http://chineseinput.net/에서 pinyin(병음)방식으로 중국어를 변환할 수 있습니다.
변환된 중국어를 복사하여 사용하시면 됩니다.
김진휘(Jin Hwi Kim),구양서(Yang Suh Koo),정종익(Jong Ik Jeong),정상용(Sang Yong Jeong),권덕호(Duk Ho Kwun),신동우(Dong Woo Shin),한병철(Byung Chul Hahn),서동진(Dong Jin Suh) 대한내과학회 2000 대한내과학회지 Vol.59 No.1
Rotor syndrome is a rare benign familial disorder characterized by chronic, fluctuating, nonhemolytic and predominantly conjugated hyperbilirubinemia with normal liver tissue. In contrast to Dubin-Johnson syndrome, there is no liver hyperpigmentation in Rotor syndrome, and BSP clearance does not show a secondary retention peak. The serum bilirubin in patients with Gilbert's syndrome is almost all unconjugated in contrast to Rotor syndrome. A 29-year-old male was admitted due to persistent jaundice. Physical examination revealed icteric sclera without hepatosplenomegaly. Laboratory findings showed increased serum bilirubin with indirect bilirubin predominance. Urinary excretion of total coproporphyrin was markedly elevated, and coproporphyrin Ⅰ was 66% of total urinary coproporphyrin. Oral cholecystography showed well visualized the gallbladder, but 99mTc-DISIDA scan showed markedly decreased hepatic uptake and poor visualization of the gallbladder and biliary tract. Histology of the liver showed no abnormal finding. We report the case with the review of literature.(Korean J Med 59:109-113, 2000)
송치욱(Chi Wook song),구양서(Yang Suh Koo),이홍식(Hong Sik Lee),이상우(Sang Woo Lee),최재현(Jai Hyun Choi),김창덕(Chang Duck Kim),류호상(Ho Sang Ryu),현진해(Jin Hai Hyum) 대한소화기학회 1995 대한소화기학회지 Vol.27 No.4
N/A Background/Aims: Recently the esophagus is considered a major source of recurrent noncardiac chest pain to patients in whom exercise stress test and/or cardiac catheterization have excluded a cardiac etiology. To investigate the esophageal origin of noncardiac chest pain, esophageal motility tests including manometry, provocation test, and radioisotope esophahgeal transit study(RETS) were studied in patients with noncardiac chest pain. Methods: A total of l26 patients with noncardiac chest pain were assessed;they included 41 patients with normal coronary angiogram and 85 patients with normal noninvasive cardiac tests such as echocardiogram and exercise stress test done in Korea University Hospital from Feb. l993 to Aug. 1994. Results: 56 out of 126 patients(44.4%) with noncardiac chest pain had abnormal manometric findings which included 20(35.7%) nonspecific esophageal motility disorder, 17(30.4%) hypertensive lower esophageal sphincter, 9(16.1%) hypo- tensive lower esophageal sphincter, and 2(3.6%) nutcracker esophagus. Thirty eight out of 126(30.1 %) patients had abnormal manometric findings but no reproducible chest pain by provocation test and were considered to have a probable esophageal chest pain. When patients having positives for both provocation tests are counted as a single positive, 39 out of l26(3l /o) patients had their chest pain reproduced and were considered to have a defini(e esophageal chest pain. The combination of patients with definite esophageal chest pain(31%) and probable(30.17c) gave an overall diagnostic yield of 61.1% for our esophageal laboratory. There was no significant difference between invasive cardiac test group and noninvasive cardiac test group in the results of esophageal motility tests. RETS merely reflected the peristaltic abnonnalities with no more informations for esophageal chest pain. Conclusions: These results reveal that esophagus is considered a source of noncardiac chest pain in 61.1%. Provocation test complements esophageal manometry alone and increases diagnostic yield. RETS can be used in diagnosis of noncardiac chest pain accompanied by peristaltic abnormality of the esophagus. (Korean J Gastroenterol 1995;27:381-387)
백세현(Sei Hyun Baik),구양서(Yang Suh Koo),김상진(Sang Jin Kim),심완주(Wan Joo Shim),최동섭(Dong Seop Choi),김인선(In Sun Kim),정희진(Hee Jin Jeong) 대한내과학회 1992 대한내과학회지 Vol.43 No.2
A POEMS syndrome is a rare diaease of which main clinical characteristics are polyneuropathy, organomegaly, endocrinopathy, M proteins and skin changes. Although the proliferation of plasma cell is considered to do a pathogenetic role, the definite etiology and pathogenesis is still unclear. A 47years old woman who has been treated for valvular heart disease admitted to the hospital because of low extremity pain, walking disturbance, aggravation of exertional dyspnea and abdominal distention. She also complained of the anterior neck swelling and dark discoloration of skin. She had been suffered from diabetes mellitus for 5months. Inspite of repeated centesis of ascitic and pleural fluid with medical freatment for heart tailure, and administration of insulin and thyroid hormone for DM and hypothyroidism, dyspnia and abdominal distention did not improved. On the tenth day of admission, 2×2 cm sized palpable axillary lymph node biopsy was done and prednisolone was prescribed under the impression of POEMS syndrome. The findings of lymph node biopsy and bone marrow biopsy which was done 6weeks later was compatible with POKMS syndrome. In bone mar- row biopsy, most plasma cells which slightly increased in proportion were positive for IgA λ on immunohistochemical stain. There was a dramatic improvement of low extremity pain, edema, skin lesions and other symptoms after 10days use of prednisolone. But blood sugar level fluctuated although splitted doses of insulin were applied. General condition of the patient was improved continuosly, so she discharged with well being sense. We exprienced a case of POEMS syndrome in a 47years woman who has all major characteristics of the syndrome. We report this case with a review of literatures.
반복성 기흉 (氣胸) 을 유발한 원발성 폐 (肺) 조직구증 - X
강세용(Sei Yong Kang),구양서(Yang Suh Koo),인광호(Kwang Ho In),강경호(Kyung Ho Kang),유세화(Se Hwa Yoo) 대한내과학회 1992 대한내과학회지 Vol.43 No.1
Pulmonary histiocytosis X can be associated with disseminated histiocytosis X, but isolated case in the lung parenchyme is rare. We report a case of primary pulmonary histiocytosis X with recurrent pneumothoraces. A 36-year-old man was referred because of recurrent pneumothorax. He had been suffered from dry cough and exertional dyspnea for 4 years. He was a heavy smoker. Plain chest X-ray and chest CT scan revealed thin-walled cysts of various sizes in both lungs. Open lung biopsy was performed. Light microscopic examination revealed proliferation arid infiltration of Langerhans'cells. Immunohistochemically, Langerhans`cells showed strong cytoplasmic staining with S-100 protein and electronmicroscopic examination showed Birbeck granules in Langerhans`cell. He was treated with bleb resection and pleurodesis, but pneumothorax recurred 1 month later.
이구(Goo Lee),조은래(Eun Rae Jo),구양서(Yang Suh Koo),이홍식(Hong Sik Lee),이상우(Sang Woo Lee),김창덕(Chang Duck Kim),류호상(Ho Sang Ryu),현진해(Jin Hae Hyun) 대한소화기학회 1994 대한소화기학회지 Vol.26 No.5
Carcinoma of the extrahepatic bile duct,s may be classified as papillary, nodular, scirrhous constricting and diffusely infiltrating types according to their rnacroscopic characteristics. Among these, the papillary carcinomas are polypoid lesions that grow exophytically into the duct lumen and often produce duct obstruction before they invade the wall of the duct. For this reason, they are more favorable than the other forms and offer the greatest chance of cu- rative resection. Hence we report two cases of papillary adenocarcinoma of extrahepatic bile ducts for which curative surgery was performed successfully. (Korean J Gastroenterol 1994; 879 884)
Endovascular stent 로 치료한 간농양에 합병된 감염성 복부 대동맥류 1 예
김성권(Sung Gwon Kim),박동균(Dong Kyun Park),구양서(Yang Suh Koo),강동훈(Dong Hoon Kang),최덕주(Duck Joo Choi),박현철(Hyun Chul Park),김주현(Ju Hyun Kim),손지원(Ji Won Son),신익균(Ik Kyun Shin) 대한내과학회 2001 대한내과학회지 Vol.61 No.2
A 72-year-old diabetic male patient with high grade fever, right upper quadrant abdominal pain and Klebsiella pneumoniae septicemia is reported. He suffered from high fever and abdominal pain in spite of aspiration of liver abscess and antibiotic treatment. A few days later, we found a palpable pulsating abdominal mass on physical examination. Computed tomography and angiography revealed infected abdominal aortic aneurysm associated with pyogenic liver abscess. He was treated by antibiotics and Endovascular stent without surgical resection. He improved without complications and has been followed-up after discharge with excellent condition. To our knowledge, this is the first case of infected abdominal aortic aneurysm as a septic metastatic lesion secondary to liver abscess.(Korean J Med 61:151-155, 2001)
한국인에서 Mitochondrial Aldehyde Dehydrogenase ( ALDH2 ) 의 유전적 결핍이 알코올성 간질환 발생에 미치는 영향
변관수(Kwan Soo Byun),권소영(So Young Kwon),박상훈(Sang Hoon Park),구양서(Yang Suh Koo),연종은(Jong Eun Yeon),김재선(Jae Seon Kim),박영태(Young Tae Bak),김진호(Jin Ho Kim),김종극(Jong Guk Kim),이창홍(Chang Hong Lee) 대한내과학회 1993 대한내과학회지 Vol.45 No.3
Background: Deficiency of mitochondrial aldehyde dehydrogenase (ALDH2) is an inborn error of metabolism that is responsible for acute alcohol sensitivity (flushing response) observed only in Orientals of Mongoloid origin. The subjects with the mutant ALDH2 gene are at much lower risk than homozygotes of normal ALDH2 genes for alcoholic liver disease presumably because of their sensitivity to alcohol. However, the role of the mutant ALDH2 gene in the development of alcoholic liver disease had not yet been we11 analyzed. In this study, genotypes of ALDH2 were compared between normal controls and patients with alcoholic liver disease to clarify the role of ALDH2 deficiency in the development of alcoholic liver disease. Method: Genotyping of ALDH2 was performed in 33 normal controls and 30 patients with alcoholic liver disease using the polymerase chain reaction and Southern blot hybridization by allele-specific oligonucleotide probes. Result: In 33 normal controls, 19 cases (57.6%) were homozygotic for the normal ALDH2 gene, 13 cases (39.4%) were heterozygotic for the normal and mutant ALDH2 genes and 1 caw (3.0%) was homozygotic for the mutant ALDH2 gene. All normal controls who had the mutant ALDH2 gene experienced facial flushing response after drinking. Amount of alcohol intake each time in controls who had the mutant ALDH2 gene was much smaller than that in normal ALDH2 homozygotes (p<0.001). All patients with alcoholic liver disease were homozygotic for the normal ALOH2 gene. The frequency of ALDH2 deficiency in patients with alcoholic liver disease was significantly lower than that in normal controls (p<0.001). Conclusion: These results suggest that ALDH2 deficiency is one of the important genetic factors in regulating alcohol consumption and plays a protective role against alcoholism and alcoholic liver diseases.
포스터 전시 : 간 15 ; 만성 간질환에서 혈중 gelatinase (Matrix metalloproteinase-2와 9)의 측정 의의
권오상 ( Oh Sang Kwon ),정혁상 ( Hyuk Sang Chung ),주기탁 ( Ki Tak Ju ),정문기 ( Moon Gi Chung ),박동균 ( Dong Kyun Park ),김선숙 ( Sun Suk Kim ),김연석 ( Yeon Suk Kim ),구양서 ( Yang Suh Koo ),김유경 ( Yu Kyung Kim ),최덕주 ( Duc 대한소화기학회 2002 대한소화기학회 추계학술대회 Vol.2002 No.-
신미경,정상용,신재욱,신동우,구양서,김진휘,천정현,정종익,권덕호 대한소화기학회 1999 대한소화기학회지 Vol.34 No.6
Multiple lymphomatous polyposis (MLP) is a rare type of malignant gastrointestinal lymphoma characterized by multiple polyps involving long segments of the gastrointestinal tract. The malignant cells of MLP share morphological, immunohistologic and cytogenetic similarity with cells of nodal- based mantle cell lymphoma. A few cases of synchronous with metachronous primary gastric lymphoma and adenocarcinoma were reported. However, we could not find any case of synchronous with metachronous MLP and gastric adenocarcinoma. We report a case of MLP involving various segments of gastrointestinal tract and synchronous gastric adenocarcinoma observed in a 78-year-old woman who complained of epigastric pain and indigestion.