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가족성 위-식도 미만성 평활근종증을 보인 2대의 Alport 증후군
문송미 ( Song Mi Moon ),장영운 ( Young Woon Chang ),장재영 ( Jae Young Jang ),김윤화 ( Yoon Wha Kim ),김효종 ( Hyo Jong Kim ),김병호 ( Byung Ho Kim ),장린 ( Rin Chang ) 대한내과학회 2010 대한내과학회지 Vol.79 No.2
Diffuse gastroesophageal leiomyomatosis is a rare, benign neoplastic condition characterized by thickening of the esophageal wall as a result ofaberrant smooth muscle proliferation. Gastroesophageal leiomyomatosis may occur in isolation or as a familial disorder and has been associated with other conditions, such as Alport syndrome. Alport syndrome is a hereditary disorder of basement membrane type IV collagen, characterized by progressive nephritis, sensorineural deafness and ocular abnormalities. In this article, we present an interesting case of gastroesophageal leiomyomatosis occurring in a single family in whichthe mother and her son had Alport syndrome. This case is the first report in Korea that gastroesophageal leiomyomatosis is associated with two generations of Alport syndrome. (Korean J Med 79:171-176, 2010)
1개 병원에서 경험한 다제 내성 Acinetobacter baumannii 중추신경계 감염 3예
김은영 ( Eun Yeong Kim ),문송미 ( Song Mi Moon ),김연주 ( Yeon Ju Kim ),박현진 ( Hyun Jin Park ),손준성 ( Jun Seong Son ),이미숙 ( Mi Suk Lee ) 대한내과학회 2011 대한내과학회지 Vol.80 No.1
In recent years, Acinetobacter baumannii has become an increasingly common nosocomial pathogen. It causes rare, but severe, central nervous system (CNS) infection, especially in patients undergoing neurosurgical procedures or with head trauma. Multi-drug-resistant A. baumannii (MDR-AB) has emerged as a pathogen causing CNS infection. We describe A. baumannii CNS infections seen during the last 5 years and focus on MDR-AB CNS infection. Seven patients were admitted to the neurosurgical intensive care unit with serious head injuries. Imipenem-susceptible A. baumannii was identified in all four cases seen from 2003 to 2006, whereas the three cases seen from 2007 to 2008 were MDR-AB CNS infections. Two cases of MDR-AB CNS infection were cured with intraventricular or intrathecal colistin without any side effects. Therefore, intraventricular or intrathecal colistin should be considered for MDR-AB CNS infection. Studies of the dose and duration of intraventricular and intrathecal administration are needed. (Korean J Med 2011;80:118-121)
송세빈 ( Se Bin Song ),문송미 ( Song Mi Moon ),조창현 ( Chang Hyun Cho ),황연희 ( Yeon Hee Hwang ),임효석 ( Hyo Seok Lim ),손준성 ( Jun Seong Son ),이미숙 ( Mi Suk Lee ) 대한내과학회 2010 대한내과학회지 Vol.78 No.3
Patients infected with human immunodeficiency virus (HIV) may develop various liver diseases, including viral hepatitis, granulomatous inflammation, malignancies, vascular disease, drug-induced hepatitis and, sometimes, diseases of unknown origin. In this case, a 35-year-old HIV-infected man presented with fatigue, myalgia, elevated liver enzymes, and multiple skin lesions for 3 months. Since the abdominal computed tomography (CT) and viral marker tests failed to explain the cause of his symptoms and signs, a liver biopsy was performed. This revealed a granuloma consisting of epithelioid cells without necrosis. His symptoms, skin lesions, and abnormal liver enzymes improved without changing his management, including the anti-retroviral agents. He was diagnosed with idiopathic granulomatous hepatitis based on the pathologic findings of the liver and clinical course. Aggressive diagnostic methods, such as a liver biopsy, should be considered for HIV-infected patients with liver disease. (Korean J Med 78:391-395, 2010)
Klebsiella ozaenae에 의한 내인성 안내염
김나혜(Na Heah Kim),문송미(Song Mi Moon),지미정(Mi Jung Chi) 대한안과학회 2016 대한안과학회지 Vol.57 No.7
목적: Klebsiella ozaenae는 주로 구강과 비인강의 상재균으로 만성 위축성 비염의 원인으로 알려져 왔다. 안내염의 원인균으로 드문 Klebsiella ozaenae에 의한 내인성 안내염의 증례를 경험하였기에 보고하고자 한다. 증례요약: 간세포암으로 항암화학요법 치료 중이던 61세 남자 환자가 2일 전부터 발생한 좌안의 시력 저하와 통증으로 의뢰되었다. 시력은 안전 수지 10 cm, 안압은 29 mmHg였으며, 공막부분파열과 맥락막 노출 소견과 함께 초음파 검사에서 망막하 농양 소견을 보였다. 배뇨 시 통증 및 빈뇨 증상과 함께 소변검사에서 백혈구뇨 및 세균뇨 소견을 보여 요로감염에 의한 내인성 안내염을 의심하였다. 유리체강내 항생제주입술 및 전신항생제 치료를 하였음에도 불구하고 4일째 시력은 광각무 상태로 저하되었다. 통증이 심해지고 안압은 조절되지 않아 이후 안구 적출술이 시행되었으며 안구 내 농 배양 검사에서 Klebsiella ozaenae가 배양되었다. 결론: Klebsiella ozaenae는 안내염의 드문 원인균으로 염증의 진행 속도가 빠르고 예후가 좋지 않았다. 또한 내인성 안내염의 원인으로 화농성 간농양 이외에 요로감염도 염두에 두어야 한다. <대한안과학회지 2016;57(7):1139-1143> Purpose: To report a case of endogenous endophthalmitis due to Klebsiella ozaenae, which is a rare causative organism of endophthalmitis. Case summary: A 61-year-old male who was undergoing chemotherapy for hepatocellular carcinoma complained of sudden visual loss and ocular pain in his left eye for 2 days. On the first examination, the patient’s visual acuity was counting fingers at 10 cm and the intraocular pressure was elevated to 29 mm Hg. Partial scleral rupture and choroidal prolapse were observed. Subretinal abscess was detected with increased echogenicity using ultrasonography. The patient complained of burning sensation on voiding and urinary frequency; subsequent urinalysis showed pyuria and bacteriuria. Intravitreal and systemic antibiotics were administered under the impression of endogenous endophthalmitis caused by urinary tract infection. Despite treatment, visual acuity decreased to no light perception in 4 days and intraocular pressure and pain was uncontrollable. Enucleation was performed and pus culture from the eye during surgery revealed Klebsiella ozaenae. Conclusions: Klebsiella ozaenae is a rare causative organism of endophthalmitis and shows a rapid progress and poor prognosis. Endogenous endophthalmitis must be highly suspected in patients with urinary tract infection as well as pyogenic liver abscess. J Korean Ophthalmol Soc 2016;57(7):1139-1143
병원획득 Extended-spectrum ß-Lactamase 생성 Escherichia coli 균혈증의 위험인자
고대식 ( Dai Sik Ko ),문송미 ( Song Mi Moon ),이지성 ( Ji Sung Lee ),박윤수 ( Yoon Soo Park ),조용균 ( Yong Kyun Cho ) 영남대학교 의과대학 2013 Yeungnam University Journal of Medicine Vol.30 No.2
Background: The prevalence of extended-spectrum β-lactamase (ESBL)-producing Escherichia coli is increasing rapidly worldwide. Treatment options for ESBL-producing E. coli are limited, and infections caused by this organism are associated with improper antibiotic use, a long hospital stay, and increased mortality. Thus, the assessment and early recognition of the risk factors of nosocomial infections due to ESBL-producing E. coli are important for the infection control and proper treatment. Methods: A case-control study was performed that included nosocomial episodes of ESBL-producing E. coli bacteremia at a tertiary care hospital from January 2004 to December 2007. For each case patient, three controls were randomly selected and data on predisposing factors were collected. Results: Fifty-five cases of nosocomial ESBL-producing E. coli bacteremia were studied. Carbapenem usage (OR: 11.3, 95% CI: 1.1-115.9, p=0.041), quinolone usage (OR: 4.5, 95% CI: 1.1-18.8, p=0.042), biliary obstructive disease (OR: 11.8, 95% CI: 3.0-46.7, p<0.001) and the APACHE II score (OR: 1.3, 95% CI: 1.2- 1.5, p<0.001) were analyzed as independent risk factors of nosocomial ESBL-producing E. coli bacteremia. Conclusion: Our results showed that physicians caring for patients with risk factors of nosocomial bacteremia should consider ESBL-producing E. coli as the causative organisms of the disease.
HIV 감염 환자에서 발생한 Ramsay Hunt 증후군
강은경 ( Eun Kyung Kang ),김지연 ( Ji Yeon Kim ),송경환 ( Kyung Hwan Song ),문송미 ( Song Mi Moon ),고광필 ( Kwang Pil Ko ),서일혜 ( Yiel Hea Seo ),박윤수 ( Yoon Soo Park ) 대한내과학회 2016 대한내과학회지 Vol.90 No.2
Ramsay Hunt syndrome is caused by reactivation of the varicella zoster virus in the geniculate ganglion of the sensory branch in the face and ears. It is characterized by peripheral facial palsy, ear pain, and vesicles in the auditory canal and auricle. We report on a first case of Ramsay Hunt syndrome in a patient with human immunodeficiency virus in Korea. The patient, a 40-year-old male, first presented with otalgia and ear fullness. On admission, he had right facial palsy of the peripheral type, otorrhea, headache, limited tongue movement, and right auricle vesicular eruptions. He had positive human immunodeficiency virus antibody and Western blot tests. His CD4 T cell count was 281/μL. The patient was treated with valacyclovir and steroid with highly active antiretroviral therapy. His symptoms and facial palsy improved with treatment. (Korean J Med 2016;90:169-172)
WOPN을 동반한 급성 괴사성 췌장염 환자에서 내시경적 췌장괴사 제거술 후 발생한 Wernicke Encephalopathy
김민수 ( Min Su Kim ),강은경 ( Eun Kyung Kang ),김수영 ( Su Young Kim ),김지연 ( Ji Yeon Kim ),문송미 ( Song Mi Moon ),서일혜 ( Yiel Hea Seo ),조재희 ( Jae Hee Cho ),박윤수 ( Yoon Soo Park ) 대한췌장담도학회 2016 대한췌담도학회지 Vol.21 No.1
Infected walled-off pancreatic necrosis (WOPN) is dangerous complication of acute pancreatitis. Open necrosectomy and post-operative irrigation of necrotic cavity have been conventional treatment for infected pancreatic necrosis, however, recently minimally invasive techniques such as endoscopic necrosectomy has been regarded as preferred treatment method for infected WOPN. Endoscopic necrosectomy provides a targeted approach with a reduction in the systemic inflammatory response and avoidance of wound complications. Non alcohol related Wernicke encephalopathy is rare disease caused by thiamine deficiency due to intravenous feeding, and presented an encephalopathy, oculomotor dysfunction, gait ataxia. We report herein a case of Wernicke encephalopathy after successful endoscopic necrosectomy for infected WOPN.
문예성(Yae-Sung Mun),고용훈(Yong-Hoon Go),이용현(Yong-Hyun Lee),이은혁(Eun-Hyuk Lee),강현아(Hyun-A Kang),김연재(Yun-Jae Kim),문송미(Song Mi Moon),황유진(You-Jin Hwang) 한국산학기술학회 2014 한국산학기술학회 학술대회 Vol.- No.-
다약재 내성을 나타내는 병원성 미생물에 의한 질병이 점점 많아지고 있다. 항생제 내성을 나타내는 유전자가 발현되어 항생제 내성을 나타내게 되고 저항성을 갖는다. 본 논문에서는 병원성 미생물인 methicillin-resistance Staphylococcus aureus (MRSA)가 다약재 내성을 나타내고 있는 것을 확인하고 다약재 내성을 나타나게 하는 유전자의 종류를 규명하고자 하였다.