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이경석,윤석만,권희,이호,김혜경,조미자,한규남,김명성 순천향의학연구소 2003 Journal of Soonchunhyang Medical Science Vol.9 No.1
Background: Recently the health insurance review agency tried to cut off the cost of unnecessary hospital stay. It is important to reduce the prolonged occupation of the hospital beds. However, there are some obstacles of the management for the prolonged bed occupation. We report our experiences and the problems of bed-control. Methods: To increase the rate of effective bed-usage, a task force was made. This team was consisted of 4 dctors, 2 nurses and 2 personnel of the administrative department. From December 20th 2001 to May 17th 2002, the task force analysed the rate, number and causes of the prolonged (more than 60 days, regardless of the disease entities) bed occupation. We announced and explained the necessity of bed-control and actively pressed to reduce the prolonged bed occupation. Results: The number of the prolonged bed occupation was 71 at the beginning of the management. It was reduced to 46 at best, then turned back to 65 at the end. It seems to be impossible to reduce the prolonged bed occupation until there are sufficient numbers of long-term care facilities. Aggressive bed control makes the sick patients to move every two or three months, it is never desirable. Conclusion: We cannot expect any Quality Improvements without improvement of the wrong system. Prior to the management for the prolonged bed occupation, it is necessary to build a sufficient number of long-term care facilities.
발달 장애 아동에게 시행된 주간 치료실 프로그램의 치료 결과에 대한 고찰
곽영숙,강경미,이혜숙 대한소아청소년정신의학회 2000 소아청소년정신의학 Vol.11 No.1
연구목적 : 본 연구는 발달 장애 아동들에 행해진 주간 발달 증진 프로그램의 효과 및 치료 결과에 대하여 고찰하고자 하였다. 방법 : 발달 장애 아동들의 애착 형성을 향상시키고 부모-아동의 상호작용 증진을 통한 발달 촉진을 목적으로 국립서울정신병원 주간 치료실에서 1996년 이후 1년 단위로 3년간 시행된 치료 프로그램에 참석한 2세에서 7세의 발달 장애 아동(전반적 발달 장애-31명, 기타 발달 장애-18명) 49명을 대상으로 하였다. 정신과 전문의 2인 이상에 의하여 진단되었고 추적 진료 동안의 언어 치료사, 작업 치료사, 사회 사업가의 평가와 관찰, 간호사 관찰 및 보호자로부터의 정보를 통하여 진단적 신뢰도를 높였다. 이들에서 프로그램 참여 기간 동안의 교육 진단 검사(PEP), 아동기 자폐증 평정척도(CARS), 그리고 사회 성숙도 검사(SMS)상의 변화를 추적 조사하였고, 프로그램 참여시의 진단, 신체 연령 및 발달 연령, 동반 질환 등에 따라 분류하여 치료 효과를 비교하였다. 결과 : 프로그램에 참여한 아동들은 PEP 종합 점수와 SMS사회지수에서 통계적으로 유의한 진전을 보였다. 치료 시작시 발달 연령, 동반 잘환, 그리고 CARS점수의 증증도에 따른 각 집단에서 치료 효과상의 유의한 차이는 없었다. 결론 : 발달 장애 아동들을 위한 주간 치료실에서의 발달 중진 프로그램의 결과는 참여한 아동 모두에게 효과적이었다. 향후 동반 질환의 특성과 발달 연령에 맞는 특수 치료 프로그램 개발이 이루어져야 할 것이다. Objective : This was conduced to evaluate the effect of early intervention to promote the development of children with developmental disorders. Methods : 49 children(31 in PDD group and 18 in DLD group) participated in a one year day treatment program conduced from 1996 to 1999. They were performed PEP, CARS , and SMS. They were grouped by diagnosis, comorbidity, chronological age and CARS score at the beginning of the program and the treatment effect was compared. Results : The children who participated in the day treatment program showed significant increase in their PEP, SMS score, and decrease trend in their CARS score. When children were grouped by diagnosis, comorbidity, chronological age, and severity in CARS score we did not find out significant difference between groups. Conclusion : Our data suggest that the day treatment program which emphasis on development is effective in treating children with developmental disorders. KEY WORDS : Day treatment program · PDD.
Intravenous fluid prescription practices among pediatric residents in Korea
Lee, Jiwon M.,Jung, Younghwa,Lee, Se Eun,Lee, Jun Ho,Kim, Kee Hyuck,Koo, Ja Wook,Park, Young Seo,Cheong, Hae Il,Ha, Il-Soo,Choi, Yong,Kang, Hee Gyung The Korean Pediatric Society 2013 Clinical and Experimental Pediatrics (CEP) Vol.56 No.7
Purpose: Recent studies have established the association between hypotonic fluids administration and hospital-acquired hyponatremia in children, and have contended that hypotonic fluids be removed from routine practice. To assess current intravenous fluid prescription practices among Korean pediatric residents and to call for updated clinical practice education Methods: A survey-based analysis was carried out. Pediatric residents at six university hospitals in Korea completed a survey consisting of four questions. Each question supposed a unique scenario in which the respondents were to prescribe either a hypotonic or an isotonic fluid for the patient. Results: Ninety-one responses were collected and analyzed. In three of the four scenarios, a significant majority prescribed the hypotonic fluids (98.9%, 85.7%, and 69.2%, respectively). Notably, 69.2% of the respondents selected the hypotonic fluids for postoperative management. Almost all (96.7%) selected the isotonic fluids for hydration therapy. Conclusion: In the given scenarios, the majority of Korean pediatric residents would prescribe a hypotonic fluid, except for initial hydration. The current state of pediatric fluid management, notably, heightens the risk of hospital-acquired hyponatremia. Updated clinical practice education on intravenous fluid prescription, therefore, is urgently required.
Genetic basis of Bartter syndrome in Korea.
Lee, Beom Hee,Cho, Hee Yeon,Lee, HyunKyung,Han, Kyoung Hee,Kang, Hee Gyung,Ha, Il Soo,Lee, Joo Hoon,Park, Young Seo,Shin, Jae Il,Lee, Dae-Yeol,Kim, Su-Yung,Choi, Yong,Cheong, Hae Il Springer International ; Oxford University Press 2012 Nephrology, dialysis, transplantation Vol.27 No.4
<P>Bartter syndrome (BS) is clinically classified into antenatal or neonatal BS (aBS) and classic BS (cBS) as well as five subtypes based on the underlying mutant gene; SLC12A1 (BS I), KCNJ1 (BS II), CLCNKB (BS III), BSND (BS IV) and CASR (BS V).</P>
Lee, Beom Hee,Kwak, Soo Heon,Shin, Jae Il,Lee, So Hee,Choi, Hyun Jin,Kang, Hee Gyung,Ha, Il Soo,Lee, Jae Seung,Dragon-Durey, Marie-Agnè,s,Choi, Yong,Cheong, Hae Il Springer Science and Business Media LLC 2009 Pediatric research Vol.66 No.3
<P>Although genetic defect of complement factor H (CFH) is a common cause of atypical hemolytic uremic syndrome (aHUS), development of autoantibodies to CFH (CFH-Ab) is also known to be an acquired cause of aHUS. Recently, a correlation between the development of CFH-Ab and the deficiency of the CFH-related proteins, CFHR1 and CFHR3, was identified. In this study, plasma complement profiles were measured and genetic analysis of the CFH, CFI, MCP, CFHR1, and CFHR3 genes were performed in three female patients diagnosed with aHUS with positive CFH-Ab. Acute stage plasmas of all the three patients revealed low C3, low or low-normal CFH antigenic levels, and high titers of CFH-Ab. All the patients also showed complete plasma CFHR1 deficiency and homozygous genomic deletion of CFHR1/CFHR3, but none had CFH, CFI, or MCP mutations. All the patients were treated with plasmapheresis, and two patients required additional immunosuppressive therapy. These patients had a novel subgroup of aHUS characterized by a combination of genetic (a homozygous deletion of CFHR1/CFHR3) and acquired (development of CFH-Ab) factors. Patients with this disease may need intensive immunosuppressive therapy in addition to plasmapheresis. Screening for CFH-Ab and the CFHR1/CFHR3 deficiency should be included in the diagnostic tests for patients with aHUS.</P>
Lee, Jiwon M,Ahn, Yo Han,Kang, Hee Gyung,Ha, I I Soo,Lee, Kyoungbun,Moon, Kyung Chul,Lee, Joo Hoon,Park, Young Seo,Cho, Yong Mee,Bae, Jun-Seok,Kim, Nayoung K D,Park, Woong-Yang,Cheong, Hae Ii Springer International 2015 Pediatric nephrology Vol.30 No.9
<P>Nephronophthisis 13 (NPHP 13) is associated with mutations in the WDR19 gene, which encodes for a protein in the intraflagellar transport complex. Herein, we describe six additional cases accompanied by Caroli syndrome or disease.</P>
정해빈 ( Hae Bin Jeong ),강현희 ( Hyeon Hui Kang ),임은주 ( Eun Joo Im ),김현경 ( Hyun Gyung Kim ),이수연 ( Su Yeon Lee ),맹일호 ( Il Ho Maeng ),이지명 ( Ji Myoung Lee ),장은희 ( Eun Hee Jang ),이상학 ( Sang Haak Lee ),문화식 ( Hw 대한결핵 및 호흡기학회 2008 Tuberculosis and Respiratory Diseases Vol.65 No.3
Rectus sheath hematoma (RSH) is a rare condition that`s caused by a sudden disruption of the deep epigastric vessels or direct damage to the rectus abdominis muscle. This condition is associated with old age, childbirth, abdominal surgery, severe cough, severe sneezing, anticoagulation therapy and/or coagulation disorders. RSH is characterized by abdominal pain and an abdominal mass, so that this is often misdiagnosed as a surgical condition such as appendicitis, intraabdominal abscess, torsion of the ovary and ruptured abdominal aortic aneurysm; this can lead to unnecessary surgery. Thus, we have to be cautious not to miss RSH when a patient with predisposing factors is suffered from abdominal pain and an abdominal mass. We report here on a case of rectus sheath hematoma that was induced by severe cough in a patient who was taking warfarin. (Tuberc Respir Dis 2008;65: 212-215)
연령, 범주전형성 및 회상조건에 따른 아동의 상위기억과 범주적 조직화 책략 사용
이혜련(Hae Lyun Lee),이경님(Gyung Nim Lee) 한국아동학회 1995 아동학회지 Vol.16 No.2
The purpose of the present research was to study developmental trends in categorical organization strategy. The subjects were 160 children-40 nine-year-old boys, 40 nine-year-old girls, 40 seven-year-old boys, 40 seven-year-old girls. All subjects received one of three lists of items differing in category representativeness in either a free-recall or a sort -recall task. The selection of list materials permitted separation of the effects of age differences in category knowledge from those of knowledge per se on children`s recall behavior. The tasks were administered to children individually with the memory task followed by the metamemory task. The data was analyzed with three -way ANOVA arid Pearson`s correlation coefficient. The results were that (1) Children`s recall, clustering, and metamemory increased with age, while age effects for clustering were restricted to the sort-recall/high typicality condition. At each age level, children showed higher level of recall, clustering and metamemory for category typical rather than atypical list, and sort-recall than free-recall. Level of clustering and metamemory were superior in the sort-recall task and for items of high category typicality. (2) 9-year-old children were capable of deliberately and efficiently using category organization as a memory strategy at least when appropriate contextual support was present (as determined by task requirements and list materials: sort-recall/high typicality).