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양동규(Dong Gyoo Yang),이돈행,임대순(Dae Soon Yim),김원호(Won Ho Kim),한광협(Kwang Hyub Han),최흥재(Heung Jai Choi),노성훈(Sung Hoon Noh),이종태(Jong Tae Lee),최인준(In Joon Choi) 대한내과학회 1991 대한내과학회지 Vol.41 No.3
Systemic hemangimatosis, involving cutaneous tissue, visceral organs and the skeletal system, is a rare condition and has not yet been reported in Korea. Hemangiomatosis involving the gastrointestinal tract may cause intestinal obstruction and gastrointestinal bleeding. Sometimes thrombocytopenia and coagulopathy facilitates spontaneous bleeding. We report a case of systemic hemangiomatosis presenting gastrointestinal belleding as a first symptom in a 36-year-old man. Multiple hemangiomas were demonstrated in the liver, spleen, and intestine by ultrasonography, computed tomography, and angiography and were confirmed by surgery.
낭종내 Minocyclin chloride 1회 주입으로 치료된 거대 간낭종
강진경(Jin Kyung Kang),박인서(In Suh Park),문영명(Young Myung Moon),임대순(Dae Soon Yim),김중영(Joong Young Kim),함기백(Ki Baik Hahm),라선영(Sun Young Ra),최흥재(kHeung Jai Choi) 대한소화기학회 1993 대한소화기학회지 Vol.25 No.2
Hepatic cysts are often encountered on ahdominal ultrasonography or computed tomography and are usually asymptomatic. However, huge cyst bothers the patients either by compression or complicaticns such as intracystic infections or hemorrhage!. Various modalitles of treatments such as alcohol instillation or other sclerosing agents instillation have been reported. However, two or more sessions of treatment are usually required to ablate cyst We report, here, one-shot instillation of minocyclin chloride to treat a large hepatic cyst causing compression symptom with improvement.
간장 및 담도 : 생검으로 확진된 지방간의 임상적 고찰
강진경(Jin Kyung Kang),최흥재(Heung Jae Choi),전재윤(Chae Yoon Chon),박찬일(Chan Il Park),윤정한(Jung Han Yoon),임대순(Dae Soon Yim) 대한소화기학회 1986 대한소화기학회지 Vol.18 No.1
N/A Fatty liver is caused by derangement of fat metabolism and can be reversed by removal of contributing factors. The contributing factors of fatty liver include overweight, chronic alcoholism, diabetes mellitus, malnutrition, and drug abuse such as tetracycline. In this study, age and sex distribution, contributing factors, clinical features, liver function tests, correlation of grade of fatty liver to body weight, liver function test and viral markers were reviewed. Clinical diagnosis, peritoneoscopic diagnosis, and pathologic findings were compared in 54 cases with fatty liver proven by peritoneoscopic liver biopsy who were admitted to Yonsei University Severance Hospital from January 1981 to June 1985. The following results were obtained. 1) The mean age of 54 cases was 39. 9 years and the male to female ratio was 2.9 to 1 2) Contributing factors of fatty liver were overweight in 27 cases(50.0%), chronic alcoh- olism in 23 cases(42.5%), diabetes mellitus in 8 cases(14.9%), and malnutrition in 1 case (1 .9%). Overweight was the only contributing factor in 13 cases(24.o%), chronic alcoholism only in 12 cases(22.2%) There were more than one contributing factors in 16 cases(29.7%) and no definite contributing factors in 12 cases(22.2%). 3) Easy fatigability was the most frequent symptom which was found in 28 cases(52.7%) and hepatomegaly was the most common physical finding which was found in 26 cases (48.6%). 4) The r-GTP level was increased in 43 cases(80%), SGOT in 35 cases(65.5%), SGPT in 40 cases(74.5%), and triglyceride in 37 cases(68.9%). 5) The r-GTP and SGOT level were more elevated with statistical significance in chronic alcoholic group than in overweight group. G) There were no correlations of grade of fatty liver to body weight and liver function tests. 7) Eleven cases(22.5%) of 49 cases were HBsAg positive which was significantly higher than that of normal population in Korea. 8) A clinical diagnosis prior to peritoneoscopy was chronic hepatitis in 34 cases(62.8%), alcoholic liver disease in 9 cases(16.7%), fatty liver in 5 cases(9.2%), and HBsAg carrier in 4 cases(7.5%) A peritoneoscopic diagnosis was fatty liver in 3l cases(57.4%), chronic hepatitis in 10 cases(18.5%), acute unresolved hepatitis in 5 cases(9.3%), and normal liver in 8 cases(14.8%). In summary, the clinical diagnosis of fatty liver was made only in 5 cases(9.2%), and peritoneoscopic diagnosis of fatty liver in 31 cases(57.4%). The majority of the rest was chronic hepatitis. Therefore, it is mandatory to perform liver biopsy to distinguish fatty liver from chronic hepatitis.
간장 ( 肝臟 ) · 담도 ( 膽道 ) 및 췌장 ( 膵臟 ) : 원발성 간외담관암의 임상적 고찰
강진경(Jin Kyung Kang),최흥재(Heung Jai Choi),박인서(In Suh Park),최원(Won Choi),정재복(Jae Bock Chung),김원호(Won Ho Kim),김영수(Young Soo Kim),임대순(Dae Soon Yim),송시영(Si Young Song) 대한소화기학회 1991 대한소화기학회지 Vol.23 No.4
N/A Despite significant advances in the diagnosis and treatment of various malignancies, the manangement of extrahepatic bile duct carcinoma remains most frustrating. Unfortunately complete excision of the tumor often impossible, because non-expandable anatomic structures are involved early. In an effort to identify the clinical characteristics and those factors associated with these car- cinomas which might have prognostic value, we analyzed the 216 patients with carcinoma of extrahe- patic bile ducts who were admitted to Severance Hospital, Yonsei University from January 1979 to July 1989. 1) The mean age of the patients clinical manifestations included jaundice in 198 cases (91.7%), abdominal pain in 125 cases (57.9%), hepatomegaly in 124 cases (57.4%) and weight loss in 120 cases (55.6%). The biliary stones were associated in 20.4% and the Clonorchis sinesis in 7.4%. 2) The range of total bilirubin levels on admission was 2.0 +- 9.9 mg/dl in 54 cases (25.0%), 10.0 +- 19. 9mg/dl in 78cases (36.1%) and more than 20mg/dl in 68cases (31.5%). 3) Abdominal ultrasonography, computed tomography, ERCP and PTC were performed in 178, 125, 133, 87 cases respectively, and their diagnostic accuracies were 51.1%, 66.4%, 84.2% and 93.1%, respecti vely. 4) The tumors were located in upper third in 83 cases (38.4%), middle third in 51 cases (23.6%) and lower third in 56 cases (25.9%). And the cases of diffuse type were found in 26 cases (12.0%). 5) The direct invasion of surrounding structures were found in 84.9% of patients, the regional lymph node metastasis in 43.9% and the distant metastasis in 12.% 6) Among 129 cases histologically confirmed the diagnosis, the tumor was well differentiated in 28 cases (21.7%), moderately differentiated in 34 cases (26.4%), poorly differentiated in 36 cases (27.9%), undetermined differentiation in 36 cases (27.9%), and epidermoid carcinoma in 1case (0.8%) and pleomorphic giant cell carcinoma in 1 case (0.8%). 7) The conservative treatment was performed in 52 cases (24.1%), non-operative biliary drainage in 41cases (18.9%). Among 119 (55.1%) cases who underwent operation, 67cases (31.1%) had t-tube choledochostomy, 29 cases (13.4%) biliary-enteric bypass and 23 cases (10.6%) radical resection. 8) The cumulative postoperative median survival from the date of definitive diagnosis was 5.8 months and its mean survival was 9.5 months. a) When analyzed survival rate according to the location of the lesion, the survival data were: upper third lesions, 12.8%, 3.7% and 3.7% at 1 year, 3year and 5year, respectively; middle third lesion, 33.7%, 7.9% and 3.9%, respectively; the lower third lesions 40.0%, 16.8% and 8.4%, respectively. And the 1 year and 2 year survival rate were 31.0% and 12.0% respectively in the patients with diffuse lesions. The survival in patients with carcinoma of lower third bile duct lesions were significantly higher than in upper third lesions and diffue leseions (p<0.05), and there was no statistical significance between in lower third and middle third lesions. b) Survival rates according to the histologic differentiation were; well differentiated lesions, 58.1%, 29.5% and 14.8% at lyear, 3year and 5year, respectively; moderate differentiated lesions, 38.6%, 18.0% and 18.0%, respectively; poorly differentiated lesions, 12.5%, 6.3% and 0.0% respectively. The survival in well differentiated lesions were significantly higher than in poorly differentiated lesions (p<0,05). c) Survival rates according to the stage were: stage II, 83.3%, 37.0% and 27.8% at lyear, 3year and 5year, respectively; stage III, 39.2%, 8.7% and 8.7%, respectively; stage IV, 17.7%, 4.7% and 2.4%., respectively. The survival rate in stage II lesions were significantly higher than stage III (p < 0. 01) and stage IV (p<0.001). d) Survival rate according to the modalities of treatment were: conservative treatment group, 6.2% at 6 month without any surviver longer than lyear; non-operative biliary drainage group
만성 간질환 및 원발성 간세포암 환자의 혈청 α1 - Antitrypsin 표현형의 변화
강진경(Jin Kyung Kang),최흥재(Heung Jai Choi),박인서(In Suh Park),문영명(Young Myung Moon),정재복(Jae Bock Chung),한광협(Kwang Hyub Han),전재윤(Chae Yoon Chon),김원호(Won Ho Kim),임대순(Dae Soon Yim),함기백(Ki Baik Hahm),신용준(Yong 대한소화기학회 1993 대한소화기학회지 Vol.25 No.2
N/A In parallel with the discovery of nev alleies inceasing the complexity of the Pi system, technical refinements have made the classification of an individual with respect to his Pi system relativeiy simple. Isoelectrofocusing in polyacrylamide gels is advantageous method in analyzing pisystem because of ease of performance, high resolution and reproclucibility. Most individuals have the PiMM phenotype resulting in normal plasma a1-antitrypsin (a,-AT) levels. The classical a1-AT deficiency is designated as Pizz in its homogygous form and has 15% of normal plasma a1-AT level, which is known to be associated with increased risk of cirrhosis and primary liver cancer But there is stilJ debate as the cause of this associated liver disease. This study is aimed to know the distribution and contribution of structural variants of a1-AT in South Korean patients with chronic liver diseases inr.uding hepatocellular carcinoma. One hundred thirty nine patients with chronic liver diseases or hepatocellular carcinoma were studied. Rlood sarnples were taken frorn each. Phenotypes of a1-AT were determined by electrofocusing in polyacrylamide gel electrophoresis. The results obtained were as folloas, None of the cases showed deficiency or null variant of a1-AT in patients with chronic liver diseases, hut two cases with hepatocellular carcinoma showed MS phenotype. About half of the cases with chronic liver disease and hepatocellular carcinoma showed homologcius polymorphism of a1-AT phenotype suballeles such as M1M1. M2M2 and M3M3. The distribution of the structural variants of a1-AT phenotype in patients with chronic liver diseases and hepatocellular carcinoma were in order as tollows; M1M1 (51.8%), M1M2(24.5%), M2M2 (7.9%), M3M3 (6.5%), M1M3, (5.8%),M3M3 (2.2%) and M1S (1.3%). In con, lusion, none of the cases with chronic liver diseases showed deficiency or null typed structural variants of a1-AT, but there were two cases with MS phenotype among the 39 patients with hepatocellular carrcinoma. Therefore, genetically determined a1-AT. deficiency seems to be not etiological]y important in South Korean patients with chronic liver disease.