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문맥압 항진과 식도 정맥류 출혈을 동반한 Agnogenic Myeloid Metaplasia
장지정 ( Jang Ji Jeong ),오기원 ( O Gi Won ),김정아 ( Kim Jeong A ),최종영 ( Choe Jong Yeong ),문찬수 ( Mun Chan Su ),서정민 ( Seo Jeong Min ),한석원 ( Han Seog Won ),심규식 ( Sim Gyu Sig ),백남종 ( Baeg Nam Jong ),김부성 ( Kim Bu 대한내과학회 1993 대한내과학회지 Vol.44 No.5
Agnogenic myeloid metaplasia is a syndrome in which the excessive fibroblast proliferation and collagen deposition in the bone marrow is accompanied by myeloid metaplasia of organ such as the liver, spleen, and lymph nodes. Typically, there is progressive splenomegaly, the gradual replacement of marrow elements by fibrosis, progressive anemla, variable changes in the number of granulocytes and platelets, and leukoerythroblastic peripheral blood picture. Here we report on a case of AMM associated with gastrointestinal bleeding due to ruptured esophageal varices. The portal vein was patent and the cause of portal hypertension was infiltration of liver by immature myeloid and erythroid cells and megakaryocytes.
이달의 엑스선 사진 : 호산구 증가를 동반한 급성 호흡 부전증
엄현석 ( Hyeon Seok Um ),장지정 ( Jie Jung Jang ),이숙영 ( Suk Young Lee ),김치홍 ( Chi Hong Kim ),권순석 ( Soon Seog Kwon ),김영균 ( Young Kyoon Kim ),김관형 ( Kwan Hyoung Kim ),문화식 ( Hwa Sik Moon ),송정섭 ( Jeong Sup Song 대한결핵 및 호흡기학회 1993 Tuberculosis and Respiratory Diseases Vol.40 No.3
다발성 소방이 형성된 결핵성 흉막염 환자에서 경부에 결핵성 단일 한성농양을 보인
이정아 ( Jeong Aa Lee ),김의숙 ( Eui Sook Kim ),백영주 ( Young Joo Baek ),이광섭 ( Gwang Seob Lee ),선우인철 ( In Cheol Sunwoo ),김대하 ( Dae Ha Kim ),장지정 ( Jie Jeong Jang ),박석민 ( Suck Min Park ),지미경 ( Mi Kyung Ji ) 대한결핵 및 호흡기학회 1996 Tuberculosis and Respiratory Diseases Vol.43 No.3
이달의 x-선 : 흉부 X-선상 속립성 결핵과 유사한 양상을 보인 Mycoplasma 폐렴에서 ARDS로 진행된 1예
김의숙 ( Eui Sook Kim ),이원석 ( Won Seok Lee ),이강룡 ( Kang Ryung Lee ),이정아 ( Jeong Aa Lee ),백영주 ( Young Joo Baek ),이광섭 ( Gwang Seob Lee ),선우인철 ( In Cheol Sunwoo ),김대하 ( Dae Ha Kim ),장지정 ( Jie Jeong Jang ) 대한결핵 및 호흡기학회 1996 Tuberculosis and Respiratory Diseases Vol.43 No.4
폐렴을 동반한 15 세 남자 환자에서 발견된 선천성 낭포성 유선종 폐기형 1 예
백영주(Young Joo Baek),이정아(Jeong Aa Lee),김의숙(Eui Sook Kim),이원석(Won Seok Lee),이강룡(Kang Ryang Lee),이광섭(Gwang Seob Lee),김신응(Synn Eung Kim),선우인철(In Cheol Sunwoo),김대하(Dae Ha Kim),장지정(Jie Jeong Jang),한영숙(Young 대한내과학회 1997 대한내과학회지 Vol.52 No.1
Congenital cystic adenomatoid malformation(C.C. A.M.) is a rare variant of congenital pulmonary cystic diseases. C.C.A.M. was first distinguished from other pulmonary cystic lesions by Ch`in and Tang in 1949. It is characterized by cessation of bronchiolar maturation with an overgrowth of mesenchymal elements and proliferation of polypoid glandular tissue in the absence of normal alveolar differentiation. In 80% to 95% of cases, C.C.A.M. of the lung is confinded to a single lobe and there is no lobe predilection and right and left predominance. The clinical presentation may be widely variable, ranging from intrauterine fetal death secondary to nonimmune hydrops fetalis to discovery in childhood after recurrent pulmonary infections. Definitive treatment is removal of affected lobe. In rare instances, there is cases of myxosarcoma, embryonal rhabdomyosarcoma. Bronchoalveolar carcinoma arising in C.C.A.M.. So, resection is recommended even if they are asymtomatic. We have experienced a case of congenital cystic adenomatoid malformation (type II) of the lung in 15 year old man with pneumonia. After the improvement of pneumonia, surgical operation was performed. A brief review of the related literature is presented.
전자 현미경상 Epinephrine 과립이 관찰된 Zuckerkandl 기관에 발생한 Norepinephrine 분비성 갈색세포종 1예
이원석,김의숙,이강룡,이정아,장지정,선우인철,김대하,이광섭,백영주 대한내분비학회 1996 Endocrinology and metabolism Vol.11 No.2
Extraadrenal pheochromocytomas developed from the paraganglia other than adrenal medulla are uncommon tumors. Such lesions have been reported that as much as 10% of retroperitoneal paragliomas arise outside the adrenal gland. But their incidence and prognosis are changing partly as a result of progression in developmental mechanism, diagnostic tools and concepts including ultrastructure, immunohistochemistry. The ultrastructure of chromaffine neoplasm from adrenal and extraadrenal tissues has been studied with chrornaffine granule specificity and type of catecholamine content. With rare exceptions, extraadrenal chrornaffine tumor mainly has high concentration of norepinephrine which is suggested as dict relationship to numoruos electrone dense granular bodies in the cell cytoplasrm. High or intermediate level of epinephrine in tissue is associated with cytoplasmic granular bodies of much less density. Recently we experienced the exception, a case of norepinephrine secreting pheochrom-ocytoma in the organ of Zuckerkandl with epinephrine granules in cytoplasm and this discrepancy probably due to the plasticity - the differences in developmental process and local factors between adrenal medulla and extraadrenal tissues(J Kor Soc Endocrinol 11:233 ~239, 1996).