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전신성 홍반성 낭창에 합병된 유미지립혈증 증후군 1 예
조철수(Chul Su Cho),이상헌(Sang Heon Lee),홍연식(Yeon Sik Hong),박동준(Dong Joon Park),김호연(Ho Yun Kim) 대한내과학회 1993 대한내과학회지 Vol.45 No.5
A case of woman aged 20 year old with acquired type I hyperlipoproteinemia and systemic lupus erythematosus is described. The patient presented with fasting chylomicronemia, hepatomegaly, abdominal pain suggesting incipient acute pancreatitis. Treatment with three sessions of plasmapheresis and concomittent use of steroid corrected the findings of chylomicronemia syndrome. It is suggested that in this case, possibly dysglobulinemia due to systemic lupus erythematosus was associated with development of hyperchylomi-cronemia.
박경수 ( Kyung Su Park ),김완욱 ( Wan Uk Kim ),이신석 ( Shin Seok Lee ),민준기 ( Jun Ki Min ),이상헌 ( Sang Heon Lee ),박성환 ( Sung Hwan Park ),홍연식 ( Yeon Sik Hong ),조철수 ( Chul Soo Cho ),김호연 ( Ho Youn Kim ) 대한류마티스학회 1998 대한류마티스학회지 Vol.5 No.2
Objective: To determine the causes of death and predictor variables for mortality in patients with SLE. Method: We evaluated 544 SLE patients who were monitored in the Lupus Clinic of Catholic Medical Center from January 1993 to December 1997 and checked clinical and laboratory variables which represent organ involvement in SLE and its disease activity. Determination of the causes of death were based on detailed clinical records in 38 cases who died during admission, and clinical and laboratory variables were compared between the survivors(n=506) and deceased(n=38). Result: Causes of death were as follows; 13 from infection(34.2%), 7 SLE-related deaths(18.4%), 6 from pulmonary hypertension(15.7%), 5 from thrombotic thrombocytopenic purpura or disseminated intravascular coagulation(13.2%), 4 from cerebrovascular accident(10.5%), and 3 from other causes(Table 2). In multivariate analysis, renal involvement(relative risk, RR 3.4), CNS involvement(RR 2.9), thrombocytopenia(RR 2.3) and age>50 years(RR 2.5) at presentation were predictor variables for mortality. Conclusion: The most common cause of death in patients with SLE was infection, followed by SLE-related death. Renal involvement, CNS involvement, thrombocytopenia, and age>50 at presentations increased the risk of death in patients with SLE.
전신성 홍반성 루푸스에 병발한 Aspergillosis 2예
김현수 ( Hyun Su Kim ),홍연식 ( Yeon Sik Hong ),배상수 ( Sang Su Pae ),김완욱 ( Wan Uk Kim ),민준기 ( Jun Ki Min ),이상헌 ( Sang Heon Lee ),박성환 ( Seong Whan Park ),조철수 ( Chul Soo Cho ),김호연 ( Ho Youn Kim ) 대한류마티스학회 1999 대한류마티스학회지 Vol.6 No.3
Invasive infections with Aspergillus species may occur in patients with severe immune deficits and have been described rarely in systemic lupus erythematosus. We present two cases of pulmonary aspergillosis in steroid-treated systemic lupus erythematosus(SLE). Both patients had active SLE treated with high dose corticosteroids and prescribed with broad spectrum antibiotics. One patient had combined infection with pulmonary tuberculosis and the other present granulocytopenia. The diagnosis was delayed because symptoms and radiologic findings were confused with lupus pneumonitis and bacterial infections. This was similar to those reported previously. Diagnosis was confirmed by identification of the typical septated hyphae within tissue. We prescribed high dose amphotericin B to both patients. But one died with sepsis. Aspergillosis should be suspected in patients with active SLE who are immunocompromised and sustain concomitant bacterial infections. More aggressive diagnostic investigation and treatment may be needed to improve poor prognosis.
제한성 베게너 육아종증(Wegener`s Granulomatosis)과 유사한 양상을 보인 NK/T세포 림프종
박윤정 ( Yun Jung Park ),조철수 ( Chul Su Cho ) 대한류마티스학회 2010 대한류마티스학회지 Vol.17 No.3
It is occasionally difficult to distinguish Wegener`s granulomatosis (WG) from other diseases including malignancy, tuberculosis, and various types of vasculitis because of the overlapping symptoms and signs. We report on a patient with NK/T cell lymphoma who was treated with a limited form of WG. At his first visit, he presented with left foot drop and recurrent nasal swelling. Necrosis and massive infiltration of inflammatory cells were identified on a nasal tissue biopsy. Sural nerve biopsy findings also showed infiltration of inflammatory cells in both the endoneurium and perivascular area; thus, a diagnosis of a limited form of WG was made. After combination therapy with a glucocorticoid and oral cyclophosphamide was initiated, his condition completely recovered without recurrence for the next 2 years. However, he visited the hospital again for recurrence of nasal swelling. Repeated biopsy of nasal tissues, combined with an immunophenotypic analysis revealed NK/T cell lymphoma. The possibility of NK/T lymphoma should be considered when evaluating a limited type of WG, which shows atypical findings on biopsy as well as recurrent deterioration, as a suboptimal dose of immunosuppressive therapy may mask its expression and lead to a poor prognosis.
항인지질 항체 증후군 환자의 혈청 내 Monocyte Chemoattractant Protein-1의 증가
박종서 ( Jong Seo Park ),박경수 ( Kyung Su Park ),최진정 ( Jin Jung Choi ),윤종현 ( Jong Hyeon Yoon ),김용주 ( Yong Ju Kim ),김완욱 ( Wan Uk Kim ),민도준 ( Do Jun Min ),박성환 ( Sung Hwan Park ),조철수 ( Chul Soo Cho ),김호연 ( Ho 대한류마티스학회 2002 대한류마티스학회지 Vol.9 No.4
Objective: To determine the association of serum monocyte chemoattractant protein-1 (MCP-1) concentration and clinical variables of antiphospholipid syndrome (APS). Methods: We investigated the serum concentration of MCP-1 in systemic lupus erythematosus (SLE) patients by ELISA. The clinical features of APS were evaluated in SLE patients, and anticardiolipin antibody (aCL) was determined at the time of blood sampling. Results: Serum MCP-1 levels (median [range]) in 76 SLE patients were significantly higher than those in 99 healthy controls (192 pg/ml [116, 560] versus 91 pg/ml [26~251], p<0.001). Patients with APS had higher levels of serum MCP-1 than those without (p=0.013). Seum MCP-1 levels were significantly higher in patients with thrombosis and recurrent fetal loss than those without. Among APS patients, patients with longer disease duration (>3 years) had higher levels of MCP-1 than those without (263 pg/ml [166,534] versus 196 pg/ml [116,322], P=0.023). Furthermore, serum MCP-1 levels correlated well with IgG aCL titers (r=0.62, p<0.001). Conclusion: Serum MCP-1 levels were elevated in SLE patients, particularly in those with APS, and correlated well with titers of IgG aCL and thrombosis. Our data suggest that increased MCP-1 may play a critical role in the development of APS in SLE patients.
신재흥(Jae-Heung Shin),이상하(Sang-Ha Lee),이상철(Sang-Chul Lee),김병직(Byung-Jik Kim),조철수(Chul-Su Cho) 대한전기학회 2009 대한전기학회 학술대회 논문집 Vol.2009 No.7
IPTV, 인터넷 전화 등 인터넷 가입자에게 제공되는 서비스가 지속적으로 증가하고 있으며, 서비스 종류의 증가와 동시에 통신 사업자가 제공하는 네트워크 속도의 향상에도 불구하고 서비스 사용자의 불만이 증가하고 있다. 이러한 불만의 원인은 인터넷을 이용하는 모든 서비스가 네트워크 자원을 공유하기 때문에 특정 서비스의 품질을 확보하지 못하는 현상의 발생에 기인한다. 따라서 인터넷 사업자의 입장에서는 인터넷을 이용하여 다양한 서비스가 이루어지지만, 해당 서비스의 품질을 확보하는 것이 중요한 과제로 등장하였다. 본 논문에서는 IPTV 서비스 환경과 유사한 실험망 환경을 구축하고, HD급 영상 데이터를 멀티캐스트 스트리밍 방송 서비스를 통해 네트워크상에서 트래픽 부하에 따른 IPTV 수신영상품질의 변화를 살펴보고, 영상품질에 따른 네트워크 측정요소의 임계치를 도출한다.
류마티스 관절염에서 제 2형 콜라겐에 대한 T림프구 증식반응과 염증지표 및 관절손상과의 관계
최진정 ( Jin Jung Choi ),김완욱 ( Wan Uk Kim ),조미라 ( Mi La Cho ),이명수 ( Myeung Su Lee ),서영일 ( Young Il Seo ),민도준 ( Do June Min ),박성환 ( Sung Hwan Park ),조철수 ( Chul Soo Cho ),김호연 ( Ho Youn Kim ),김기준 대한류마티스학회 2002 대한류마티스학회지 Vol.9 No.2
Objective: To investigate the role of T cell responses to type II collagen (CII) in disease progression in rheumatoid arthritis (RA). Methods: T cell proliferative responses to bovine CII by peripheral blood mononuclear cells (PBMC) from early RA patients (duration <5 years) were assayed by mixed lymphocyte culture. Clinical and laboratory variables including erythrocyte sedimentation rate (ESR) and C reactive protein (CRP) were examined at the time of sampling. Radiographic damage on hand X-rays was evaluated by the method of Steinbrocker and Sharp. Results: In a cross-sectional study, patients (n=22) with positive T cell responses (stimulation index: SI≥2) had higher levels of CRP and ESR than those (n=21) not showing T cell responses. The number of damaged joints (by Steinbrocker`s method) and damaged joint scores (by Sharp`s method) were significantly higher in patients with positive T cell responses than in those without. The joint space narrowing scores correlated well with T cell responsiveness to CII. Patients (n=15) with both positive T cell responses and RA-susceptible allotypes, HLA-DR1 or DR4, had greater damaged joint scores than the rest of patients (n=24). Conclusion: T cell proliferative responses to CII are associated with inflammatory activity and radiographic severity in RA. Our data suggest that CII reactive T cells may play an important role in the pathogenic process of joint damage.
권낙기 ( Nak Ki Kwun ),민준기 ( Jun Ki Min ),박경수 ( Kyung Su Park ),전은정 ( Eun Jung Jun ),조철수 ( Chul Soo Cho ),변재영 ( Jae Young Pyun ),김호연 ( Ho Youn Kim ) 대한류마티스학회 1998 대한류마티스학회지 Vol.5 No.2
With varying frequency, systemic sclerosis may involve nearly all parts of the gastrointestinal tract. Pneumatosis cystoides intestinalis(PCI) which is characterized by the presence of multiple gaseous cysts in the intestinal wall of either subserosal or submucosal location rarely occurs in patients with systemic sclerosis. PCI may be asymptomatic, but weight loss, abdominal distension, and nausea are frequent symptoms secondary to sytemic sclerosis. Although the mechanisms responsible for the development of PCI in systemic sclreosis remains unclear, bacterial overgrowth, mucosal damage secondary to ischemic bowel disease are considered to be possible mechanisms. It is a benign condition that often responds to conservative management, however it may be a harbinger of end stage disease particularly in systemic sclerosis. Here, we report a case of PCI accompanying by systemic sclerosis with brief review of literatures.
내과적 질환에 병발된 반사성 교감신경계 위축 증후군 20 예의 분석
송소향(So Hyang Song),이정득(Jeong Deuk Lee),이상헌(Sang Heon Lee),홍연식(Yeon Sik Hong),조철수(Chul Su Cho),박동준(Dong Joon Park),정수교(Soo Kyo Chung),김호연(Ho Yun Kim) 대한내과학회 1993 대한내과학회지 Vol.45 No.5
Reflex sympathetic dystrophy syndrome (RSDS) is an distinct symptom complex characterized by diffuse distal-limb pain, edema, vasomotor skin change and dystrophic skin change. It has been associated with limb-trauma, acute stoke, myocardial ischemia, peripheral neuropathy, phamacological agents such as phenobarbital and antituberculosis agents and malignancy. We report the clinical and radiological features of 20 patients who were diagnosed of RSDS at Kangnam Saint Mary's Hospital between January 198S and May 1991. The results were as fo1lows: 1)According to Kozin's criteria, seven (35%) are diagnosed of definite RSDS, eight (40%) of probable RSDS, and five (25%) of doubtful RSDS. 2) Disorders associated with RSDS were cerebrovascular disease (7 patients), malignancy (4 patients), myocardial ischemia (4 patients) and antituberculosis drug (2 patients). The remaining 6 padtients (30%) had no specific precipitating events. 3) Review of the Three phase bone scitigraphy (TPBS) for 20 patients indicated that nineteen of twenty patients (95%) has asymmetric and abnormal blood flow in TPBS. 4) Most patients were diagnosed early, therefore, had symptomatic relief without sequele such as flexion contracture of skin or subcutaneous atrophy by analgesics, steroid, calcitonin and physical therapy. In summary, the TPBS is a potentially sensitive and specific test to corroborate the diagnosis of RSDS and we can expect to have symptomatic relief without sequence if this disorder could be diagnased and treated, early.
강성호(Sung Ho Kang),김석찬(Seok Chan Kim),위성헌(Sung Heon Wie),김용주(Yong Joo Kim),박성환(Sung Hwan Park),이상헌(Sang Heon Lee),조철수(Chul Su Cho),김호연(Ho Yun Kim) 대한내과학회 1995 대한내과학회지 Vol.49 No.1
Mononeuritis multiplex is characterized by multifocal and random lesions of peripheral nerves and associated with systemic vasculitis such as diabetes, rheumatoid arthritis, systemic lupus erythematosus, polyarteritis nodosa. Sjogren syndrome, temporal arteritis, leprosy, amyloidosis. Mononeuritis multiplex was distributed bilaterally throughout the body. The early diagnosis and the aggressive treatment should be required in view of the significant mortality. We experienced a case of vasculitis of rheumatoid arthritis complicated by mononeuritis multiplex. We could make a diagnosis based on the biopsy of the peroneal muscle and the sural nerve. Pathologic findings showed vasculitic change of muscle and vasa nervorum. Electrodiagnostic abnormalities were very similar to those seen in mononeuritis multiplex. This patient was treated with prednisolone plus cyclophosphamide. He showed clinical improvement and was discharged. We presents this case with a review of the literature.