http://chineseinput.net/에서 pinyin(병음)방식으로 중국어를 변환할 수 있습니다.
변환된 중국어를 복사하여 사용하시면 됩니다.
증례 : 신장 ; 발작성 야간혈색소뇨증에서 발생한 급성 신부전증
남현경 ( Hyun Kyung Nam ),유현승 ( Hyun Seung Yoo ),안원석 ( Won Suk An ),김성은 ( Seong Eun Kim ),김성현 ( Sung Hyun Kim ),나서희 ( Seo Hee Rha ),윤성국 ( Seong Kuk Yoon ) 대한내과학회 2009 대한내과학회지 Vol.77 No.5S
저자들은 PNH 진단 후 2년간 경구 스테로이드로 조절하던 중 상기도 감염과 동시에 용혈 발작과 단백뇨를 동반한 급성 신부전이 발생, 신생검과 신장 자기공명촬영을 통해 혈철소 침착을 확인하였으나 다른 만성적 신손상 소견 없이 급성 세뇨관 괴사 소견만을 보였던 환자에서 급성 신부전회복 후 골수 이식을 시행하여 치료하고 신기능을 정상으로 유지하였던 경험을 문헌고찰과 함께 보고하는 바이다. Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired chronic hemolytic anemia characterized by persistent intravascular hemolysis. The kidneys are subject to acute failure or chronic injury in association with ischemia, intravascular hemolysis, and he-mosiderin deposition; however the pathogenesis of renal failure has not been clearly defined. In Korea, there has been 1 case of acute renal failure with PNH demonstrated by MRI and a kidney biopsy. A 39-year-old female patient with PNH who received low dose oral prednisolone for 2 years developed oliguric acute renal failure after 2 days of fever and sore throat. The serum LDH level was elevated, and indirect bilirubinemia was noted. A renal biopsy showed features of acute tubular necrosis and hemosiderosis. Magnetic resonance imaging revealed characteristic features of renal hemosiderosis. There was no evidence of either renal vein thrombosis or cortical infarct. Her renal function became stabilized with hemodialysis and intravenous fluid, and she recovered 4 weeks later. (Korean J Med 77:S1231-S1236, 2009)
구정모 ( Jeong Mo Koo ),김영훈 ( Young Hoon Kim ),홍현종 ( Hyun Jong Hong ),김혜인 ( Hye In Kim ),윤성국 ( Seong Kuk Yoon ),안원석 ( Won Suk An ),이성원 ( Sung Won Lee ),정원태 ( Won Tae Chung ) 대한신장학회 2007 Kidney Research and Clinical Practice Vol.26 No.2
Idiopathic retroperitoneal fibrosis (IRF) is a rare disease characterized by inflammatory and fibrous tissue proliferation in the retroperitoneum, which often surrounds the adjacent retroperitoneal structure to cause compressive complications such as hydronephrosis. Its pathogenesis is still unknown, but recently the association with autoimmune disease is being suggested. Although the prognosis is generally good, if diagnosis or treatment is delayed, the disease can progress to acute or chronic renal failure. In the past, surgical procedures such as ureterolysis or transpositioning of the involved ureter were the mainstay of the treatment. But recent studies using steroids, immunosuppressants and tamoxifen have reported generally good results. However, the adequate dose or duration of medical treatment and the treatment for recurred disease have not been established yet. We report a case of that retroperitoneal fibrosis recurred 1 year after 2-weeks steroids therapy. It was successfully treated with combination therapy of steroids and tamoxifen.