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뇌척수액 신경잔섬유 가벼운사슬의 호전을 보이는 성인 척수근위축증 3a형 증례: 실사용 근거
고판우,이종목 대한신경과학회 2024 대한신경과학회지 Vol.42 No.1
A 38-year-old male was diagnosed with spinal muscular atrophy (SMA) type 3a, previously misdiagnosed as muscular dystrophy. He began treatment with nusinersen after getting approval from health insurance service. Cerebrospinal fluid (CSF) was collected when nusinersen was intrathecally injected. We measured the neurofilament light chain (NfL) level using a single molecular array as an efficacy biomarker. The CSF NfL level was markedly decreased after finishing the loading dosage. Our case implies that nusinersen is also effective in adults with SMA as a biomarker from real-world evidence.
ChatGPT가 한국 신경과 의사들에게 실제 임상에서 유용할까?
고판우 대한신경과학회 2024 대한신경과학회지 Vol.42 No.3
Background: Since the emergence of artificial intelligence (AI), such as ChatGPT, there has been extensive research on its utility in the medical field. This study evaluates the potential of utilizing the ChatGPT AI platform to provide specialized advice to Korean neurologists. Methods: Through a multifaceted approach, it assesses both the knowledge and practical clinical utility using neurology training evaluation questions and clinical case reports. Results: The accuracy of ChatGPT in answering medical exam questions (45.1%) is comparable to or slightly lower than previous studies. The study also examines performance of ChatGPT in providing advice based on clinical case reports, finding that while it can offer suitable diagnostic suggestions and propose relevant tests in some cases (8/12), its overall diagnostic accuracy is limited (2/12). Limitations include the platform’s text-based nature, which hinders the interpretation of image-based questions, and the uneven distribution of case reports across subfields. Conclusions: Despite these limitations, ongoing advancements in AI technology offer prospects for improved performance and expanded applications in the medical field, warranting continued research and monitoring of AI’s role in medicine.
오랜 기간 완전완화 후 말초신경병증으로 재발한 신경림프종증
황준현,고판우,서안나,채종민,강병욱,이재혁,서정규,송현석 대한임상신경생리학회 2011 Annals of Clinical Neurophysiology Vol.13 No.2
Neurolymphomatosis, an uncommon manifestation of non-Hodgkin’s lymphoma, is lymphomatous infiltration of peripheral nerves. We confirmed the diagnosis of neurolymphomatosis in a 75-year old woman with a history of complete remission of diffuse large B cell type lymphoma on the nasal cavity seven years ago. She complained of painful weakness of left leg and took the electrophysiologic study, extremity ultrasonography, fluorodeoxyglucose PET-CT, and extremity MRI serially. She was diagnosed as neurolymphomatosis by targeted posterior tibial nerve mass biopsy.
Vestibular Rehabilitation in Central Dizziness
한병인,고판우,이호원,김현아,이형 대한평형의학회 2015 Research in Vestibular Science Vol.14 No.4
Vestibular rehabilitation therapy (VRT) is an exercise-based treatment program designed to promote vestibular adaptive and compensatory mechanisms already existing in the human brain. Although the evidence is sparse for improvement in subjects with central vestibular dysfunction following VRT, it improves postural stability in cerebellar diseases and reduces subjective complaints and fall risk in Parkinson disease. Possible mechanisms of recovery after central nervous system lesions may include neural sprouting, vicarious functions, functional reorganization, substitution, and plasticity. VRT regimens for patients with central causes should include balance and gait training, general strengthening and flexibility exercises, utilization of somatosensory and vision and utilization of alternate motor control strategies. VRT would be an option to relieve the symp-toms of the many patients who have central dizziness.Res Vestib Sci 2015;14(4):97-100
Asymmetric and Upper Body Parkinsonism in Patients with Idiopathic Normal-Pressure Hydrocephalus
강경훈,전지수,김태영,최동호,고판우,황성규,이호원 대한신경과학회 2016 Journal of Clinical Neurology Vol.12 No.4
Background and Purpose Our aims were to analyze the characteristics of parkinsonian features and to characterize changes in parkinsonian motor symptoms before and after the cerebrospinal fluid tap test (CSFTT) in idiopathic normal-pressure hydrocephalus (INPH) patients. Methods INPH subjects were selected in consecutive order from a prospectively enrolled INPH registry. Fifty-five INPH patients (37 males) having a positive response to the CSFTT constituted the final sample for analysis. The mean age was 73.7±4.7 years. The pre-tap mean Unified Parkinson’s Disease Rating Scale motor (UPDRS-III) score was 24.5±10.2. Results There was no significant difference between the upper and lower body UPDRS-III scores (p=0.174). The parkinsonian signs were asymmetrical in 32 of 55 patients (58.2%). At baseline, the Timed Up and Go Test and 10-meter walking test scores were positively correlat¬ed with the total motor score, global bradykinesia score, global rigidity score, upper body score, lower body score, and postural instability/gait difficulties score of UPDRS-III. After the CS¬FTT, the total motor score, global bradykinesia score, upper body score, and lower body score of UPDRS-III significantly improved (p<0.01). There was a significant decrease in the num¬ber of patients with asymmetric parkinsonism (p<0.05). Conclusions In the differential diagnosis of elderly patients presenting with asymmetric and upper body parkinsonism, we need to consider a diagnosis of INPH. The association be¬tween gait function and parkinsonism severity suggests the involvement of similar circuits producing gait and parkinsonian symptoms in INPH.