외이부에 발생한 유피낭종 3예

부성현,홍지원 대한이비인후과학회 2009 대한이비인후과학회지 두경부외과학 Vol.52 No.5

Dermoid cysts, also referred as “dysontogenetic cyst”, are ectodermal cysts that contain epithelial linings as well as adnexal structures. They are divided into 3 categories : epidermoids, dermoids and teratoids. Although dermoid cysts represent a separate entity, the term “dermoid” is generally used to indicate all 3 categories. Dermoid cysts may occur in numerous areas of the body. However, dermoid cysts on the head and neck region are relatively rare. A few cases of dermoid cysts have been reported especially in the auriculotemporal area but not in the external auditory canal or preauricular area. We experienced 3 unusual cases of dermoid cysts occurring in the auriculotemporal area that includes external auditory canal, preauricular and postauricular area. Because of its location and rarity, we report these cases of dermoid cyst in the auriculotemporal area with a brief review of literatures.

비전정에 발생한 신경초종 1예

부성현,홍지원,허민정 대한비과학회 2008 Journal of rhinology Vol.15 No.2

A schwannoma, also known as neurilemmoma, is a relatively rare benign tumor originating from the schwann cells of the nerve sheath. It occurs along any somatic, sympathetic and cranial nerves except the olfactory and optic nerves. It occurred most frequently in the head and neck but rarely in the nasal cavity and paranasal sinuses. Occurrence was especially rare in the nasal vestibule. Recently we experienced an unusual case of the schwannoma involving the left nasal vestibule. The mass was completely removed via a sublabial approach and histopathological examination and immunohistochemical staining study confirmed the schwannoma. We report this case with review of literatures. A schwannoma, also known as neurilemmoma, is a relatively rare benign tumor originating from the schwann cells of the nerve sheath. It occurs along any somatic, sympathetic and cranial nerves except the olfactory and optic nerves. It occurred most frequently in the head and neck but rarely in the nasal cavity and paranasal sinuses. Occurrence was especially rare in the nasal vestibule. Recently we experienced an unusual case of the schwannoma involving the left nasal vestibule. The mass was completely removed via a sublabial approach and histopathological examination and immunohistochemical staining study confirmed the schwannoma. We report this case with review of literatures.

Repair of Spontaneous Cerebrospinal Fluid Otorrhea from Defect of Middle Cranial Fossa

부성현 대한청각학회 2013 Journal of Audiology & Otology Vol.17 No.3

Spontaneous cerebrospinal fluid (CSF) otorrhea is defined as CSF otorrhea where there are no identifiable causes including previous trauma, surgery, infection, neoplasm or congenital anomaly. The condition is rare. The origin of CSF leak is commonly a defect in the tegmen of the middle cranial fossa. The pathophysiology of spontaneous CSF otorrhea is unclear. Two theories of the etiology of bony defects of the temporal bone are the congenital bony defect theory and arachnoid granulation theory. The authors experienced a case of a 49-year-old female patient admitted with the complaint of persistent right ear fullness. Computed tomography revealed a large defect of the middle fossa and suspicious CSF otorrhea through the defect of tegmen tympani. Repair was successful with multiple bone chips using the transmastoid approach. The postoperative course was good and there has been no recurrence of the CSF leakage.

A Novel Frameshift Mutation of the USH2A Gene in a Korean Patient with Usher Syndrome Type II

부성현,송민정,김희진,조양선,추호석,고문희,정원호,김종원,홍성화 대한이비인후과학회 2013 Clinical and Experimental Otorhinolaryngology Vol.6 No.1

Usher syndrome type II (USH2) is the most common form of Usher syndrome, characterized by moderate to severe hearing impairment and progressive visual loss due to retinitis pigmentosa. It has been shown that mutations in the USH2A gene are responsible for USH2. The authors herein describe a 34-year-old Korean woman with the typical clinical manifestation of USH2; she had bilateral hearing disturbance and progressive visual deterioration, without vestibular dysfunction. Molecular genetic study of the USH2A gene revealed a novel frameshift mutation (c.2310delA; Glu771LysfsX17). She was heterozygous for this mutation, and no other mutation was found in USH2A, suggesting the possibility of an intronic or large genomic rearrangement mutation. To the best of our knowledge, this is the first report of a genetically confirmed case of USH2 in Korea. More investigations are needed to delineate genotype-phenotype correlations and ethnicity-specific genetic background of Usher syndrome.

제2형 Usher 증후군 1예

부성현,박동진,한치성 대한이비인후과학회 2008 대한이비인후과학회지 두경부외과학 Vol.51 No.9

The Usher syndrome is an autosomal recessive disorder that cause bilateral sensorineural hearing loss and progressive loss of vision. It is genetically heterogeneous and is the most frequent cause of hereditary deafness and blindness in human. There are three types of Usher syndrome that can be distinguished clinically and into different subtypes. Type 2 Usher syndrome is the most common form and less severe than Type 1. It is characterized by congenital, moderate to severe, high frequency sloping hearing loss, retinitis pigmentosa which is typically diagnosed in late adolescence, and normal vestibular function. Recently, we have experienced a case of clinically diagnosed Type 2 Usher syndrome in a 34 years old female. We report this case with a brief review of literature. This is the first Type 2 Usher Syndrome to be reported in the otolaryngologic field in Korea. (Korean J Otorhinolaryngol-Head Neck Surg 2008;51:833-7)

응급의료센터에 내원한 측두골 골절의 임상분석

부성현,김택희 대한이비인후과학회 부산,울산,경남 지부회 2010 임상이비인후과 Vol.21 No.1

Background and Objectives:Head injuries are commonly seen in emergency medical center, but within this group only a small number of patients will have a temporal bone fracture. The aim of this study is to evaluate the clinical findings of temporal bone fractures and to compare the efficacy between traditional and petrous based fracture classification system. Materials and Methods:We reviewed charts and computed tomography scans representing 108 temporal bone fractures at regional emergency medical center. Hearing evaluation was performed in 57 cases. Results:The temporal bone fractures were predominantly occurred in 5 decades (24.8%). The most common symptom was ear bleeding which occurred 75 cases, vertigo in 20cases, TM perforation in 19 cases, tinnitus in 17 cases, facial palsy in 16 cases, and CSF leakage in 3 cases. Sensorineural hearing loss did not correlate with transverse fracture but was significantly more prevalent in petrous fractures. Also, vertigo and pneumolabyrinth were significantly occurred in petrous fracture. Conclusion:The incidence of the elderly was regional feature. Petrous based classification was significantly correlated with the occurrence of main symptoms of temporal bone fractures.

골결손을 동반한 고위 경정맥구 박동성 이명의 수술적 치료 1예

고영범,부성현 대한이비인후과학회 부산,울산,경남 지부회 2014 임상이비인후과 Vol.25 No.1

A high jugular bulb is usually asymptomatic and incidentally found during otologic examination. But high jugular bulb dehiscence may cause vascular pulsatile tinnitus. It is thought to be one of the treatable cause of venous pulsatile tinnitus, but there were previous 2 case reports of surgical treatment for pulsatile tinnitus due to high jugular bulb dehiscence in Korean literature. The authors present a case of pulsatile tinnitus owing to dehiscent high jugular bulb which has been successfully treated by surgical reconstruction. We used conchal cartilage piece as a reconstruction material. The procedure was simple and easy to introduce and worth for it.

양성 경부 낭종에서의 Picibanil(OK-432)을 이용한 경화치료 효과

홍지원,부성현,박재홍,김명구,Hong, Ji-Won,Boo, Sung-Hyun,Park, Jae-Hong,Kim, Myung-Gu 대한기관식도과학회 2008 大韓氣管食道科學會誌 Vol.14 No.2

Background and Objectives: In most cases of benign neck cysts, surgical excision has been considered as treatment of choice. However, sometimes complete excision is very difficult, and recurrences has been occured due to insufficient surgery frequently. In this point of view, non-surgical treatment has been attempted with sclerosing agents such as picibanil(OK-432). In this study, we evaluated the efficacy of picibanil sclerotherapy for benign neck cysts. Materials and methods: We retrospectively reviewed 53 patients(27 males, 26 females) who had undergone sclerotherapy with picibanil for benign neck cysts such as ranula, lymphangioma, thyroglossal duct cyst and branchial cyst. Information was gathered with respected to age, sex, number of injections, side effect and outcome of treatment. All patients were treated with intralesional aspiration of cystic contents and injection of picibanil, and followed on neck ultrasonography or neck CT. Results: 53 patients received sonoguided sclerotherapy using picibanil(OK-432). 31 patients(41.3%) showed total shrinkage, near total shrinkage(more than 90% of volume) in 7 patients(9.3%), marked shrinkage(more than 70%) in 5 patients(6.6%) and partial shrinkage(less than 70%) in 17 patients. 15 patients(20%) reaveled no response and 8 patients showed recurrences with repeated sclerotherapy. The side effects of therapy were observed by symptoms such as fever, localized pain and odynophagia. However, these complications disappeared after several days in all cases. Conclusions: We recognized that picibanil(OK-432) sclerotherapy for benign neck cyst is a safe and effective procedures as a primary treatment before considering surgery.

9개월된 영아에서 발생한 급성 융합성유양동염과 동반된 Bezold 농양 1예

백영진,부성현 대한이비인후과학회 부산,울산,경남 지부회 2014 임상이비인후과 Vol.25 No.2

Complications of acute otitis media are greatly decreased since the introduction of antibiotics. However, inap-propriate antibiotic therapy leads to complications of acute otitis media in children associated with significantmorbidity. Among the complication of acute otitis media, Bezold’s abscess is an abscess in the sternocleidomas-toid muscle where pus from a mastoiditis escapes into the sternocleidomastoid. It is a rare complication of acuteotitis media in these days. The authors report a case of Bezold’s abscess with acute coalescent mastoiditis occur-ring in 9-month-old infant with review of literatures. To our knowledge, this is the youngest case report ofBezold’s abscess in Korea.

Comparison of right versus left radial access for coronary artery catheterization

이경환,부성현,임성민,김찬준 대한내과학회 2021 대한내과학회 추계학술대회 Vol.2021 No.1