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아스파라기나제 과민성에 대한 전처치와 급속 탈감작의 효용성
윤다혜 ( Da Hye Yoon ),강성희 ( Sung Hee Kang ),김환수 ( Hwan Soo Kim ),이재욱 ( Jae Wook Lee ),윤종서 ( Jong Seo Yoon ),정낙균 ( Nack Gyun Chung ),조빈 ( Bin Cho ) 대한천식알레르기학회 2015 Allergy Asthma & Respiratory Disease Vol.3 No.4
Purpose: L-asparaginase is a crucial chemotherapeutic agent for the treatment of acute lymphoblastic leukemia. However, hypersensitivity to L-asparaginase is common which limits its clinical use. Methods: We performed 44 cases of premedication and 3 cases of desensitization in 16 patients with hypersensitivity to L-asparaginase. Results: With premedication, 33 cases completed L-asparaginase injection with no hypersensitivity reactions. Eleven cases showed mild hypersensitivity reactions, such as urticaria. Desensitization was performed in 3 cases: in 2 cases, desensitization was successful, and in 1 case the medication was switched to Erwinia asparaginase. Conclusion: Premedication and desensitization appear to be useful in helping patients receive desired doses of L-asparaginase in pediatric patients with acute lymphoblastic leukemia. (Allergy Asthma Respir Dis 2015;3:288-293)
대학생의 장애체험 교육을 통한 장애에 대한 태도 및 인식 변화
윤다혜(Yoon, Da-Hye),권오정(Kwon, Oh-Jung) 한국주거학회 2016 한국주거학회 학술대회논문집 Vol.28 No.2
The purpose of the study was to observe the change in attitude and awareness towards disability through experience-based education of university students. The data for the analysis was collected through questionnaire survey before and after disability experience from July 25 to August 23, 2016, and the sample consisted of 30 participants who were university students. The experience included blindness and physical disability and the participants were given several activities to try out in either blindfolds or wheelchairs. The results were as follows : 1) When we compare the change in attitude before and after the experience, there were significant change in items such as ‘being near a disabled person doesn’t make me uncomfortable’, ‘they aren’t that different from abled people’ and ‘it wouldn"t make me uncomfortable if a friend introduced me to a disabled person.’ 2) The difference in all the items before and after the experience were small, which shows that change in attitude cannot be achieved in a short amount of time. Therefore, such factor should be considered when developing a future experience-based educational programs for accurate results. 3) Change in awareness after the experience were big in items related to spatial problems, such as ‘toilet for the disabled’, ‘raised blocks for the blind’, ‘the surroundings’, etc. which shows that awareness towards the space designed for the disabled was small.
장미진(Mi Jin Jang),윤다혜(Da Hye Yoon),이지은(Ji Eun Lee),박선영(Sun Young Park),이인구(In Goo Lee) 대한소아신경학회 2016 대한소아신경학회지 Vol.24 No.2
목적: 본 연구는 소아에서 발생한 얼굴신경 마비의 임상적인 특징과 예후 뿐 아니라, 기저질환이 없는 환자의 얼굴신경 마비와 백혈병 환자의 얼굴신경 마비를 비교하여 차이점을 알아봄으로써 향후 얼굴신경 마비의 치료와 예후를 예측하는데 도움을 주고자 하였다. 방법: 2009년 1월부터 2014년 12월까지 가톨릭대학교 서울성모병원 소아신경분과에 안면마비 증상을 보여 내원한 18세 미만의 환자들 중 최소 6개월 이상 추적 관찰이 가능하였던 기저질환이 없었던 48명과 백혈병 환자 5명을 대상으로 하였다. 얼굴 신경 마비의 정도와 prednisone 치료 후 변화는 House-Brackmann 안면신경마비 판정 시스템을 이용하였고, 병변의 위치는 얼굴 근육의 마비 외에 통증의 여부, 맛감각의 변화 및 청각과민증 등의 여부를 통해 알아보았다. 결과: 얼굴 신경의 손상 정도는 기저질환이 없었던 환자들에서는 House-Brackmann 안면신경 마비 판정 시스템의 grade III와 grade IV가 90% 이상을 차지하고 있었고, 백혈병 환자에서는 모두 grade IV의 중증 기능이상을 보이고 있었다. 얼굴 신경 마비의 병변 부위는 모든 환자의 90% 이상에서 얼굴 신경의 가장 말단 부위인 붓꼭지 구멍 이하 이었다. Prednisone 치료 후 기저질환이 없었던 환자 43명 중 30(69.8%)명에서는 완전히 증상이 소실되었고, 11(25.6%)명에서는 약간의 마비 증상이 남아 있으나 기능의 80% 이상을 수행할 수 있는 grade II를 보이고 있었다. 그러나 백혈병 환자들에서는 2(40%)명에서 증상이 완전히 소실되었으나 나머지 3명은 각각 1명 씩 grade II, III, IV 상태를 보이고 있었다. 결론: 소아의 얼굴 신경 마비의 병변은 대부분 붓꼭지 구멍 이하에서 발생하며, 마비 정도도 심하지 않아 예후가 좋은 것으로 생각된다. 그리고 경구 Prednisone 치료는 기저질환이 없는 환자의 경우 90% 이상에서 좋은 효과를 기대할 수 있지만, 백혈병 환자의 경우는 절반 정도에서만 효과를 기대할 수 있다. Purpose: This study was designed to identify the clinical characteristics and prognosis of facial nerve palsy in children, and to determine the different characteristics of the facial nerve palsy patients without underlying condition as opposed to the patients with leukemia, which will help to predict the prognosis and to help treat them. Methods: We investigated 53 patients under 18 years old retrospectively who were diagnosed as facial nerve palsy at the pediatric neurology department of Seoul St. Mary's Hospital from January 2009 to January 2015, and 5 patients with leukemia were included. The degree of nerve damage in a facial nerve palsy patients was determined according to House-Brackmann score. Results: More than 90% of the patients without underlying condition showed grade III and grade IV in the degree of facial nerve damage, meanwhile all of the leukemia patients had grade IV. The location of lesion in more than 90% of the facial nerve palsy patients was under stylomastoid foramen that is the end of the facial nerve. After oral prednisone therapy, 30(69.8%) of 43 patients without underlying condition showed a complete recovery, 11(25.6%) showed little remaining of palsy but was able to conduct 80% of the normal function, which is grade II. In 5 leukemia patients, 2 (40%) showed complete recovery, but 3 patients showed grade II, III and IV, respectively. Conclusion: In children with facial nerve palsy, the location of lesion is usually under stylomastoid foramen, and the degree of palsy is mild so we can predict good outcome. In treatment with oral prednisone, we can expect more than 90% of effectiveness in patients without underlying condition, but only half in leukemia patients.
정우진 ( Woo Jin Chung ),윤다혜 ( Da Hye Yoon ),이의경 ( Eui Gyung Lee ),방경원 ( Kyong Won Bang ),김환수 ( Hwan Su Kim ),전윤홍 ( Yoon Hong Chun ),윤종서 ( Jong Seo Yoon ),김현희 ( Hyun Hee Kim ),김진택 ( Jin Tack Kim ),이준성 ( 대한천식알레르기학회 2014 Allergy Asthma & Respiratory Disease Vol.2 No.2
Purpose: Children admitted to pediatric intensive care unit (PICU) with respiratory tract disease, often have a tendency to be readmitted to PICU with disease progression. We studied the risk factors for readmission to PICU, with respiratory disease progression. Methods: Among 286 children admitted to Seoul St. Mary’s Hospital PICU from April 2009 to March 2012, 129 children admitted with respiratory tract disease were enrolled. We grouped the children readmitted to PICU with respiratory tract disease progression within 2 weeks (readmission group), and the others (control group). We compared basic and respiratory tract disease characteristics at initial PICU admission between them, by retrospective chart review. Results: Among 129 children, 8 were included in the readmission group, and 121 in the control group. Mortality and underlying disease incidence were higher in the readmission group (P=0.003 and P=0.033, respectively). The readmission group showed higher parenchymal lung disease incidence, and lower initial saturation by pulse oxymeter (SpO2)/fraction of inspiratory oxygen (FiO2), despite underlying disease influence (P=0.035 and P=0.041, respectively). Logistic regression on the underlying disease and respiratory variables showed no single factor with a significantly independent influence on readmission, but parenchymal lung disease had more independent influence. Conclusion: For PICU readmission with respiratory tract disease progression, parenchymal lung disease and lower initial SpO2/FiO2 can be a risk factor despite underlying disease influence. Underlying disease and each respiratory characteristic were not significantly independent risk factors, suggesting a correlation of factors. But, parenchymal lung disease can be a more independent risk factor. (Allergy Asthma Respir Dis 2014;2:128-133)