Seog Seo),오동주(Dong Joo Oh),이은미(Eun Mi Lee),한승환(Sung Whan Han),박희남(Hui Nam Pak),임도선(Do Sun Lim),박창규(Chang Kyu Park),김영훈(Young Hoon Kim),심완주(Wan Joo Shim),노영무(Young Moo Ro),권정아(Jung Ah Kwon),이갑 대한내과학회 1996 대한내과학회지 Vol.51 No.1
Objectives: Recently, lipoprotein (a) is known as an independent genetic risk factor for cardiovascular disease. Lipoprotein (a) contains a unique structure, apolipoprotein(a), that shares a partial homology with plasminogen without haboring enzymatic activity. Several in vitro studies reported that lipoprotein(a) competes with plgsminogen for their receptors showing inhibited thrombolysis and promoted thrombosis. We investigated whether evalvuated that lipoprotein(a) has same properties in vivo by determining the homeostatic relation between lipoprotein(a) concentration and several parameters of thrombosis and thrombolysis, and whether parameters of thrombosis and thrombolysis are different in atherosclerotic vascular diseases. Methods: Lipoprotein(a), fibrinogen, plasminogen, FDP-d, antithrombin-III, prothrombin time, activated partial thromboplastin time, tissue-type plasminogen activator, alpha-2 antiplasmin, plaminogen activator inhibitor-l, platelet counts, and other lipid profiles were measured and were compared each others by venous samles in 239 cases with atherosclerotic vascular disease which consisted of 146 cases of coronary heart disease, 39 cases of non-hemorrhagic cerebral infarction, and 10 cases of arteriosclerosis obliterans and in 185 cases without atherosclerotic vascular disease., Results: There was neither significant homeostatic relationship between lipoprotein(a) levels and paramets d thrombolysis, nor between lipids levels and parameters of thrombosis and thrombolysis. Serum lipoprotein(a) levels were higher in patients with myocardial infarction than in those with non- atherosclerotic vascular disease(30.0±28.2mg vs 23.8±21.4mg/dl). Among the thrombogenic and thrombolytic parameters, only tPA and FDP-d were significantly elevated in patients with atherosclerotic vascular disease. Conclusion: The findings that lipoprotien(a) was not correlated with thrombogenic and thrombolytic profiles in vivo suggests that lipoprotein(a) is not related to thrombogenicity in Korean people, al- though lipoprotein(a) is a independent genetic risk factor for carodiovascular disease.
정성주,김성범,박대원,정혜원,기세윤,권정아,박만석,박미연,정희진,김우주 대한감염학회 2004 감염과 화학요법 Vol.36 No.3
브루셀라증은 전 세계적으로 발생하는 인수공통 전염병중에 하나로서, 본 증례는 국내에서 감염된 가축에 대한 노출력이 없는 집단에서 현증 브루셀라증이 발생한 첫 증례이기에 문헌 고찰과 함께 보고한다. 또한 환자가 근무하였던 축산물 부산물 시장에서 역학 조사를 실시하여, 현증환자 및 기감염자를 발견하여 축산물 부산물 시장 근무자에서 현증 브루셀라증이 발생할 위험성을 평가하였다. 역학 조사 결과 축산물 부산물을 다루는 일을 하는 사람들에서 감염된 가축과의 직접 접촉이 없이도 브루셀라증이 발생할 수 있음을 알 수 있었다. Brucellosis is a world-wide zoonotic disease. We report the first case of brucellosis in South Korea that is not related to direct contract with intected cattles. The patient had been working in the market of by-product, stock raising for twenty years and complained of 1-month history of fever, chill, and intermittent epistaxis. We confirmed brucellosis by anti-brucella antibody test and PCR. After 6 weeks' treatment with rifampicin and doxycycline, fever and chilling subsided, and, generalized weakness and oral intake improved. We performed seroepidemiology study against workers who were working in the same market as the patient. However, we couldn't find out other cases with seropositivity. We concluded that although the workers of by-product market have a risk of getting brucellosis, the risk is low.