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조영미(Yong Mee Cho),김규래(Kyu Rae Kim),노재윤(Jae Y Ro),장세진(Se J Jang),김상윤(Sang Yoon Kim),조경자(Kyung Ja Cho) 대한두경부종양학회 2004 대한두경부 종양학회지 Vol.20 No.2
Basaloid squamous carcinoma (BSC) is an uncommon aggressive variant of squamous cell carcinoma with a predilection for hypopharynx, tongue base, and larynx. We present 5 cases of BSC of unusual sites, each from maxillary sinus, external auditory canal, submandibular gland, tonsil, and nasopharynx. Only a few cases arising in these sites have been reported to date. Patients included 3 men and 2 women with the age range of 45-69 years (mean, 56.4 years). Microscopically, the tumors were characterized by solid lobules and nests of ovoid basaloid cells with abundant desmoplastic stroma. Comedonecrosis, peripheral palisading of tumor cells, trabecular pattern, and rosette-like arrangement were commonly observed. Tumor cells had scanty cytoplasm and their nuclei were ovoid, relatively uniform, and hyperchromatic. In two cases, concomitant squamous cell carcinoma in situ was identified. Immunohistochemical stains revealed that tumor cells were strongly positive for pancytokeratin and negative or weakly positive for p63. Being aware of BSC that can arise from unusual sites would help diagnose correctly and treat properly this rare and distinct clinicopathologic entity.
세포 병리 자문 재판독의 진단 불일치에 관한 연구: 서울아산병원의 경험
박소형,노재윤,조경자,공경엽,조영미,강신광,Park, So-Hyung,Ro, Jae-Y.,Cho, Kyung-Ja,Gong, Gyung-Yub,Cho, Yong-Mee,Khang, Shin-Kwang 대한세포병리학회 2008 대한세포병리학회지 Vol.19 No.2
Background : Second opinion diagnosis of outside pathology slides is a common practice for efficient and proper patient management. We analyzed cytology slides from outside hospitals submitted for a second opinion diagnosis to determine whether the second opinion diagnosis had any influence on patient care. Methods : We reviewed 1,153 outside cytology slides referred to Asan Medical Center for second opinions from January, 2007, to December, 2007. All cases were categorized into three groups; no diagnostic discrepancy, minor diagnostic discrepancies (no impact on the management), and major diagnostic discrepancies (significant impact on the management and subsequent follow-up). Results : The thyroid was the most common organ system (933 cases, 80.9%), Forty cases (3.6%) belonged to the major diagnostic discrepancy group and 149 cases (12.8%) to the minor discrepancy group. For validation of second opinion diagnoses in major discrepancy cases, subsequent biopsy or surgical resection specimens and clinical information were reviewed, which were available in 29 cases. The second opinion diagnoses resulted in alteration of clinical management in 21 of 29 cases. Conclusion : For all referred patients, second opinion diagnosis is important and mandatory for appropriate patient care.
진성다혈구증에 병발한 미세변화신증을 동반한 IgA 신병증
정영종 ( Young Jong Jung ),김범 ( Beom Kim ),조영미 ( Yong Mee Cho ),김희섭 ( Hee Sup Kim ),김지호 ( Ji Ho Kim ),김수연 ( Soo Yeun Kim ),김봉석 ( Bong Seog Kim ),최윤미 ( Youn Mi Choi ),문경협 ( Kyoung Hyoub Moon ) 대한신장학회 2008 Kidney Research and Clinical Practice Vol.27 No.6
Polycythemia vera is a hematopoietic stem cell disease, characterized by sustained and excessive proliferation of erythrocytic, granurocytic and megakaryocytic cells in the bone marrow resulting in pancytosis in peripheral blood. There have been a few reports of glomerulonephritis with polycythemia vera, most of which were IgA nephropathy. We report a case of a polycythemia vera associated with proteinuria. We confirmed the polycythemia vera according to World Health Organization criteria. Renal pathology showed IgA nephropathy and minimal change disease. Periodic phlebotomy was done and hydroxyurea was administered without specific managements for renal disease. After 3-month treatment, hemoglobin level decreased and proteinurea disappeared.
만성 항체 매개성 거부 반응에서 경정맥 면역 글로불린으로 치료한 1예
변승운 ( Seung Woon Byun ),여영선 ( Young Sun Yeo ),박정식 ( Jung Sik Park ),조영미 ( Yong Mee Cho ),박수길 ( Su Kil Park ) 대한신장학회 2009 Kidney Research and Clinical Practice Vol.28 No.4
A 66-year-old male was admitted for increasing azotemia. He was diagnosed with chronic antibody-mediated rejection and had received a livingdonor renal transplant from his 32-year-old son prior to his admission. The peritubular capillaries of his kidney were diffusely positive on C4d immunostaining. It is known that there is an agreement between C4d staining and serological and histopathological data during rejection that is thought to have a humoral component. The role of alloantibodies in chronic renal allograft deterioration and the corresponding morphologic changes have been increasingly recognized during the recent years. However the treatment guidelines for chronic antibody-mediated rejection have not yet been established. Intravenous immunoglobulin (IVIG) has been shown to decrease the titers of anti-HLA antibodies in highly sensitized patients awaiting transplant. There are also numerous proposed mechanisms regarding how IVIG exerts its immunomodulatory action. As we have experienced chronic antibody-mediated rejection and how IVIG treatment improves renal function, we recognize that IVIG has the potential to be used for treating certain subgroups of chronic allograft nephropathy patients with positive C4d staining and anti-HLA antibodies.
Se Young Choi(최세영),Ho Heon Kim(김호헌),Bumjin Lim(임범진),Jong Won Lee(이종원),Young Seok Kim(김영석),Jeong Kon Kim(김정곤),Jae Lyun Lee(이재련),Yong Mee Cho(조영미),Dalsan You(유달산),In Gab Jeong(정인갑),Cheryn Song(송채린),Jun 대한비뇨기종양학회 2021 대한비뇨기종양학회지 Vol.19 No.4
Purpose: To construct a urologic cancer database using a standardized, reproducible method, and to assess preliminary characteristics of this cohort. Materials and Methods: Patients with prostate, bladder, and kidney cancers who were enrolled with diagnostic codes in the electronic medical record (EMR) at Asan Medical Center from 2007–2016 were included. Research Electronic Data Capture (REDCap) was used to design the Asan Medical Center-Urologic Cancer Database (AMC-UCD). The process included developing a data dictionary, applying branching logic, mapping clinical data warehouse structures, alpha testing, clinical record summary testing, creating “standards of procedure,” importing data, and entering data. Descriptive statistics were used to identify rates of surgeries and numbers of patients. Results: Clinical variables (n=407) were selected to develop a data dictionary from REDCap. In total, 20,198 urologic cancer patients visited our institution from 2007–2016 (bladder cancer, 4,616; kidney cancer, 5,750; prostate cancer, 10,330). The overall numbers of patients and surgeries increased over time, with robotic surgeries rapidly growing over a decade. The most common treatment for urologic cancer was surgery, followed by chemotherapy and radiation therapy. Conclusions: Using a standardized method, the AMC-UCD fosters multidisciplinary research. This constructed database provides access to clinical statistics to effectively assist research. Preliminary data should be refined through EMR chart review. The successful organization of data from 2007–2016 provides a framework for future periods of investigation and prospective models.
증례 : 신장 ; 피부병변과 고칼슘혈증, 신부전으로 발현한 유육종증 1예
민보영 ( Bo Young Min ),박원형 ( Won Hyeong Park ),송대근 ( Dae Geun Song ),김태균 ( Tae Gyun Kim ),박현경 ( Hyun Gyung Park ),김범 ( Beom Kim ),조영미 ( Yong Mee Cho ) 대한내과학회 2009 대한내과학회지 Vol.77 No.5S
본 증례는 유육종증이 피부와 신장을 동시에 침범하여, 특히 신장에서는 육아종성 간질성 신염에 의한 신부전까지 일으켰으나 고용량의 스테로이드에 좋은 치료 반응을 보인 예로써 신기능 저하와 고칼슘혈증이 동반된 환자에서 신장 유육종증은 주요 감별진단에 포함되어야 하겠다. Sarcoidosis is a granulomatous inflammatory disorder of unknown etiology. It can involve any organ and present in various clinical forms, but renal involvement is very unusual. We report on a 68-year-old man with renal sarcoidosis. He presented with unexplained renal impairment, hypercalcemia, and multiple light brown papules on the buttock and lower extremities. Non-caseating granulomas and interstitial nephritis were revealed in skin and kidney biopsies. The serum creatinine, hypercalcemia, and skin lesions rapidly improved on high-dose steroid therapy. One year later, the serum calcium level was normal, and serum creatinine was 1.3 mg/dL. (Korean J Med 77:S1226-S1230, 2009)
서지영 ( Ji Young Seo ),김광실 ( Gwang Sil Kim ),김대명 ( Dae Myung Kim ),김선영 ( Sun Young Kim ),유경돈 ( Kyung Don Yoo ),홍진희 ( Jin Hee Hong ),주혜원 ( Hye Won Joo ),조영미 ( Yong Mee Cho ),김상현 ( Sang Hyun Kim ),박원도 ( W 대한신장학회 2009 Kidney Research and Clinical Practice Vol.28 No.5
Kidney involvement in systemic lupus erythematosus (SLE) is common. The incidence of venous thrombosis in SLE ranges from 5-15%, and venous thrombosis in lupus nephritis associated with nephritic syndrome or antiphospholipid antibody syndrome is reported in 30-35%. Lupus nephritis with nephrotic syndrome is not infrequently encountered at the point of diagnosis of SLE, but venous thrombosis as the first manifestation of SLE is rare. Herein we present our clinical experience with a case of multiple venous thrombosis with nephrotic-range proteinuria as the first manifestation of lupus nephritis.
서재원 ( Jae Won Seo ),임병훈 ( Byung Hoon Lim ),이현정 ( Hyun Jeong Lee ),강은미 ( Eun Mi Kang ),이병욱 ( Byung Uk Lee ),김범 ( Beom Kim ),조영미 ( Yong Mee Cho ) 대한내과학회 2011 대한내과학회지 Vol.80 No.4
Thin basement membrane disease is defined as diffuse thinning of the glomerular basement membrane, and is clinically characterized by persistent hematuria, minimal proteinuria, normal renal function, and a benign course. It can occur together with other glomerular diseases. We experienced a case of thin basement membrane disease concurrent with minimal-change disease. Treatment with corticosteroid resulted in improved proteinuria and peripheral edema during the follow-up period. (Korean J Med 2011;80:469-472)