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수술로 호전되지 않은 췌장 농양을 내시경 치료로 완치한 1 예
서희영;전태주;김선영;강미선;허란;박지영;서동대;오태훈 인제대학교 백병원 2011 仁濟醫學 Vol.32 No.-
Necrotizing pancreatitis develops in about 10-20% of patients with acute pancreatitis, and pancreatic abscesses develop in 3% of them. The mortality of pancreatic abscess has been reported up to 40% in one study. Recently, there are several reports that show good results with n on-surgical therapy, such as percutaneous drainage and endoscopic drainage, but if the non-surgical drainage fails, surgical therapy are recommended. However, there is no definite therapeutic method which is suggested yet so far after the failure of the surgical drainage. So we report the case in which we experienced successful treatment of pancreatic abscess by endoscopic removal of necrotic tissue through the gastrocystostomy, after the failure of the surgical debridement and internal drainage through gastrocystostomy.
소원섭,이지연,강희라,손원진,허승덕 대구대학교 특수교육재활과학연구소 2012 再活科學硏究 Vol.30 No.1
이 연구는 이학적·청각학적 정상 소견을 가진 성인들의 다중주파수 고막운동도(multi-frequency tympanogram, MFT)와 다중성분 고막운동도(multi-component tympanogram, MCT)의 특성을 알아보고자 하였다. 연구 참여자는 D대학교 재학 중인 19명(M:F=9:10, 만 19∼23세)으로 하였다. MCT는 각 성분(admittance; Y, susceptance; B, conductance; G)별 정점의 수를 확인하였고, MFT는 200 ㎐부터 2 ㎑ 순음에 대한 고막 긴장 및 이완상태에서 전도율을 통해 공명주파수와 ΔB, Δ∅를 각각 구하였다. MCT는 668 ㎐ 자극에 대해 47.4 %가 1Y1B1G를, 52.6 %가1Y3B1G를 보였고, MFT의 공명주파수는 829~1,213(1,021±192) ㎐, ΔB와 Δ∅의 평균은 각각 –0.18, -19.3으로 관 찰되었다. This study will be to confirm the characteristic of Multi-component tympanogram(MCT) and Multi-frequency tympanogram(MFT) of adults who have physical and audiological normal findings. Participants were 19 students(M:F = 9:10) who are attending D-university. MCT checked the number of peaks per each component(admittance; Y, susceptance; B, conductance; G) and MFT got the resonance frequency through the conductivity rate of tympanic membrane's tense and relaxation state, and ΔB, Δ∅ respectively. 47.4% of MCT showed 1Y1B1G about 668 ㎐ stimulus and 52.6% of that showed 1Y3B1G. Resonance frequency of MFT was 829~1,213(1,021±192) ㎐, and the average of ΔB and Δ∅ was observed -0.18, -19.3 respectively.
강미선;박상훈;박지영 서희영;허란;김상현 인제대학교 백병원 2011 仁濟醫學 Vol.32 No.-
Acute fatty liver of pregnancy (AFLP) was first described as a specific clinical entity in 1940 and thought to be universally fatal. Maternal mortality in the past approached 75 percent. However early diagnosis and prompt delivery have dramatically improved the prognosis, and maternal mortality rate is now less than 18 percent. A early diagnosis, a prompt delivery, and a intensive supportive care have improved maternal and perinatal outcome. We report a 30—year—old woman at 37 weeks gestation who have multiple complications including acute pancreatitis in AFLP. She was complicated with acute renal failure, disseminated intravascular coagulation, duodenal ulcer bleeding, spontaneous bacterial peritonitis, pulmonary edema and acute pancreatitis.
Genetic mutations and clinicopathological correlation in Korean melanoma - preliminary study
( Ji Hye Heo ),( Seon Bok Lee ),( Hee Seong Yoon ),( Si Hyub Lee ),( Jeonghyun Shin ),( Gwang Seong Choi ),( Ji Won Byun ) 대한피부과학회 2019 대한피부과학회 학술발표대회집 Vol.71 No.2
Background: Recently, identifying individual mutated genes in cutaneous melanoma have emerged as effective biomarkers and therapeutic targets. Next-generation sequencing (NGS) shows comprehensive genomic mutations with high sensitivity. Objectives: We assessed the genetic alteration in patients with melanoma and their prognosis. Methods: We analyzed clinicopathological features of 11 patients with melanoma who obtained surgical resection and examined genetic mutations using NGS. Results: Among 11 cases of melanoma, gene mutations were identified in five. Case #1 presented lentigo maligna melanoma with vertical growth pattern on the neck. NGS identified CCND1 amplification and TP53 mutation. No recurrence was observed for 21 months without adjuvant treatment. Case #2 showed acral lentiginous melanoma (ALM) on the foot. NRAS mutation was identified, and metastasis to lymph nodes and lung occurred 8 months after surgery. After eighteenth anti-PD1 therapy, the treatment was changed to dacarbazine due to disease progression. Case #3 presented ALM on the great toe and case #4 presented nodular melanoma on the heel. NGS confirmed RAF1 amplification and KRAS mutation, and FGFR1 amplification and PTEN deletion, respectively. In case #5, tumorigenic phase of ALM developed on the sole and KIT gain was found. There is no recurrence after surgery in case #3 and #5. Conclusion: Further studies are needed to analyze the factors affecting therapeutic outcome including genetic mutations and target therapy.
A Case of Immunoglobulin A Pemphigus: Intraepidermal Neutrophilic Dermatosis Type
( Ji Hye Heo ),( Hee Seong Yoon ),( Si Hyub Lee ),( Seung Dohn Yeom ),( Lucia Kim ),( Soo-chan Kim ),( Ji Won Byun ),( Jeonghyun Shin ),( Gwang Seong Choi ) 대한피부과학회 2019 대한피부과학회지 Vol.57 No.8
Immunoglobulin A (IgA) pemphigus is a rare variant of an autoimmune bullous disease with IgA antibodies. IgA pemphigus is divided into 2 major subtypes: the subcorneal pustular dermatosis (SPD) type and intraepidermal neutrophilic (IEN) dermatosis type. We documented a case of an 18-year-old woman with recurrent generalized blisters and pustules that were especially severe in the intertriginous areas. Some half-and-half blisters and coalesced pustules in an annular pattern with crusts were simultaneously observed. A biopsy specimen from one of the halfand- half blister lesions showed intraepidermal separation with multiple neutrophils. Direct immunofluorescence staining revealed lace-like intercellular deposition of IgA in the entire epidermis. IgA antibody deposits were also observed in the patient's serum. The eruptions cleared with systemic steroids and colchicine 0.6 mg for 1 week, and the patient remained in partial remission at the 8-month follow-up. Herein, we report a case of IEN-type IgA pemphigus, clinically mimicking SPD with half-and-half blisters. (Korean J Dermatol 2019;57(8):492∼495)
A case of spindle cell hemangioma
( Ji Hye Heo ),( Seon Bok Lee ),( Hee Seong Yoon ),( Si Hyub Lee ),( Seung Dohn Yeom ),( Jeonghyun Shin ),( Gwang Seong Choi ),( Ji Won Byun ) 대한피부과학회 2018 대한피부과학회 학술발표대회집 Vol.70 No.1
Spindle cell hamangioma is an uncommon benign vascular tumor. It usually presents as dermal or subcutaneous nodule and most commonly arises in distal extremities. The histopathologic findings are coexistence of dilated and congested cavernous space and more solid area composed of spindle-shaped cells consisting epithelioid type in part. Immunohistochemical findings show variable positivity with endothelial markers depending on the composition of vascular endothelial cells and epithelioid cells in solid area. Surgical excision is treatment of choice and follow-up is necessary because of the possibility of recurrence. We report a case of a 56-year-old woman presented with tender bluish to skin colored mass on the left sole for several months ago. Ultrasound of the lesion revealed an well defined hypoechoic mass at subcutaneous layer with no vascularity. Surgical removal was performed. Histopathologic findings showed dermal tumor composing of spindle cells with cytologic atypia but no mitosis and dilated and thin-walled vascular spaces. There were hemosiderin deposition and collagen dissection. As differential diagnoses, spindle cell hemangioma, Kaposi sarcoma, angiosarcoma, hobnail hemangioma and hemangioendothelioma can be considered. Immunohistochemical stains for CD31, ERG and SMA were positive but CD34 and HHV-8 were negative. Ki-67 was presented approximately 1% positivity. A final diagnosis of spindle cell hemangioma was made.
[P345] A case of pseudovascular squamous cell carcinoma
( Ji Hye Heo ),( Hee Seong Yoon ),( Si Hyub Lee ),( Seung Dohn Yeom ),( Ji Won Byun ),( Gwang Seong Choi ),( Jeonghyun Shin ) 대한피부과학회 2017 대한피부과학회 학술발표대회집 Vol.69 No.1
Pseudovascular squamous cell carcinoma (SCC) is one of the rare variant of acantholytic SCC. It usually arises in sun-exposed sites such as head and neck in middle-aged or elderly patients. The histologic findings are pseudovascular channels lined with neoplastic cells and acantholytic cells moving from squamous nest. Immunohistochemical findings are positivity with monoclonal antibodies to cytokeratin and vimentin and negativity in vascular markers. Mohs micrographic surgery or surgical excision which is available to access the tumor margin is the primary management of high-risk cutaneous SCC. Radiation therapy is also used in cases suspected incomplete surgical removal. We report a case of a 67-year-old man presented with pruritic and painful erythematous grouped papules on the right chin area for two months ago and also in the right oral mucosa where the lesion had started first. Skin biopsy findings showed overlying epidermis permeating down with irregular shaped cellular proliferation, neoplastic cells with pleomorphic nuclei and acantholytic cells in cleft of dilated vessels. Stains for high-molecular weight cytokeratin and p63 were all positive in tumor cells and Ki-67 was presented approximately 10% positivity. It was consistent with pseudovascular SCC. We could not monitor the patient because of failure to follow up. To our best knowledge, this is the first case report on pseudovascular SCC in Korean dermatologic literature.