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임용성(Yong Seong Lim),유창달(Chang Dal Yoo),이은봉(Eun Bong Lee),송영욱(Yeong Wook Song),백한주(Han Ju Paik) 대한내과학회 1996 대한내과학회지 Vol.51 No.4
Calcium pyrophosphate dihydrate (CPPD) deposition disease has various patterns of clinical manifestation ranging from an absence of symptoms to a severely dertructive arthropathy. The occurrence of CPPD deposition disease at the tempormandibular joint accompanied by mass formation around the joint is very rare, with only 5 previous reports worldwide. Our report points out the importance of considering pathologic entities other than parotid tumor and osteogenic neoplasm in the differential diagnosis of a preauricular mass. We report a case of CPPD deposition disease at and around the tempormandibular joint diagnosed by polarized microscopic examination of surgical specimen.
현저한 후복막강내 임파절 종대를 보인 아급성 괴사성 임파선염 1 예
경춘숙(Choon Suk Kyeong),김안나(An Na Kim),김성용(Seong Yong Kim),임용성(Yong Seong Lim),임선희(Seon Hee Lim),이계회(Kye Heui Lee),최상전(Sang Jeon Choi),손인(In Son),박성훈(Seong Hoon Park),유병욱(Byeong Uk You),박경주(Kyung Joo Pa 대한내과학회 1991 대한내과학회지 Vol.41 No.6
Subacute necrotizing lymphadenitis is a self-limiting lymphadenitis that could be misdiagnosed as malignant lymphoma both clinically and histologically. It was initially reported by Kikuchi in 1972, but its etiology is still unknown. It mainly affects young women and usually manifests as moderate fever and lymphadenopathy with or without local pain. The lymphadenopathy appears most commonly in the neck, and lymphadenopathy in sites other than cervical lesions or, generalized lymphadenopathy is less common. Histologcally, the involved lymph nodes are characterized by a well-circumscribed necrotic area, varying degrees of nodal architectural loss, abundant karyorrhectic nuclear debris, infiltrations of large lymphoid cells, histiocytes, and macrophages phagocytosing nuclear debris, and the absence of a significant number of plasma cells and neutrophils. Recently we experienced a rare case of subacute necrotizing lymphadenitis that showed prominent enlargement of the multiple retroperitoneal lymph nodes in a 17-years-old man.
혈청 제4형 콜라겐 7S Domain 측정에 의한 만성 간염의 섬유화 정도 예측
이계희(Kye Heui Lee),박성훈(Seong Hoon Park),최신은(Shin Eun Choi),김안나(An Na Kim),김성용(sung Yong Kim),임선희(Sun Hee Lim),임용성(Yong Sung Lim),손인(In Son) 대한소화기학회 1993 대한소화기학회지 Vol.25 No.2
N/A The degree of fibrosis is a major prognostic factor in chronic liver disease. Although liver biopsy is essential to assess the degree of fibrosis, a more simple diagnostic method would be helpful for its invasive nature. Type IV collagen is one of major constituents of basement membrane and serum collagen IV-7S level reflects the degree of fibrosis. To evaluate the usefulness of serum collagen IV-7S in assessing the state of hepatic fibrosis, we compared the level of serum collagen IV-7S in various liver diseases and normal volunteers. The normal value of the serum collagen IV-7S was 3.6+- 1.2 ng/ml. There was no statistically significant difference in serum collagen IV-7S levels among the group of acute hepatitis, fatty liver, chronic persistent hepatitis and the normal controls. And there was no significant difference between the group of chronic active hepatitis and liver cirrhosis, either. But the level of serum collagen IV-7S of the group of chronic active hepatitis and liver cirrhosis was significantly higher than that of the group of acute viral hepatitis, fatty liver and chronic persistent hepatitis. These results suggest that the measurement of serum collagen IV-7S is a valuable aid for evaluating the state of fibrrosis in chronic liver disease.
신기철 ( Ki Chul Shin ),한창완 ( Chang Wan Han ),임용성 ( Yong Seong Lim ),송영욱 ( Yeong Wook Song ) 대한류마티스학회 1998 대한류마티스학회지 Vol.5 No.2
Orbtial myositis is an idiopathic, nonspecific inflammation of primarily one or more extraocular muscles and is considered as a subgroup of orbital pseudotumor. It can be distinguished as acute, subacute or chronic form. Acute orbital myositis is a single episode of orbital pain without fever lasting less than 6 weeks, whereas subacute or chronic form is a persistent episode lasting more than 2 months or with recurrence. The diagnosis is made by CT scan, ultrasonography or MRI, which is characterized by enlargement of extraocular muscle bellies and tendons. Although spontaneous resolution may be anticipated within 3 to 6 weeks, good treatment response is shown with corticosteroids. We recently experienced a case of orbital myositis in a 50 year-old female. She had bilateral orbital swelling 1 year prior to admission. Orbital swelling was relieved gradually but relapsed to show limitations of extraocular muscle movement. In orbit CT scan, there was diffuse thickening of eyeball muscle and swelling of facial subcutis. She was treated with methylprednisolone with marked clinical improvement after 4 days. After 1 month period of corticosteroid treatment, she had residual limitation of upward eyeball movement. We present this case with literature reviews.
경골 결절부의 통풍성 결절 및 동반된 경골 상부 국한성 연조직염
정재천 ( Jae Cheon Jeong ),박창하 ( Chang Ha Park ),조한균 ( Han Kyun Cho ),최성식 ( Sung Sik Choi ),서명덕 ( Myung Deok Seo ),임용성 ( Yong Seong Lim ),송영욱 ( Yeong Wook Song ) 대한류마티스학회 2004 대한류마티스학회지 Vol.11 No.2
Gout is characterized by hyperuricemia and recurrent attacks of acute arthritis. Gout is a clinical syndrome resulting from the deposition of urate (monosodium urate monohydrate) crystals. Urate deposition occurs in articular cartilage, subchondral bone, synovial membrane, joint capsule and periarticular tissues, with articular cartilage being especially susceptible. The first metatarsophalangeal joint is commonly involved at presentation and other commonly affected joints are the ankle, knee and tarsal area. Gouty tophus located on the tibial tuberosity has never been reported in korea. We report a case of gouty tophus on the tibial tuberosity with (chemical) cellulitis occurred at the upper tibial area in a 46-year-old man.
백한주(Han Joo Baek),이은봉(Eun Bong Lee),유창달(Chang Dal Yoo),김현아(Hyun An Kim),송영욱(Yeong Wook Song),임용성(Yong Seong Lim) 대한내과학회 1997 대한내과학회지 Vol.52 No.6
Objectives: The aim of this study is to enhance understanding the clinical features, pathogenesis, diagnosis and treatment of gouty arthritis in Korea by analyzing the clinical manifestations of the patients with urate crystal-proven gouty arthritis. Methods: 78 cases who had been diagnosed as gouty arthritis by confirming the urate crystals in synovial fluids or tophi in Seoul National University Hospital between January 1, 1989 and July 31, 1995 were analysed for their histories, symptoms, signs, laboratory data, and X-ray findings. Results: 1) Male to female ratio was 18.5:1. The mean age of onset is 49.3±14.5 years(range 11-83 years); the mean duration of disease 6.5±7.0 years(range 0-30 years); the mean duration of gouty attack 7.2±5.5 days(range 1-30 days). 2) The frequent precipitating factors of gouty arthritis were hospitalization(37%) and alcohol drinking(15%). The most frequent accompanying disease was hypertension(24%). Obesity, diabetes, chronic renal failure, hyperlipidemia, ischemic heart diseases, or cerebrovascular diseases were also accompanied by gouty arthritis. 3) The patterns of joint involvement were devided into 3 groups: monoarthritis; 42%, oligoarthritis; 35%, polyarthritis; 23%, The most frequent site of the first gouty attack was the 1st toe(65%). The most frequently involved joint at gouty attack was also the 1st toe(68%). While only lower extremities were involved in most cases with monoarthritis and oligoarthritis(91% and 78%, respectively), both lower and upper extremities were involved in most cases with polyarthritis(78%). 4) Hyperuricemia was found in 74% of the cases at gouty attack. But serum uric acid level was normal in 26%. With respect to pathogenesis of hyperuricemia, 14% of the cases had uric acid overproduction and 86% had uric acid underexcretion. 5) Bony changes in radiologic findings were found in 47% of the cases and tophi in 33%. Bony changes and tophi was significantly related to the younger age of gouty onset and higher serum uric acid level at gouty attack. 6) Acute gouty arthritis responded well to colchicine and NSAIDs. There was no difference in efficacy and the frequency of side effects between them. Conclusion: The clinical features of the gouty arthritis in Korea showed no difference from those in foreign studies except higher prevalence of oligo-/polyarthritis and tophi. To be remarkable, 26% of the patients with gouty arthritis did not have hyperuricemia at gouty attack. This finding indicates that urate crystals should be confirmed by synovial fluid examination for diagnosis of gouty arthritis.
피부근염에서 발생한 자연 기종적증과 피하기종 증례 보고 및 국외 보고 증례들의 임상상에 대한 분석
오주현(Ju Hyeon Oh),고재중(Jae Jung Ko),이창균(Chang Kyun Lee),고영회(Young Hee Ko),윤구섭(Ku Sud Yun),임용성(Yong Seong Lim),송영욱(Yeong Wook Song) 대한내과학회 1998 대한내과학회지 Vol.55 No.1
Spontaneous pneumomediastnum is a very rare complication of systemic autoimmune diseases, The precise mechanism of pneumomediastinum in dermatomyositis is not well known. Pulmonary alveoli rupture secondary to interstitial pneumonitis or pulmonary infarctions consequent upon vasculitis are the suggested mechanisms, Among the idiopathic inflammatory myopathies, dermatomyositis and polymyositis show similar clinical manifestations except skin lesions. But pneumomediastinum occurs exclusively in cases with dermatomyositis, not in case with polymyositis. In a literature review, patients with dermatomyositis and pneumomediastinum had some characteristic features. As compared with dermatomyositis without pneumomediastinum, CK level was normal in about half and concomitance of interstitial lung disease and cutaneous vasculitis were very frequent. We experienced a case of dermatomyositis with spontaneous pneumomediastinum and subcutaneous emphysema, Thus we report that with a review of the literature and analysis of reported cases.
박란영 ( Ran Young Park ),남수연 ( Su Youn Nam ),이지현 ( Ji Hyun Lee ),이창수 ( Chang Soo Lee ),정의준 ( Euh Jun Jeong ),임용성 ( Yong Seong Lim ),송영욱 ( Yeong Wook Song ) 대한류마티스학회 2002 대한류마티스학회지 Vol.9 No.4
Most cases of the popliteal cyst rupture in rheumatic diseases have been reported in patients with rheumatoid arthritis. A ruptured popliteal cyst is unusual in other diseases, especially in gouty arthritis. The clinical presentations of a ruptured popliteal cyst may include pain, swelling, tenderness and erythema of the calf, and mimic deep vein thrombophlebitis. It is therapeutically important to differentiate ruptured popliteal cyst from deep vein thrombophlebitis. A ruptured popliteal cyst in gouty arthritis has never been reported in Korea. We would like to report one case of the ruptured popliteal cyst into the calf in gouty arthritis mimicking deep vein thrombophlebitis.
류마티스 관절염에서 간침범을 동반한 이차성 유전분증 -메토트렉세이트와 저용량 스테로이드에 의해 호전된 증례의 보고-
한윤주 ( Yoon Ju Han ),송찬호 ( Chan Ho Song ),신동혁 ( Dong Hyuk Sheen ),양상석 ( Sang Seok Yang ),이지연 ( Jee Youn Lee ),임용성 ( Yong Seong Lim ),송영욱 ( Yeong Wook Song ) 대한류마티스학회 2000 대한류마티스학회지 Vol.7 No.3
Amyloidosis is a heterogenous group of often fatal disorders characterized by extracellular deposition of a proteinaceous material with a unique fibrillar form in various tissues and organs. Presenting with severe hepatomegaly, a 46 year-old man who has suffered with rheumatoid arthritis lasting more than 12 years was confirmed to have secondary amyloidosis by liver biopsy. After treatment with methotrexate and low dose prednisolone, we have observed clinical improvement in which hepatomegaly was resolved remarkably. This is the first published case report of a patient with rhuematoid arthritis complicated by liver amyloidosis which partially regressed after treatment with methotrexate and prednisolone.
백한주(Han Joo Baek),이은봉(Eun Bong Lee),유창달(Chang Dal You),허대석(Dae Seog Heo),송영욱(Yeong Wook Song),임용성(Yong Seong Lim) 대한내과학회 1998 대한내과학회지 Vol.54 No.2
Rheumatic manifestations in non-Hodgkin's lymphoma (NHL) are common but actual arthritis as a presenting feature appears to he very rare. We experienced a case of NIK, presenting as polyarthritis in a 24-year-old woman. Eight months ago she was admitted to the hospital due to polyarthritis and skin rash. She had pleural and pericardial effusion. Antinuclear antibody was positive and rheumatoid factor was negative. Joint X-ray showed periarticular osteopenia at both knees, wrists, hands and feet. Prednisolone, salsalate and anti-tuberculosis drugs were administered under the impression of either probable lupus or rheumatoid arthritis and pleural tuberculosis. After then pleuropericardial effusion and skin rash improved. But polyarthralgia persisted and she developed right cervical lymphadenopathy. On her second admission she was found to have a round mass in left lower lung field and multiple mediastinal lymph node enlargement. Cervical lymph node biopsy revealed non-Hodgkin's lymphoma. She received 8 cycles of systemic chemotherapy until 1996 July. NHL was remitted completely and polyarthralgia disappeared. We report a case of non-Hodgkin's lymphoma presenting as polyarthritis and literatures are reviewed.