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증례 : 소화기 ; 췌장 전이를 동반한 원발성 후두 소세포암 1예
홍순창 ( Sun Chang Hong ),이엄석 ( Eaum Seok Lee ),김석현 ( Seok Hyun Kim ),이병석 ( Byung Seok Lee ),문희석 ( Hee Seok Moon ),정현용 ( Hyun Yong Jeong ),강대영 ( Dae Young Kang ) 대한내과학회 2011 대한내과학회지 Vol.80 No.2S
원발성 폐외 소세포암은 드문 질환으로 위장관, 두경부, 비뇨생식기 등 전신에 걸쳐 발생하는 것으로 알려져 있다. 두경부의 소세포암은 후두부에 가장 흔하고, 절반 이상에서 경부 림프절 전이를 보이며, 14-18%에서 원격 전이를 보여, 예후가 불량한 것으로 알려져 있다. 저자들은 42세 남자의 후두에서 발생한 소세포암이 췌장으로 전이된 매우 드문 증례를 경험하였기에 문헌고찰과 함께 보고하는 바이다. Small cell carcinoma (SCC) is predominantly found in the lungs, and extrapulmonary small cell carcinoma (EPSCC) is a relatively rare disease, encompassing 2.5-4% of all SCCs. EPSCCs are commonly found in the esophagus, pancreas, skin, uterus, breasts, and prostate. SCC of the head and neck is aggressive and has a propensity for distant and regional spread. However, solitary metastasis to the pancreas is very rare. We report a case of laryngeal SCC with pancreatic metastasis in a 42-year-old man. The patient underwent resection of a primary SCC followed by a pylorus preserving pancreatoduodenectomy. (Korean J Med 2011; 80:S126-S130)
홍순창 ( Sun Chang Hong ),김지훈 ( Ji Hoon Kim ),이정민 ( Jung Min Lee ),정준오 ( Jun Oh Chung ),김윤권 ( Yun Kwon Kim ),김소연 ( So Yon Kim ),이경인 ( Gyeong In Lee ) 대한내과학회 2006 대한내과학회지 Vol.71 No.3
Chronic neutrophilic leukemia (CNL) is a rare myeloproliferative disorder characterized by clonal proliferation of mature neutrophils, hepatosplenomegaly, elevated leukocyte alkaline phosphatase score (ALP score) and a negative Philadelphia chromosome. To date, approximately 150 cases have been reported in the literature, including some cases presenting with a leukemic state reflected by a neutrophilic reaction. The term rue CNL, recently introduced by Reilly, highlights the need for more experience with CNL cases to improve the diagnostic criteria. In Korea, about 10 cases have been reported in the literature and some of those cases did not meet the WHO diagnostic criteria for CNL. We present a typical case of CNL in a 66-year-old man who complained of general weakness and weight loss. On admission, the white blood cell count from the peripheral blood was 175,600/L with 80% segmented neutrophils. The cytogenic study was negative for the Philadelphia chromosome and had a normal karyotype.(Korean J Med 71:328-332, 2006)
백운희 ( Baeg Un Hui ),김영욱 ( Kim Yeong Ug ),홍순창 ( Hong Sun Chang ),박상준 ( Park Sang Jun ),김윤권 ( Kim Yun Gwon ),김소연 ( Kim So Yeon ),김영중 ( Kim Yeong Jung ),조민구 ( Jo Min Gu ),이권전 ( Lee Gwon Jeon ) 대한신장학회 2003 Kidney Research and Clinical Practice Vol.22 No.4
Liddle`s syndrome is a rare inferited disease with characteristic clinical manifestations of hytertension an hypokalemic metabolic alkalosis. Markedly suppressed serum aldosterone and renin levels are important laboratory findings to differentiate this disorder from primary hyperaldosterionism. When Liddle et al. reported the disorder in 1963, they proposed aggressive Na+ absorption and increased excretion of K+ as the pathogenesis of the syndrome. Since then, specific mutaion in the epithelial Na+ channel located in the collecting duct of the kidney has been dlucidated as a disease mechanism. Liddle`s syndrome is inherited by an autosomal dominant trait and generally the onset of the syndrome is before the age of 20 with increased risk of premature death due to stroke or heart failure. Recently, however, a few cases of late onset and genetically proven non-familial cases with de novo mutation of β or γ Na+ channel have been reported. We report a case of seventy-one year old woman who had hypertension with hypokalemic metabolic alkalosis and was diagnosed as Liddle`s syndrome. Further evaluation revealed low renin and aldosterone levels. Primary aldosteronism, Cushing`s syndrome, glucocorticoid remediable aldosteronism and deficiency of 11 β-OHase and 17α-OHase were ruled out based on her laboratory data and history. Her hypertension and hypokalemia responded to amiloride treatment but not to spironolactone. (Korean J Nephrol 2003;22(4):464-468)
이희정 ( Hee Jung Lee ),정현용 ( Hyun Yong Jeong ),박남환 ( Nam Hwan Park ),홍순창 ( Sun Chang Hong ),남관우 ( Gwan Woo Nam ),문희석 ( Hee Seok Moon ),이엄석 ( Eaum Seok Lee ),김석현 ( Seok Hyun Kim ),성재규 ( Jae Kyu Sung ),이병 대한소화기학회 2011 대한소화기학회지 Vol.57 No.4
Background/Aims: Recently colonoscopy and screening programs have led to the detection and removal of increasing numbers of early colorectal cancer (ECC), which can reduce its related mortality. We analysed the clinical, endoscopic, and histologic findings, as well as the follow-up data, to evaluate the effectiveness and the long-term results of endoscopic mucosal resection (EMR) for ECC. Methods: We analysed, retrospectively, 94 lesions in 92 patients who underwent EMR for ECC from January 2002 to June 2009. Results: The overage age of patients was 60 years old. The mean follow-up period was 22.1 months (6-80). En bloc resection rate was 64.9%. Submucosal invasion was found in 30 cases (31.9%). De novo cancer rate was 26.6% which had higher submucosal invasion rate (60%, p=0.003). The complete resection rate was 87.2%, and there was no recurrence of cancer during follow-up (p=0.000). Twelve incomplete resection cases had received further surgical treatments. No procedure-related mortality was found and no recurrent malignancy was found except 1 case. Conclusions: This study shows that EMR is an effective and safe treatment for ECC. En bloc resection provides precise histologic information and prevention of tumor recurrence. (Korean J Gastroenterol 2011;57:230-236)
교통경찰과 비 교통경찰의 폐기능과 혈중 Carboxyhemoglobin 수치에 대한 비교연구
김성민 ( Kim Seong Min ),전규락 ( Jeon Gyu Lag ),김영욱 ( Kim Yeong Ug ),김준형 ( Kim Jun Hyeong ),이호학 ( Lee Ho Hag ),홍순창 ( Hong Sun Chang ),이승희 ( Lee Seung Hui ),박상준 ( Park Sang Jun ),정준오 ( Jeong Jun O ),김윤권 ( K 대한결핵 및 호흡기학회 2003 Tuberculosis and Respiratory Diseases Vol.55 No.6