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심한 우심실 유출로 폐쇄가 동반된 양심실 비후성 심근증 1예
임달수 ( Dal Soo Lim ),이창하 ( Chang-ha Lee ) 대한내과학회 2019 대한내과학회지 Vol.94 No.1
Hypertrophic cardiomyopathy (HCM) has diverse pathophysiological and clinical features, according to the extent and severity of the hypertrophy development. Hypertrophy mostly involves the left ventricle and sometimes causes a left ventricular outflow tract obstruction. Right ventricular involvement is less frequent, and even the severe form of a right ventricular outflow tract (RVOT) obstruction by concurrent right ventricular hypertrophy in a patient with HCM is rare. We report a case of biventricular HCM with a clinically, morphologically, and hemodynamically significant RVOT obstruction, which had been treated successfully with surgical myectomy. (Korean J Med 2019;94:119-123)
혈소판막 당단백질 전기영동으로 확진된 혈소판 무력증 1 예
현대성(Dae Sung Hyun),오성윤(Sung Yun Oh),임달수(Dal Soo Lim),황기석(Kee Suk Whang),송경순(Kyung Soon Song) 대한내과학회 1992 대한내과학회지 Vol.43 No.1
Glanzmann`s thrombasthenia is a rare autosomal recessive inherited bleeding disorder associated with abnormal clot retraction and a normal platelet count. This disorder is characterized by the inability of the aggregation of platelets in response to the stimulation of ADP, epinephrine or collagen but it can aggregate by ristocetin. The primary feature of this disorder is the deficiency or abnormality of the glycoprotein IIb/IIIa complex, one of the major surface proteins of the platelet membrane participating in the aggregation between the platelets with fibrinogen. This disorder can be detected by the analysis of the glycoprotein Ilb/IIIa complex on the platelet membrane of the patient by sodium dodecyl sulfate polyacrylamide gel electrophoresis (SDS-PAGE). We experienced one case of Glanzmann's thrombasthenia with iron deficiency anemia in a 16-year-old male, who had suffered from frequent gingival bleeding, epistaxis, and easy bruising. After platelet function test and SDS-PAGE, we diagnosed him as Glanamann`s thrombasthenia with iron deficiency anemia due to chronic blood loss.
간장 ( 肝臟 ) 및 담도 ( 膽道 ) : 고령자에서 간질환의 임상적 고찰
배정동(Jung Dong Bae),최재진(Jae Jin Choi),현대성(Dae Sung Hyun),임달수(Dal Soo Lim),오성윤(Sung Yoon Oh) 대한소화기학회 1991 대한소화기학회지 Vol.23 No.2
N/A Recently, aged patient admitted more frequently due to increased longevity and accessibility to medical center. This report is clinical review of 92 patients who were diagnosed as liver disease at the Department of Internal Medicine, Catholic Hospital from January, 1988 to December, 1990. The following results were obtained. 1) Liver cirrhosis was 67%, hepatoma was 29% type B hepatitis was 4%, and combined liver cirrhosis and hepatoma was 5%. 2) The male to female ratio was 1.5 : 1 in liver cirrhosis and 2 : 1 in hepatoma. 3) HBs antigenemia was 40%; in liver cirrhosis and 29% in hepatoma. 4) 50% of liver cirrhosis patients and 33% of hepatoma patients had history of alcohol drinking. 5) In liver cirrhosis, the symptoms and signs on admission were abdominal pain (45%), hematemesis (16%), and jaundice (14%), and in hepatoma, those were abdominal pain (74%) and weight loss (11%). 6) Overall hospital mortality was 41%. and the cause of death was hematemesis (6 cases) and hepatic encephalopathy (6 cases) in liver cirrhosis, and hepatic failure (15 cases) in hepatoma.
Child-Pugh 분류 A군 간경화에 수반된 간폐증후군
김정선 ( Jung Sun Kim ),김창환 ( Chang Hwan Kim ),김계수 ( Gye Su Kim ),임달수 ( Dal Soo Lim ),황흥곤 ( Hweung Kon Hwang ),노영무 ( Young Moo Ro ) 대한결핵 및 호흡기학회 2009 Tuberculosis and Respiratory Diseases Vol.66 No.1
Hepatopulmonary syndrome (HPS) is characterized by a defect in arterial oxygenation that`s induced by pulmonary vascular dilatation in the setting of liver disease. Some studies have shown the relationship between the presence of the HPS and the severity of liver disease, but there are only rare cases of HPS inpatient with Child-Pugh class A liver cirrhosis. We report here on a case of a 58 years-old male who suffered from progressive dyspnea for the previous few years. He was diagnosed with alcoholic liver cirrhosis 5 years previously. There was no significant abnormality on the chest radiograph and transthoracic echocardiography, but the arterial blood gas analysis revealed severe hypoxemia. Contrast-enhanced transesophageal echocardiograpy with agitated saline demonstrated a delayed appearance of microbubbles in the left cardiac chambers. Thus, he was finally diagnosed with HPS. This case suggests that we should consider HPS when a patient with compensated liver cirrhosis has unexplained dyspnea.
김우규(Woo Gyu Kim),김정경(Jeong Kyung Kim),전성희(Seong Hee Jeon),임달수(Dal Soo Lim),홍석근(Suk Keun Hong),황흥곤(Hweung Kon Hwang),김미영(Mi Young Kim) 대한내과학회 2000 대한내과학회지 Vol.58 No.4
Fungal prosthetic valve endocarditis is a rare, poo-prognostic disease. The risk factors for fungal valve endocardits are open heart surgery, hyperalimentation, antibiotic therapy, IV drug abuse, concomitant bacterial endocarditis and immunosuppression. We report a case of aspergillus endocarditis in the aortic valve, which extended to ascending aorta after Redo-aortic valve replacement surgery. A 22-year-old male patient underwent Redo-aortic valve replacement surgery with 23mm-sized Sorin valve(bi-leaflet tilting disc valve) due to prosthetic valve failure. He was readmitted because of development of cough, anorexia, fatigue and fever after operation. The results of repeated blood culture were negative, and the symptoms continued in spite of 2 week treatment with broad spectrum antibiotics. Echocardiography and spiral computed tomographic angiography revealed multiple, huge masses in the aortic valve extending to ascending aorta. Emergent surgery was performed. Infected valve and surrounding areas were widely excised and aortic homograft was inserted. Resected aorta and prosthetic valve showed multiple mass-forming vegetations, measuring up to 4㎝×3㎝×3㎝. Microscopically, they revealed fungal organisms, showing sharp-angle branching and septate hyphae. Aspergillus flavus was isolated in culture of resected tissue. The patient suddenly died of ventricular fibrillation 3 weeks after surgery in spite of treatement with intravenous amphotericin B.(Korean J Med 58:466-471, 2000)