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류마티스 관절염 환자에서 발생된 치골지와 천골의 부전형 피로 골절
정자헌 ( Ja Hun Jung ),전재범 ( Jae Bum Jun ),심승철 ( Seung Cheol Shim ),장대국 ( Dae Kook Chang ),고희관 ( Hee Kwan Koh ),김태환 ( Tae Hwan Kim ),정성수 ( Sung Soo Jung ),이인홍 ( In Hong Lee ),배상철 ( Sang Cheol Bae ),유대현 ( 대한류마티스학회 1998 대한류마티스학회지 Vol.5 No.2
Insufficiency fractures of the sacrum and pubic rami commonly occurs as a results of osteoporosis, usually without a history of trauma, especially in the patients with rheumatoid arthritis. In addition to rheumatoid arthritis and osteoporosis, the other predisposing factors for this condition were renal failure, prolonged corticosteroid therapy, pelvic irradiation, inflammatory diseases, malignancy and mechanical changes after hip surgery. The clinical presentation included progressive inguinal pain, limping, and inability to walk. If a high index of suspicion is not present, subtle findings on radiographs may be missed. Diagnosis of insufficiency fractures is difficult in the early stages. Because initial radiographs are not usually diagnostic, bone scintigraphy and computed tomography were necessary to confirm the diagnosis and detect additional fractures. In most patients, bed rest, non-weight bearing ambulation, symptomatic treatment, and therapy for osteoporosis resulted in rapid improvement, and long-term follow-up of this fractures shows usually benign outcome. So insufficiency fracture of the pelvic bone should be suspected in cases of unexplained inguinal or hip-area pain and inability to walk in the elderly. We present 3 patients with rheumatoid arthritis in our hospital who were found to have insufficiency fractures of sacrum and pubic rami in 2 patients and that of pubic rami on 1 patients with literature review.
전신성 홍반성 루푸스의 진단 실태 및 지연 요인과 예후와의 연관성
정자헌 ( Ja Hun Jung ),심승철 ( Seung Cheol Shim ),장대국 ( Dae Kook Chang ),김태환 ( Tae Hwan Kim ),전재범 ( Jae Bum Jun ),정성수 ( Sung Soo Jung ),유대현 ( Dae Hyun Yoo ),김성윤 ( Seong Yoon Kim ),배상철 ( Sang Cheol Bae ) 대한류마티스학회 2001 대한류마티스학회지 Vol.8 No.3
Objective: This study is aimed to investigate clinical time course in the diagnosis of SLE, clinical features at disease onset, and their effects on organ damage and disease activity Methods: We evaluated 244 patients in the Korean Hanyang Lupus Cohort by medical record review and direct interview: the time at disease onset, clinical diagnosis, and diagnosis meeting ACR criteria for SLE (ACR diagnosis), clinical features at onset, SLICC/ACR damage index, SLAM-R, education, and income. The risk factors of delayed diagnosis and their effect on damage and activity were examined with uni and multivariate analyses. Results: Mean age and disease duration were 33.9 (±11.9) and 6.2 (±4.4) years. The mean time from onset to clinical diagnosis and ACR diagnosis were 2.4 (±3.6) and 2.7 (±3.3) years. The clinical features at disease onset were as follows; arthritis (46.3%), skin rash (13.7%), fever (7.4%), hematologic disorder (7.4%), nephritis (5.7%), Raynaud phenomenon (3.7%), neuropsychiatric syndrome (2.4%). Diagnosis was delayed when oral ulcer, photosensitivity, and arthritis were presented as 1st clinical features compared to when nephritis, malar rash, and fever as 1st clinical features. Delayed diagnosis (based on median time in clinical diagnosis) was not associated with damage, disease activity, education, and income. Conclusions: SLE was diagnosed late over 2 years after first symptoms onset and the time interval from clinical symptoms to ACR diagnosis is about 4 months; the delayed diagnosis and the prognosis in terms of damage and activity might depend on 1st clinical features.
전신성 홍반성 루푸스 환자의 장기 손상에 대한 예비시험적 연구
정자헌 ( Ja Hun Jung ),배상철 ( Sang Cheol Bae ),송용호 ( Yong Ho Song ),김태환 ( Tae Hwan Kim ),전재범 ( Jae Bum Jun ),정성수 ( Sung Soo Jung ),이인홍 ( In Hong Lee ),유대현 ( Dae Hyun Yoo ),김성윤 ( Seong Yoon Kim ) 대한류마티스학회 1998 대한류마티스학회지 Vol.5 No.2
Objectives: The Systemic Lupus International Collaborative Clinics/American College of Rheumatology (SLICC/ACR) Damage Index was created to assess persistent reflection of disease activity in SLE patients. This study was designed to investigate the presence of early organ damage in patients with SLE and to discribe the distribution of SLICC/ACR organ damage index in assessing of morbidity of these patients. Methods: We studied organ damage in 209 SLE patients with disease duration less than 7 years, randomly selected from 1986 through 1995. SLICC organ damage index was measured at first visit by reviewing medical record retrospectivly. The SLICC score for each organ system and the prevalence of damage within organ systems were assessed for the study population. Results: Renal (28%) and musculoskeletal (12.9%) system were the most frequently involved, followed by neurologic (10%) and pulmonary (3%) systems, all with median SLICC system scores of 1. More than half of the patients (51.7%) showed some damage at least one organ. Among 59 patients with renal damage, many of them are less than 40 years old, with disease duration less than 3 years. There was no significant difference in association of SLICC/ACR organ damage index with stratification of age and disease duration in this study. Conclusions: There is an evidence of early organ damage in SLE. And, using the SLICC/ACR damage index, we are expected to evaluate an outcome measure for therapeutic trials and progression of the cumulated organ damage. Above data from this study warranted further evaluation in prospective studies with greater numbers of patients.
정자헌(Ja Hun Jung),손동현(Dong Hyun Sohn),박준용(Joon Yong Park),오광택(Kwang Taek Oh),한동수(Dong Su Han),양석철(Suck Chul Yang),손주현(Ju Hyun Sohn),김순길(Soon Kil Kim),김호중(Ho Jung Kim) 대한내과학회 1996 대한내과학회지 Vol.51 No.4
Objectives: Hyponatremia is the most common finding of electrolyte disorder in patients admitted to medical ward. It is suggested that the prognosis of patients with hyponatremia is worse than that with normal sodium concentration in morbidity and mortality. We performed the study to evaluate the incidence and cause of hyponatremia in inpatients admitted to medical ward via emergency room with prospective study. Methods: Hyponatremia was defined as a serum sodium concentration equal to or less than 134 mEq/L. A total 225 medical patients were prospectively studied for 45 days. Other chemistry and electrolytes of blood and urine were determined within 24 hrs following admission. Results: 1) Of medical inpatients through emergency room, hyponatremia was detected in high frequency (16%) and mild hyponatremia (125-134 mEq/L) was showed in 90% or more. 2) The most common cause of hyponatremia was decreased effective circulating blood volume group (76%), and its common underlying disease was liver disease. 3) Compared to other groups, the group with decreased effective circulatory volume showed significant decrease in spot urine sodium concentration, fractional excretion of uric acid and serum creatinine concentration. 4) There was no correlation between serum concentration of hyponatremia and other parameters associated with it. As it was corrected, no significant simultaneous changes on BUN and serum uric acid concentration was noted. Conclusion: Interpretation of this data depend on not decreased circulatory volume but also other compounding factor as production and excretion of which is related to underlying variable disease.
전신성 홍반성 루푸스 양상으로 발현된 Human Adjuvant Disease
정자헌(Ja Hun Jung),정성수(Sung Soo Jung),문희식(Hee Sig Mun),송용호(Yong Ho Song),조영중(Young Jung Cho),오광택(Kwang Taek Oh),김태환(Tae Hwan Kim),전재범(Jae Bum Jun),이인홍(In Hong Lee),배상철(Sang Cheol Bae),유대현(Dae Hyun Yoo) 대한내과학회 1998 대한내과학회지 Vol.54 No.2
Human adjuvant disease means the autoimmune disease or autoimmune disease like syndrome developed after plastic surgery using foreign body implantation. After first report of l by Miyoshi at 1964, a number of cases have been reported especially from Japan. Silicone has been known as biologically inert material, but a couple of side reaction and experimental data argue against such conventional idea. It is impossible to identify the exact role of implanted substance in the occurrence of autoimmune disease, but there are a few indirect evidences for adjuvant effect of silicone. The spectrum of HAD are as follows: unclassifiable connective disease like syndrome, rheumatoid arthritis, SLE, polymyositis, adult Still's disease, ITP, Hashimoto's thyroiditis, ctc. We experienced two cases of HAD manifesting as SI.E who had been injected with silicone fluid with for augmentation mammoplasty and report this with a review of the literature.
전신성 홍반성 루푸스 환자에서 다발성 간농양으로 발생된 Yersinia pseudotuberculosis 폐혈증
정자헌(Ja Hun Jung),김태환(Tae Hwan Kim),이인홍(In Hong Lee),양석철(Seok Chul Yang),전용철(Yong Cheol Jeon),김용수(Yong Soo Kim),김성윤(Seong Yoon Kim) 대한내과학회 1999 대한내과학회지 Vol.57 No.2
A 40-year-old man with systemic lupus erythematosus (SLE) and diabetes was found to have sepsis with multiple small hepatic abscesses secondary to Yersinia pseudotuberculosis which were detected by computed tomography (CT) scan and blood cultures. Sepsis with Y. pseudotuberculosis is uncommon but usually seen in patients with underlying liver diseases or diabetes. A few of those patients are accompanied by liver abscesses. Those patients with liver abscesses invariably have multiple small abscesses. CT scan of the liver was important in demonstrating the multiple small liver abscesses. Identification of the pathogen on blaod culture and elevated serum antibody titer to Y. pseudotu-berculosis are useful for diagnosis. Although rare, Y. pseudotuberculosis should be also considered as a possible cause in febrile patient with immunocompromised state such as SLE, diabetes or hemochromatosis.
황해 남동부 니질대의 물리적 성질: 동해 및 남해 니질대와의 비교
김대철,김신정,서영교,정자헌,김양은,김길영,Kim, Dae-Choul,Kim, Shin-Jeong,Seo, Young-Kyo,Jung, Ja-Hun,Kim, Yang-Eun,Kim, Gil-Young 한국해양학회 2000 바다 Vol.5 No.4
황해 남동부 니질대(mudbelt)퇴적물의 물리적 성질을 연구하기 위하여 총 10개 정점에서 해저 퇴적물을 채취하였다. 그 자료는 동해(남동 내대륙붕)및 남해니질대 자료와 비교하였다. 시추퇴적물들의 대부분은 실트질이 우세하며, 그 외 사질니 및 니로 구성되어 있다. 연구지역 표층퇴적물은 주로 금강에서 유입된 세립질 퇴적물이 연안류에 의해 남쪽으로 이동하여 분급화되면서 평균입도, 속도 및 습윤전밀도값은 점진적으로 감소하고 공극율은 증가하는 경향을 잘 보인다. 평균입도가 물성 및 음파전달속도를 결정하는데 주요한 변수로 나타났고, 수직적인 변화도 다져 짐작용이나 고화작용에 의한 영향보다는 퇴적물 조직 (주로 실트함량)의 변화 경향을 잘 반영하는 것으로 나타났다. 조직 및 물성간의 상관관계를 보면 비교모델로 사용한 남해 및 동해역 퇴적물과 가벼운 편차는 있으나 전반적인 경향은 유사하다 다만 가벼운 편차가 나타나는 것은 실트함량의 차이, 퇴적환경, 광물조성의 차이 및 가스의 함량 등 복합적인 결과로 보인다. Physical and acoustic properties of the Southeastern Yellow Sea Mud (SEYSM) of Korea were studied by using 10 piston cores. The data were also compared with mudbelt sediments in the South Sea and the East Sea (southeastern inner shelf) of Korea. The sediments were mainly composed of homogeneous silt. Sandy mud and mud were minor components. The major source of sediment in the study area is probably the Keum River. Finegrained sediments discharged from the river are transported southward by coastal current, resulting in a gradual southward increase in porosity and a decrease in wet bulk density and sound velocity. The mean grain size especially appears to be the most important variable to determine the physical properties and velocity. The variations of physical properties with burial depth are dependent more strongly on sediment texture (especially, silt content) than compaction and/or consolidation. Correlations between the physical properties and the sediment texture show slight deviations from those of the East Sea and the South Sea of Korea in spite of similar pattern within the limiting values. This is probably due to the differences in silt contents, sedimentary environments, mineral compositions, and gas contents.