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혈장반출법으로 호전된 혈전성 혈소판 감소성 자반증 1 예
조인성(In Sung Cho),배일훈(Ill Hoon Bae),고광선(Kwang Sun Ko),이경주(Kyoung Joo Rhee),안성구(Sung Ku Ahn),이혜림(Hye Rim Lee) 대한내과학회 1991 대한내과학회지 Vol.40 No.6
Thrombotic thrombocytopenic purpura is a relatively rare syndrome of uncertain etiology, characterized by thrombocytopenia and microangiopathic hemolytic anemia. Most patietns have either fever, neurologic manifestations, or renal abnormalities. Thrombotic thrombocytopenic purpura was considered a rapidly progressive disase with a high mortality. However, recent reports indicate that most patients recover by improvement of treatment method. The pathologic finding is that hyaline thrombi, composed of aggregated platelets, occlude arterioles and capillaries of virtually every tissue. Although endothelial cell proliferation may be observed in proximity to the lesions, inflammatory reactions and vasculitis are not observed. We experienced a patient treated with steroids, anti-platelet agents, and fresh frozen plasma which had little therapeutic effect. But clinical and labor a brief review of the literature.
박성규,고광선,김선영,조인성,이경주,배일훈,박찬권,백상현 대한내과학회 1990 대한내과학회지 Vol.39 No.2
Lymphangioleiomyomatosis is a rare disease of women, usually of childbearing age, characterized by the proliferation of benign but atypical smooth muscle cells in the walls of the lymphatics of the lower respiratory tract, pleula, mediastinum, and retroperitoneum. The disease is clinically manifested by recurrent chylous pleural effusion, Pneumothorax, or ascites and hemoptysis. We experienced a case of pulmonary 1ymphan-gioleiomyomatosis in a 30-year-old female patient who had suffered from recurrent pneumothorax associated with normal pregnancy, so we report it with a brief review of the literature.