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유순집(Soon Jib Yoo),윤형규(Hyung Kue Yoon),윤건호(Kun Ho Yoon),강무일(Moo Il Kang),차봉연(Bong Yun Cha),최의진(Eu Jin Choi),이광우(Kwang Woo Lee),손호영(Ho Young Son),강성구(Sung Koo Kang),이해규(Hae Giu Lee),김태규(Tae Kyu Kim),한훈( 대한내과학회 1995 대한내과학회지 Vol.48 No.6
Autoimmune polyglandular syndrome encompasses a number of diseases, ranging from unusual endocrine and nonendocrine disorders to the co-occurrence of common organ specific autoimmune disease. Knowledge of these syndrome is important for several respects: given the presence of one disease, certain others become more likely(in relatives as well as in the primary patient); there are similarities in the etiology and genetics of the different diseases; and immunologic treatment of one disease may be applicable to others. We recently experienced type II autoimmune polyglandular syndrome in a twenty-two-year old female patient who had insulin dependent diabetes mellitus associated with diabetic ketoacidosis, Hashimoto's thyroiditis, autoimmune Addison's disease, primary gonadal failure and alopecia totalis. Among the family member, twenty-year-old sister showed primary gonadal failure. Evaluation of the histocompatibility leukocyte anti- gene(HLA) was done in the patient and 4 relatives by two-step polymerase chain reaction(PCR). In HLA typing, the patient showed HLA-Al, B8, DR3, DR4 haplotypes, which had been known to be related with the autoimmune polyglandular syndrome.
특집-주요 내분비질환의 진료 지침 : 남성갱년기 증후군 -후기 발현 남성 성선기능저하증-
유순집 ( Soon Jib Yoo ) 대한내과학회 2008 대한내과학회지 Vol.75 No.3
Male climacteric syndrome is a clinical and biochemical syndrome characterized by the decline in serum concentration of biologically active forms of testosterone with aging in men which may result in detrimental effect on the quality of life(QOL) and adversely affect the function of multiple organ systems. Androgen replacement therapy may have favorable effect in QOL, body composition, cardiovascular disease, sexual dysfunction and osteoporosis. Controversy in defining the clinical syndrome and in long-term effect of androgen replacement therapy continues. An international consensus document was recently published and provides guidance on the diagnosis, treatment and monitoring of late-onset hypogonadism (LOH) in males. The diagnosis of LOH requires biochemical and clinical components. Any clinical intervention testosterone treatment should be judged on a balance of risk versus benefit. There have been potential concerns regarding the effects of testosterone on prostate disease and polycythemia. The available treatment methods have increased in recent years with the availability of a number of testosterone preparations which can reliably produce physiological serum concentrations. Periodic physician`s evaluations is required to assess the clinical response and to avoid potential adverse events and must be tailored individually. (Korean J Med 75:262-266, 2008)
내분비 질환에 의한 이차 고혈압의 진단과 치료 ; 갈색세포종의 진단과 치료
유순집 ( Soon Jib Yoo ) 대한내과학회 2012 대한내과학회지 Vol.82 No.4
Pheochromocytomas are rare neuroendocrine tumours with a highly variable and heterogeneous clinical manifestation. With a noticeable progress in genetics, biochemical diagnosis and tumour imaging techniques, modifications of the traditional rule of tens for pheochromocytomas are inevitable consequence. Diagnosis of pheochromocytoma depends on biochemical evidence of catecholamine production by the tumor. Plasma free metanephrines provide the best test for excluding or confirming pheochromocytoma and should be used as an initial screening tool, but if it is not available, urinary fractionated metanephrines could be used as an alternative method. Different anatomical and functional imaging modalities are used to localize biochemically proven pheochromocytomas. These include computed tomography, magnetic resonance imaging, single-photon emission computed tomography (SPECT) using 123/131I-metaiodobenzylguanidine (MIBG) or 111In-DTPA-pentetreotide and positron emission tomography (PET). Timely laparoscopic tumour removal in combination with appropriate pre-and intraoperative management of the effects of secreted catecholamines are essential components for excellent prognosis. (Korean J Med 2012;82:403-410)
유순집(Soon Jib Yoo),안중현(Jung Hyune Ahn),윤건호(Kun Ho Yoon),차봉연(Bong Yun Cha),최의진(Euy Jin Choi),이광우(Kwang Woo Lee),손호영(Ho Young Son),강성구(Sung Koo Kang),김욱(Wook Kim),장은덕(Eun Deok Chang),이해규(Hae Giu Lee) 대한내과학회 1994 대한내과학회지 Vol.46 No.6
Hypercalcemia associated with chronic renal failure is often a matter of clinical problems. Among the many cause of hypercalcemia, tertiary hyperparathyroidism, which is secreting parathyroid hormone autonomously in spite of hypercalcemia, is seldom reported. Sometimes it requires surgical intervention due to not only symptomatic hypercalcemia, but also longlasting asymptomatic hypercalcemia. We recently have experienced a female patient with hypercalcemia in a thirty- seven-year old, who maintains on hemodialysis. She had received kidney from her husband due to chronic renal failure, but it had rejected acutly. She had markedly elevated level of C-terminal parathyroid hormone and radiologic manifestation of adernoma of the parathyroid gland. The bone pathology was consistent with ostitis fibrosa. Subtotal parathyroidectomy showed 1 adenoma and 2 hyperplasia pathologically, afterthen improved clinically and biochemically.
유순집,김석헌,김용주,방병기,강문원,최의진,김석영,우제영,양철우 대한감염학회 1993 감염 Vol.25 No.3
Tuberculous arachnoiditis of the spine is a serious illness with no known definite pathogenesis and therapeutic modalities. It usually has been diagnosed by invasive procedures such as conventional myelography and CT myelography. We recently experienced two patients with arachnoiditis whose conditions were too poor to perform these invasive studies. One was CRF patient in the course of tuberculous meningitis and the other was the patient with comatous mentality and paraplegia which developed during the acute stage of tuberculous menigitis. These patients were diagnosed tuberculous arachnoiditis by spine MRI and medicated antituberculous drug and steroid combination or steroid therapy alone with successful clinical improvement. We reviewed the MRI as a diagnostic tool and steroid as a therapeutic regimen.
Oak-Kee Hong,Soon-Jib Yoo,Jang-Won Son,Mee-Kyoung Kim,Ki Hyun Baek,Ki-Ho Song,Bong-Yun Cha,Hanjoong Jo,Hyuk-Sang Kwon 대한생리학회-대한약리학회 2016 The Korean Journal of Physiology & Pharmacology Vol.20 No.2
Here, we investigated whether hyperglycemia and/or free fatty acids (palmitate, PAL) aff ect the expression level of bone morphogenic protein 4 (BMP4), a proatherogenic marker, in endothelial cells and the potential role of BMP4 in diabetic vascular complications. To measure BMP4 expression, human umbilical vein endothelial cells (HUVECs) were exposed to high glucose concentrations and/ or PAL for 24 or 72 h, and the effects of these treatments on the expression levels of adhesion molecules and reactive oxygen species (ROS) were examined. BMP4 loss-of-function status was achieved via transfection of a BMP4-specific siRNA. High glucose levels increased BMP4 expression in HUVECs in a dose-dependent manner. PAL potentiated such expression. The levels of adhesion molecules and ROS production increased upon treatment with high glucose and/or PAL, but this effect was negated when BMP4 was knocked down via siRNA. Signaling of BMP4, a proinfl ammatory and pro-atherogenic cytokine marker, was increased by hyperglycemia and PAL. BMP4 induced the expression of infl ammatory adhesion molecules and ROS production. Our work suggests that BMP4 plays a role in atherogenesis induced by high glucose levels and/or PAL.
Hong, Oak-Kee,Yoo, Soon-Jib,Son, Jang-Won,Kim, Mee-Kyoung,Baek, Ki-Hyun,Song, Ki-Ho,Cha, Bong-Yun,Jo, Hanjoong,Kwon, Hyuk-Sang The Korean Society of Pharmacology 2016 The Korean Journal of Physiology & Pharmacology Vol.20 No.2
Here, we investigated whether hyperglycemia and/or free fatty acids (palmitate, PAL) affect the expression level of bone morphogenic protein 4 (BMP4), a proatherogenic marker, in endothelial cells and the potential role of BMP4 in diabetic vascular complications. To measure BMP4 expression, human umbilical vein endothelial cells (HUVECs) were exposed to high glucose concentrations and/or PAL for 24 or 72 h, and the effects of these treatments on the expression levels of adhesion molecules and reactive oxygen species (ROS) were examined. BMP4 loss-of-function status was achieved via transfection of a BMP4-specific siRNA. High glucose levels increased BMP4 expression in HUVECs in a dose-dependent manner. PAL potentiated such expression. The levels of adhesion molecules and ROS production increased upon treatment with high glucose and/or PAL, but this eff ect was negated when BMP4 was knocked down via siRNA. Signaling of BMP4, a pro-inflammatory and pro-atherogenic cytokine marker, was increased by hyperglycemia and PAL. BMP4 induced the expression of inflammatory adhesion molecules and ROS production. Our work suggests that BMP4 plays a role in atherogenesis induced by high glucose levels and/or PAL.
Kim, Sung Rae,Yoo, Ji Han,Song, Ho Cheol,Lee, Seong Su,Yoo, Soon Jib,Kim, Young-Du,Lim, Yeon Soo,Kim, Hyung Wook,Yang, Chul Woo,Kim, Yong-Soo,Choi, Euy Jin,Kim, Yong Kyun Springer International ; Oxford University Press 2011 Nephrology, dialysis, transplantation Vol.26 No.11
<P>Obesity and diabetes mellitus (DM) are established risk factors for the development of chronic kidney disease. Visceral adiposity (VAT) and subcutaneous adiposity (SAT) may be associated with the differential metabolic risk. Our study was performed to determine whether VAT or SAT was associated with the decrease of renal function in people with type 2 DM.</P>