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정풍만,이석현 대한소화기학회 1992 대한소화기학회지 Vol.24 No.6
pigmentation and gastrointestinal hamartomas. Hamartomas are not generally regarded to be premalignant, but in the Peutz-Jeghers syndrome a number of authors have found the existence of malignancies in hreast, gonad as well as gastrointestinal tract. We studied 11 cases of Peutz-Jegher. syndrome admitted at Department of Surgery of Hanyiang University hospital and acquired the following results: The age ranged from 3 years old to 44 years old, with average age 16 years old. All patients had had mucocutaneous pigmentation since early infants, repeated episodes of abdominal pain due to intussusception, occult blood loss from the intestinal traqt, and anemia are main symptoms. Eight cases out of 11 cases had family history. The polyps distributed as follows: Jejunum (11 cases, 100%), ileum (9 cases, 81.896), colon (9 cases, 81. S), stomach (4 cases, 36.44), and duodenum (3 cases, 29. 3%). Colonic adenocarcinoma develqped in a 44 years old man. The development of malignancies in breast, gonad as well as gastrointestinal tract and recurrnce of polyps in GI tract required regular follow-up study.
담도폐쇄증 의심하에 수술을 위해 전원된 환자의 임상 경과 분석
정풍만,이종인,Jung, Poong-Man,Lee, Jong-In 대한소아외과학회 2001 소아외과 Vol.7 No.2
Biliary atresia (BA) is very difficult to distinguish from neonatal hepatitis (NH) and its prognosis depends on the age at the time of Kasai operation. Therefore early differentiation between these two conditions is very important. Although various clinical and laboratory tests have been reported to differentiate between them, they are still of limited value. From 1980 to 1999, forty-five infants were referred to our pediatric surgical unit for operation for suspected BA. Eight patients underwent Kasai operation immediately because of late diagnosis. These were excluded from the study. The clinical history, physical findings. radiologic and laboratory examinations of 37 cases were analyzed retrospectively. The average age of BA (n=20) was $55.1{\pm}16.7$ days, and that of NH (n=17) was $55.8{\pm}15.6$ days. The sex ratio of BA was 13:7, and that of NH was 14:3. All the patients had obstructive jaundice and acholic stool except 4 BA and 6 NH patients. Acholic stool with yellow component was more frequent in NH. Onset of jaundice was within 2 weeks after birth in 85 % of BA, and in 65% of NH. The onset of acholic stool was within 2 weeks after birth in 60 % of BA, and in 23.5 % of NH. The duration of jaundice and acholic stool of BA were $50.9{\pm}16.6$ days and $41.3{\pm}18.4$ days and those of NH were $40.1{\pm}23.1$ days and $26.6{\pm}25.4$ days respectively. The ultrasonogram and hepatobiliary scan were useful, but not a definitively reliable method for the differentiation of these two diseases. There was no difference in laboratory data. Seventeen cases had NH among 45 referred cases for Kasai operation with the clinical impression of BA, and 4 cases of 17 NH cases needed to be explored to rule out BA. In conclusion. false positive rate of clinical impression of BA was 37.8 %. and negative exploration rate was 8.9 %, Therefore. careful clinical observation for 1-2 weeks by an experienced pediatric surgeon was very important to avoid unnecessary operation to rule out NH up to the age of 8 - 10 weeks. so long as the stool had yellow component.
정풍만,이종인,Jung, Poong-Man,Lee, Jong-In 대한소아외과학회 1999 소아외과 Vol.5 No.1
Among 60 children with teratoma, forty-three (71.7 percent) were girls and 17 (28.3 percent) boys, Primary sites were sacrococcygeal in 30 patients (50 percent), retroperitoneal in 12 (20 percent), ovarian in 11 (18.3 percent), testicular in 3 (5 percent), and one in each of nasopharyngeal, gastric, hepatic and pancreatic (1.6 percent, respectively). Fifty-five (91.7 percent) teratomas were benign and 5 (8.3 percent) malignant. Malignant teratomas W8,re detected only in the sacrococcygeal region (16.7 percent). Age greater than 2 mouths at diagnosis, presence of urinary or colonic obstructive symptoms, multiple masses and elevated serum alpha-fetoprotein were indicators of malignancy in the sacrococcygeal region. Tumor size, presence of calcification, and gross apperance (cystic or solid) did not correlate with malignancy. Thirteen (21.7 percent) cases were associated with other anomalies. For the immature teratoma, operative resection without adjuvant chemotherapy was adequate treatment. Three patients with malignant tumors survived, one who received chemotherapy survived 3 years and the others without chemotherapy survived for 5 and 10 years.