http://chineseinput.net/에서 pinyin(병음)방식으로 중국어를 변환할 수 있습니다.
변환된 중국어를 복사하여 사용하시면 됩니다.
전혜정(Hye Jeong Jeon),이백희(Baeck Hee Lee),황세희(Se Hee Hwang),황용승(Yong Seung Hwang),지제근(Je G. Chi) 대한소아신경학회 1993 대한소아신경학회지 Vol.1 No.1
Alexander disease is a rare progressive dysmyelogenetic leukodystrophy of still unkown etiology clinically characterized by of megallencephaly, psychomotor retardation, spasticity and seizure. We experienced one case of Alexander disease in a 9 month old male infant. He was delivered by Caesarean section a 33 weeks gestational age with birth weight of 2. 15kg and birth head circumference 34cm. Between 4 months and 7months of age, his head circumference was abruptly increased and delayed motor milestone were appeared. On examination at admission at 9 months of his age, he had focal seizure, visual inattentiveness, spastic quadriparesis with marked head lag and extensor response on Babinski sign. Brain MRI showed abnormal signal intensities in deep white matter and subcortical white matter symmetrically, low densities in TWI and high signal in TWI. We tried brain biopsy and it showed diffuse deposition of Rosenthal fiber in white matter of frontal lobe. He was managed with phenytoin and phenobarbital due to subsequent generalized clonic seizure. After anticonvulsant therapy, the seizure was controlled. We report this case and the brief review of literature of Alexander lisease.
병원 근무 간호사들의 염색체 이상 및 소핵 빈도에 미치는 위험요인
전혜정(Hye Jeong Jeon),김태환(Tae Hwan Kim),최수용(Soo Yong Choi),정해원(Hai Won Chung) 한국환경성돌연변이발암원학회 2005 한국환경성돌연변이·발암원학회지 Vol.25 No.4
Analysis of chromosome aberration (CA) and cytokinesis-block micronucleus (CBMN) assay in peripheral lymphocytes of nurses exposed to low levels of anticancer drug and Ethylene Oxide (EO) gas in a hospital were performed. The frequency of CA was increased in the exposed compared to the controls whereas no increase of the frequency of MN was found. The frequencies of chromatid type CA were 1.2, 3.91 and 9.67 per 500 cells in the controls, workers exposed to anticancer drug and workers exposed to EO, respectively. Lower frequency of CA in nurses handling anticancer drugs with safety covers compared to those without safety covers was observed, but it was not statistically significant. The frequency of CA in nurses handling anticancer drugs increased by the frequency of mixing anticancer drugs. Poisson regression analysis showed a significant association of the frequency of chromatid type CA with age, duration of work, exposure to anticancer drug and EO gas exposure, but no association of the frequency of chromosome type CA with any variables. The results suggested that there were associations between CA and the occupational exposure to low levels of anticancer drug and EO gas.
전혜정(Hye Jeong Jeon),김기중(Ki Joong Kim),고태성(Tae Sung Ko),김동욱(Dong Wook Kim),황용승(Yong seung Hwang) 대한소아신경학회 1993 대한소아신경학회지 Vol.1 No.1
Tuberculous mentingitis is the major cause of death in childhood tuberculosis, and early diagnosis and treatment are important prognositic factors. Hydrocephlus is common and serious cpmplication that affect the neurologic outcome. In the management of hydrocephalus, instead of ventriculo-peritioneal shunt(VPS)after clinical improvement with only antituberculous chemotherapy, early decompression of increased intracranial pressure by extraventricular drainage(EVD) makes rapid recovery of mental or clinical status and decreases incidence of VPS and improves prognosis. We did EVD in 19 patients of severs hydrocephalus or altered mentality due to hydrocephalus among 59 tuberculous meningitis patients who was admitted to Pediatric Department of SNUCH from March, 1987 to March, 1992. Thirteen Patients who didn't have hydrocephalus were excluded and we studied with 46 patients. During 48 hours after EVD, headache, vomiting, seizure, fever and abnormal neurologic finding improved about half of the patients. For evaluating and comparing prognosis of EVD or VPS group, we classified 46 patients according to clinical stage1,2,3. In 6 patients of clinical stagel, EVD was not done. In 21 patients of clinical stage2, outcomes were as followed. In VPS group after EVD(5 patients), one (20%) was improved without neurologic deficit, two(40%) were improved with neurologic deficit and two(40%) were stationary. Two patients of non-VPS after EVD were improved in all cases. In VPS group without EVD(7 patients), two(28.6%) were improved without neurologic deficit, four(51.7%) were stationary and one(14.3%) was aggravated. In conservative therapy group(7 patients), five(71.4%)were improved without neurologic deficit, one(14.3%) was stationary and one(14.3%) died. In 19 patients of clinical stage3, early EVD were done in all VPS group. There is no statistical significance in comparing these groups because of small patients numbers and selection bias among these groups. But clinical outcomes suggest that early EVD helps to improve the prognosis of severe hydrocephalic patients with tuberculous meningitis.