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거대세포바이러스 감염을 동반한 선천성 흉선이형성증 1 예
이상일(Sang Il Lee),남승연(Seung Yeon Nam),강미애(Mee Ae Kang),안강모(Kang Mo Ahn),고영재(Young Jae Koh),서연림 대한소아알레르기호흡기학회(구 대한소아알레르기 및 호흡기학회) 2000 소아알레르기 및 호흡기학회지 Vol.10 No.2
N/A Twenty-four months old female child was expired with disseminated Cytomegalovirus infections. The child had a history of intrauterine and postnatal growth retardation and recurrent episodes of upper respiratory tract infection. At the age of 17 months, she had idiopathic thrombocytopenic purpura which was unresponded to intravenous immunoglobulin and steroid. Depending upon the bone marrow biopsy finding at the age of 21 months, myelodysplastic syndrome was suspected and she was treated with chemotherapy(Ara-C). Two months later, pancytopenia was developed with severe pneumonia. Cytomegalovirus was isolated from trachea, blood and urine, and she died. Postmorterm examination revealed congenital thymic dysplasia, which was characterized by a mass of mescenchymal and endothelial cells with occasional lymphocytes and the absence of Hassall`s corpuscles. Lymph nodes were composed of supporting tissue without follicular differentiation. Cytomegaloviral inclusions were found in the endothelial or epithelial cells of visceral organs including lung, heart, liver, pancreas, gastrointestinal tract, thymus, spleen, lymph nodes, retina, brain, kidney and adrenal glands.
배상영,박선주,남승연,정지아,서정완,이선화,Bae, Sang-Young,Park, Sun-Joo,Nam, Seung-Yeon,Jung, Ji-A,Seo, Jeong-Wan,Lee, Sun-Wha 대한소아소화기영양학회 1999 Pediatric gastroenterology, hepatology & nutrition Vol.2 No.2
저자들은 심한 빈혈과 복통을 주소로 내원한 폐결핵을 동반하지 않은 9세 여아에서 시행한 대장내시경 소견과 생검 조직의 배양 검사로 진단하고 항결핵제 치료로 증상이 호전된 예를 경험하여 보고하는 바이다. Childhood intestinal tuberculosis is difficult to diagnose for its protean clinical manifestations, especially in cases without pulmonary involvement. Differential diagnosis with Crohn's disease, inflammatory bowel disease and other malignancy is also important. Surgery has often been required for pathologic confirmation or therapy. Colonoscopy may be performed safely under consciousness sedation in children for bacteriologic and histopathologic confirmation of the biopsy specimen in addition to gross appearance of the lesion. We have experienced a case of intestinal tuberculosis presenting with chronic abdominal pain, diarrhea, weight loss and anemia in a 9 year old girl who was diagnosed by a colonoscopic examination and culture of the biopsy specimen from the ascending colon. The patient was managed with antituberculous drugs and recovered uneventfully.
소아의 아토피피부염과 급성 두드러기 환자에서 계란 , 우유 및 대두에 대한 감작률 비교
정진아(Jin A Jung),남승연(Seung Yeon Nam),한영신(Young Shin Han),박용민(Yong Mean Park),이주석(Ju Suk Lee),전경희(Kyoung Hee Jeon),정은희(Eun Hee Jeong),안강모(Kang Mo Ahn),이상일(Sang Il Lee) 대한천식알레르기학회 2001 천식 및 알레르기 Vol.21 No.4
Background: Atopic dermatitis(AD) and urticaria(UR) are common allergic diseases associated with various food allergens. We evaluated possible differences of sensitization rates to egg, milk, and soy bean according to the age in children with AD and UR. Materials and method: One hundred and thirty-six patients(n=100 in AD, n=36 in UR) who had visited Samsung Medical Center from January 1998 to February 2000 were enrolled and divided into 3 groups by age: group Ⅰ, children under 1year of age (45 in AD, 17 in UR); group Ⅱ, between 1 and 3 years of age (32 in AD, 12 in UR); and group Ⅲ, children over 3 years of age (23 in AD, 7 in UR). Total and specific IgE to cow milk, a-lactalbumin(a-LA), β-lactoglobulin(β-LG), casein, soy, egg white(EW) and egg yolk(EY) were measured by RAST or CAP system. Results: Total IgE was highest in group Ⅲ of AD patients(p<0.05), while there were no significant differences among the three groups of UR patients(p>0.05). The most common allergen among AD patients was EW(54%) for all age groups (51.1% in group Ⅰ, 56.3% in group Ⅱ, 56.5% in group Ⅲ), while among UR patients, β-LG(22.2%) was the most common food allergen, especially β-LG(35.3%) in Group Ⅰ, CM/casein(27.3%) in Group Ⅱ, and CM/α-LA/casein/EW(12.5%) in Group Ⅲ. Sensitization rate to EW, EY and soy bean were higher in AD than in UR(p<0.05). Conclusion: Sensitization rate to egg was higher in patients with AD than in those with UR. Restriction of eggs maybe helpful in management of infants with a family history of AD. (J Asthma Allergy Clin Immunol 21: 610-7, 2001)
근거이론을 통한 사회적기업의 지속발전 모형에 대한 연구
이영범(Lee, Young-Bum),박성우(Park, Sung-Woo),남승연(Nam, Seung-Yeon),정무권(Chung, Moo-Kwon) 서울행정학회 2012 한국사회와 행정연구 Vol.22 No.4
The purpose of this study is to suggest a model of sustainable development for Korean social enterprises. The literature in this field tends to be fragmented, focusing on the factors for social enterprise success, and as such lacks a coherent theory-based model. Using grounded theory, this study builds a model of sustainable development for social enterprises in Korea. This research confirms that sustainable development is a core requirement of social enterprises with social and economic goals. This requirement can be seen through low competitiveness and profitability, a lack of skilled workers, a conservative inclination toward the non-profit sector, and inappropriate institutional support. Accordingly, the strategies for enhancing the market power of social enterprises could allow the organizations to realize their dual goals and stabilize operations through the intervening effects of network and leadership. The study concludes by stating the importance for social enterprises to recognize the cycles of the growth process and to create multifaceted measures for their sustainability.
열처리에 따른 콩 단백질 Allergenicity 변화
손대열,이보련,손동화,이광신,안강모,남승연,이상일,Son, Dae-Yeul,Lee, Bo-Ryun,Shon, Dong-Wha,Lee, Kwang-Shin,Ahn, Kang-Mo,Nam, Sung-Yeon,Lee, Sang-Il 한국식품과학회 2000 한국식품과학회지 Vol.32 No.4
콩은 우유, 계란과 더불어 우리나라에서 과민성 알레르기를 일으키는 대표적인 식품중의 하나로 손꼽힌다. 이에 본 연구에서는 콩에 알레르기 반응을 일으키는 환아의 혈청과 콩 단백질을 토끼에 면역하여 얻은 다클론 항체를 이용하여 immunoblotting 및 ELISA 방법을 통하여 가열 처리한 콩과의 반응성을 조사 함으로서 가열처리가 콩의 항원성 내지는 알레르기성에 미치는 영향을 조사하였다. 물중탕으로 1 시간까지 가열처리 후 SDS-PAGE에 의해 분리된 콩 단백질은 열처리에 따른 콩 단백질 band의 변화를 관찰할 수 없었다. 또한 다클론 항체와의 반응성 확인을 위한 immunoblot 방법에서도 열처리에 따른 반응성의 차이는 나타나지 않았으며 콩 알레르기 환자의 혈청 역시 가열 처리에 따른 콩과의 반응성의 차이가 ELISA법을 이용한 측정에서 관찰되지 않았다. 이상의 결과로 부터 콩 알레르겐의 항원성 및 알레르기성은 가열처리에 의해 변화되지 않음을 확인할 수 있었다. Soy bean is one of the most common food material to cause food hypersensitivity reactions in Korea. In this study we have investigated the effect of heating on antigenicity and allergenicity change of soybeans by using immunoblotting and ELISA methods with serum of soybean allergic patients and polyclonal antibody against soybean proteins. Soybean proteins were extracted by one-hour heating in boiling waterbath and separated by SDS-PAGE. After heat treatment, no significant changes of soy protein patterns were observed in SDS-PAGE analysis. Furthermore, the heat treatment had no effect on the results in immunoblotting with polyclonal antibody as well as in ELISA with soybean allergic patients' serum. With these results it may be concluded that allergenicity and antigenicity of soybeans do not reduce by thermal treatment.
최종영 ( Jong Young Choi ),정은희 ( Eun Hee Chung ),남승연 ( Seung Yeon Nam ),성기웅 ( Ki Woong Sung ),안강모 ( Kang Mo Ahn ),김철규 ( Chul Kyu Kim ),이상일 ( Sang Il Lee ) 대한소아알레르기호흡기학회 2000 소아알레르기 및 호흡기학회지 Vol.10 No.4
Purpose : Causes of acute lower respiratory tract infections(ALRI) in children are diverse. But virus is the most common cause of ALRI, so it is important to under- stand the etiology and epidemiology of ALRI. This study was performed to investigate the etiologic organisms, age distribution, clinical manifestations and seasonal occurrence of ALRI in hospitalized children. Methods : We confirmed viral etiologies using nasopharyngeal aspirates in 377 patients of the ages of 15 years or younger who were hospitalized for ALRI from March, 1996 to February, 1999 at Samsung Seoul Hospital, Seoul, Korea. Viral agents were detected by virus isolation and antigen detection by indirect immunofluorescent staining. Results: The viral pathogens identified `were influenza A(22.2%), influenza B(9.0%), adenovirus(21.2%), parainfluenza virus type 1(8.8%), type 2(3.4%), type 3(15.1%) and respiratory syncytial virus(RSV)(20.2%). The occurrence of ALRIs was high under 2 year old. The clinical patterns of viral ALRI include pneumonia (49.9%), croup (20.2%), bronchiolitis(22.0%), tracheobronchitis(8.0%). The specific viruses are frequently associated with specific clinical syndrome of ALHI. The respiratory agents and associated syndromes frequently have characteristic seasonal patterns. Conclusion: This study will help us to estimate the etiologic agents of ALRI, and to avoid inappropriate antibiotic therapy. An annual nationwide survey is necessary to understand the viral epidemiology associated with respiratory illness.
아토피피부염 환아에서 난백에 대한 IgG western blotting 분석
신미용(Mi Yong Shin),이광신(Kwang Shin Lee),손대열(Dae Yul Son),남승연(Seung Yeon Nam),함세창(Se Chang Ham),안강모(Kang Mo Ahn),강이석(I Seok Kang),이상일(Sang Il Lee) 대한천식알레르기학회 2000 천식 및 알레르기 Vol.20 No.4
Background: and objective: Specific IgE to food allergen is associated with atopic dermatitis, but it does not always show good clinical correlation. It has been suggested that IgG may be partly involved in allergen-induced reaction. This study was designed to investigate the clinical significance of specific IgG antibody to egg white (EW) in atopic dermatitis patients who showed improvement with egg elimination diet. Method: Eleven atopic dermatitis patients who responded to egg elimination diet were selected. They were classified into two groups group I(n=5) with positive specific IgE to EKV and group II(n=6) with normal levels of serum specific IgE. Two volunteers with no allergic diseases were enrolled in the control group. EW-specific IgG western blotting was performed with patient's serum and purified protein extracted from EW. Results : IgG western blotting to EKV in group I showed bands at 51.8 kD in two patients and bands at 35 kD in the others. In group II. Two showed bands at 51.8 kD, and diffuse bands at 35 kD -51.8 kD were found in four patients. There were no bands in the control group. Conclusion : Regardless of the presence of specific IgE. Specific IgG to EVJ was detected by western blotting in patients with egg-associated atopic dermatitis, suggesting that specific IgG may play a role in the pathogenesis of atopic dermatitis. (J Asthma Allergy Clin Immunol 20: 627-6:32. 2000)