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Acute unilateral isolated abducens nerve palsy associated with anti-GM1 immunoglobulin M antibody
Hyoshin Son,Ahwon Kim,Sang Bin Hong,Dae Lim Koo 대한임상신경생리학회 2019 Annals of Clinical Neurophysiology Vol.21 No.2
Acute ophthalmoparesis that includes the oculomotor, trochlear, or abducens nerve may occur as an initial presentation of Miller Fisher syndrome (MFS). The symptoms of MFS or variant forms of Guillain-Barre syndrome are pathogenically related to anti-GQ1b antibodies. We report a case of a 36-year-old man with unilateral isolated abducens nerve palsy associated with anti-GM1 antibody. To the best of our knowledge, this is the first report of unilateral isolated abducens nerve palsy with positivity for anti-GM1 immunoglobulin M antibody.
Paraneoplastic demyelination in the brain presenting as a clinically occult non-Hodgkin's lymphoma
Son, Hyoshin,Choi, Jongsuk,Kim, Sung Un,Park, Kyung Seok The Korean Society of Clinical Neurophysiology 2019 Annals of Clinical Neurophysiology Vol.21 No.2
Non-Hodgkin's lymphoma (NHL) may initially present with atypical neurological manifestations, including paraneoplastic neurological syndromes. Herein, we report the case showing an initial manifestation of systemic NHL with paraneoplastic demyelination in the brain that initially mimicked the symptoms of stroke, seizure, and brain tumor. A high index of suspicion and timely diagnostic workup is required to prevent diagnostic delay and commence proper management of the condition. In this situation, a whole-body FDG PET/CT could be useful to screen for occult malignancy.
Acute unilateral isolated abducens nerve palsy associated with anti-GM1 immunoglobulin M antibody
Son, Hyoshin,Kim, Ahwon,Hong, Sang Bin,Koo, Dae Lim The Korean Society of Clinical Neurophysiology 2019 Annals of Clinical Neurophysiology Vol.21 No.2
Acute ophthalmoparesis that includes the oculomotor, trochlear, or abducens nerve may occur as an initial presentation of Miller Fisher syndrome (MFS). The symptoms of MFS or variant forms of Guillain-Barre syndrome are pathogenically related to anti-GQ1b antibodies. We report a case of a 36-year-old man with unilateral isolated abducens nerve palsy associated with anti-GM1 antibody. To the best of our knowledge, this is the first report of unilateral isolated abducens nerve palsy with positivity for anti-GM1 immunoglobulin M antibody.
Hyoshin Son,Kyung-Il Park,Dae-Seop Shin,Jangsup Moon,Soon-Tae Lee,Keun-Hwa Jung,Ki-Young Jung,Kon Chu,Sang Kun Lee 대한신경과학회 2023 Journal of Clinical Neurology Vol.19 No.3
Background and Purpose Focal cortical dysplasia (FCD) is one of the most common causes of drug-resistant epilepsy, and necessitates a multimodal evaluation to ensure optimal surgical treatment. This study aimed to determine the supportive value of the morphometric analysis program (MAP) in detecting FCD using data from a single institution in Korea. Methods To develop a standard reference for the MAP, normal-looking MRIs by two scanners that are frequently used in this center were chosen. Patients with drug-resistant epilepsy and FCD after surgery were candidates for the analysis. The three-dimensional T1-weighted MRI scans of the patients were analyzed as test cases using the MAP. Results The MRI scans of 87 patients were included in the analysis. The radiologist detected abnormal findings correlated with FCD (RAD positive [RAD(+)]) in 34 cases (39.1%), while the MAP could detect FCD in 25.3% of cases. A combination of the MAP (MAP[+] cases) with interpretations by the radiologist increased the detection to 42.5% (37 cases). The lesion detection rate was not different according to the type of reference scanners except in one case. MAP(+)/RAD(-) presented in three cases, all of which had FCD type IIa. The detection rate was slightly higher using the same kind of scanner as a reference, but not significantly (35.0% vs. 22.4% p=0.26). Conclusions The results of postprocessing in the MAP for detecting FCD did not depend on the type of reference scanner, and the MAP was the strongest in detecting FCD IIa. We suggested that the MAP could be widely utilized without developing institutional standards and could become an effective tool for detecting FCD lesions.
Paraneoplastic demyelination in the brain presenting as a clinically occult non-Hodgkin’s lymphoma
Hyoshin Son,Jongsuk Choi,Sung Un Kim,Kyung Seok Park 대한임상신경생리학회 2019 Annals of Clinical Neurophysiology Vol.21 No.2
Non-Hodgkin’s lymphoma (NHL) may initially present with atypical neurological manifestations, including paraneoplastic neurological syndromes. Herein, we report the case showing an initial manifestation of systemic NHL with paraneoplastic demyelination in the brain that initially mimicked the symptoms of stroke, seizure, and brain tumor. A high index of suspicion and timely diagnostic workup is required to prevent diagnostic delay and commence proper management of the condition. In this situation, a whole-body FDG PET/CT could be useful to screen for occult malignancy.
Guillain–Barré Syndrome After COVID-19 Infection in Korea: A Case Series
Ryoo Nayoung,Son Hyoshin,Kim Jean Hee,Bae Dae Woong,An Jae Young 대한의학회 2024 Journal of Korean medical science Vol.39 No.5
Guillain–Barré syndrome (GBS) is an autoimmune-driven condition characterized by acute polyneuropathy, often emerging as a sequel to prior infections or vaccinations. This study presents the first reported cases of GBS emerging after the full recovery from coronavirus disease 2019 (COVID-19) infection in Korea. Despite experiencing mild acute COVID-19 symptoms, these patients faced substantial weakness attributed to GBS, significantly affecting their daily lives. The timely administration of intravenous immunoglobulin treatment halted the progression of symptoms, underscoring the critical importance of early intervention. These cases highlight the potential for neurological complications associated with COVID-19 and underscore the necessity for continuous monitoring and timely medical care.
김미림,이정민,윤정희,Hyoshin Son,최진우,한준구,최병인 대한영상의학회 2014 Korean Journal of Radiology Vol.15 No.2
Objective: To evaluate the impact of the adaptive iterative dose reduction (AIDR) three-dimensional (3D) algorithm in CT on noise reduction and the image quality compared to the filtered back projection (FBP) algorithm and to compare the effectiveness of AIDR 3D on noise reduction according to the body habitus using phantoms with different sizes. Materials and Methods: Three different-sized phantoms with diameters of 24 cm, 30 cm, and 40 cm were built up using the American College of Radiology CT accreditation phantom and layers of pork belly fat. Each phantom was scanned eight times using different mAs. Images were reconstructed using the FBP and three different strengths of the AIDR 3D. Theimage noise, the contrast-to-noise ratio (CNR) and the signal-to-noise ratio (SNR) of the phantom were assessed. Two radiologists assessed the image quality of the 4 image sets in consensus. The effectiveness of AIDR 3D on noise reduction compared with FBP were also compared according to the phantom sizes. Results: Adaptive iterative dose reduction 3D significantly reduced the image noise compared with FBP and enhanced the SNR and CNR (p < 0.05) with improved image quality (p < 0.05). When a stronger reconstruction algorithm was used, greater increase of SNR and CNR as well as noise reduction was achieved (p < 0.05). The noise reduction effect of AIDR 3Dwas significantly greater in the 40-cm phantom than in the 24-cm or 30-cm phantoms (p < 0.05). Conclusion: The AIDR 3D algorithm is effective to reduce the image noise as well as to improve the image-quality parameters compared by FBP algorithm, and its effectiveness may increase as the phantom size increases.
Additional Value of Metagenomic Sequencing in Diagnosis of Ventilatorassociated Pneumonia
( Ha Won Hwang ),( Jinwoo Lee ),( Hyoshin Son ),( Chang Kyung Kang ),( Hong Yeul Lee ),( Sang-min Lee ),( Jangsup Moon ) 대한결핵 및 호흡기학회 2021 대한결핵 및 호흡기학회 추계학술대회 초록집 Vol.129 No.-
Background Ventilator associated pneumonia (VAP) is associated with high mortality and morbidity. Unfortunately, conventional Methods often fail to identify the etiology of VAP and accurate microbial diagnosis remains difficult. As a result, broad-spectrum antimicrobial treatment is frequently used for long durations without clear evidence. We compared the use of nanoporebased metagenomic sequencing to conventional diagnostic Methods in the diagnosis of VAP. Method Patients who underwent bronchoscopy with suspicion of VAP between February 2020 and February 2021 in a medical intensive care unit of a university affiliated hospital were screened for analysis. There were 37 cases in which both the conventional diagnostic Methods and nanopore sequencing were performed using bronchial washing or bronchoalveolar lavage specimens. The nanopore sequencing Results were compared to the conventional diagnostic Methods. Results Among the 37 cases, conventional culture was positive in 12 cases and negative in 25 cases. In culture-positive cases, nanopore sequencing detected the same pathogen in 11 cases (concordance rate 91.7%). Nanopore sequencing did not detect S.maltophilia in 1 case. In culture-negative cases, nanopore sequencing also were negative in 6 cases and upper respiratory tract flora was detected in 5 cases (concordance rate 44%). Additional microbiological diagnosis was possible using nanopore in 14 cases. The additional microorganisms detected were E.faecium, A.baumanni, S,maltophilia, P.jirovecii, E.coli, S.aureus, L.pneumophilia, etc (table 1). Conclusion In patients with clinical suspicion of VAP, nanopore sequencing of bronchoscopic specimens showed high concordance rate with the conventional diagnostic Methods. In culture-negative cases, additional microbiologic diagnosis was also possible using nanopore sequencing.