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이달의 X-선 : 척추 경막외 기종이 동반된 기관지 천식 1례
이철호 ( Lee Cheol Ho ),권형주 ( Kwon Hyeong Ju ),박영우 ( Park Yeong U ),이무열 ( Lee Mu Yeol ),유흥선 ( Yu Heung Seon ),황인석 ( Hwang In Seog ),김진관 ( Kim Jin Gwan ),김미영 ( Kim Mi Yeong ),신미정 ( Sin Mi Jeong ),황순철 ( Hw 대한결핵 및 호흡기학회 2000 Tuberculosis and Respiratory Diseases Vol.49 No.3
윌슨병 환자에서 Penicillamine 복용 후 발생한 독성표피괴사용해증 1예
이윤임 ( Yoon Im Lee ),이무열 ( Mu Yeol Lee ),박용태 ( Yong Tae Park ),박찬호 ( Chan Ho Park ),성준영 ( Jun Young Sung ),서호석 ( Ho Seok Seo ),최승원 ( Seung Won Choi ) 대한천식알레르기학회 2014 Allergy Asthma & Respiratory Disease Vol.2 No.4
Toxic epidermal necrolysis (TEN) is rare but life-threatening severe cutaneous adverse reaction, which is mostly induced by drugs. It characterized by widespread epidermal necrosis, resulting in bullae with sloughing and frequent involvement of the mucous membrane. Due to high mortality, management of patients requires prompt withdrawal of the causative drug, appropriate supportive care, and consideration of immune-modulating agents, such as intravenous immunoglobulin or corticosteroids. Wilson disease is an inherited disorder of copper transport that results in excessive accumulation of copper in the body. Copper chelation with penicillamine is an effective first line therapy in most patients. We present a 20-year-old man with Wilson disease who developed TEN following administration of penicillamine. He was successfully treated with systemic corticosteroid, intravenous immunoglobulin, and supportive management.
만성 C형 간염에서 B형 간염바이러스 잠재감염의 임상양상과 C형 간염 치료에 미치는 영향
김경훈 ( Kyung Hoon Kim ),홍정민 ( Jung Min Hong ),이무열 ( Mu Yeol Lee ),박능화 ( Neung Hwa Park ),신정우 ( Jung Woo Shin ),최혜정 ( Hye Jeong Choi ),변성수 ( Sung Soo Byun ),박보령 ( Bo Ryung Park ),고명관 ( Myung Kwan Ko ),정 대한내과학회 2012 대한내과학회지 Vol.83 No.6
Background/Aims: The prevalence of occult HBV infection (OBI) in patients with chronic hepatitis C (CHC) in Korea has not been reported. Additionally, it is unclear whether OBI influences treatment outcome in CHC patients. We investigated the prevalence of OBI and its impact on treatment outcome in patients with CHC. Methods: Seventy-six patients with CHC were enrolled and treated with pegylated or conventional interferon and ribavirin. Hepatitis B virus (HBV) DNA was detected by nested polymerase chain reaction. Results: Among the 68 patients who completed treatment and follow-up, HBV DNA was detected in serum from nine (13.2%) patients, liver tissue from 10 (14.7%), and serum or liver tissue from 15 (22.1%). OBI was diagnosed in nine (12.7%) control subjects. No difference in the prevalence of OBI between patients with CHC and controls was observed (13.2 vs. 12.0%; p = 0.92). No significant differences in age, sex, genotype 1 frequency, amount of hepatitis C virus RNA, anti-hepatitis B surface antigen/anti-hepatitis B core-IgG seropositivity, staging, or histology grading were observed in patients with or without HBV DNA. Sustained virological response was achieved in 73.3% of patients with OBI and 83.0% without OBI (p = 0.46). Conclusions: These results demonstrate that a significant proportion of patients with CHC have occult HBV infection and that OBI does not affect treatment outcome in patients with CHC. (Korean J Med 2012;83:731-739)